-
1
-
-
0027282274
-
Abnormal RNA processing associated with a novel tRNA mutation in mitochondrial DNA. A potential disease mechanism
-
Bindoff LA, Howell N, Poulton J, McCullough DA, Morten KJ, Lightowlers RN, Turnbull DM & Weber K (1993). Abnormal RNA processing associated with a novel tRNA mutation in mitochondrial DNA. A potential disease mechanism. J Biol Chem 268, 19559-19564.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 19559-19564
-
-
Bindoff, L.A.1
Howell, N.2
Poulton, J.3
McCullough, D.A.4
Morten, K.J.5
Lightowlers, R.N.6
Turnbull, D.M.7
Weber, K.8
-
2
-
-
0015407979
-
Relation between the oxidation state of nicotinamide-adenine dinucleotide and the metabolism of spermatozoa
-
Brooks DE & Mann T (1972). Relation between the oxidation state of nicotinamide-adenine dinucleotide and the metabolism of spermatozoa. Biochem J 129, 1023-1034.
-
(1972)
Biochem. J.
, vol.129
, pp. 1023-1034
-
-
Brooks, D.E.1
Mann, T.2
-
3
-
-
0032993159
-
Clinical, biochemical and molecular genetic features of Leber's hereditary optic neuropathy
-
1410
-
Chalmers RM & Schapira AH (1999). Clinical, biochemical and molecular genetic features of Leber's hereditary optic neuropathy. Biochim Biophys Acta 1410, 147-158.
-
(1999)
Biochim. Biophys. Acta
, pp. 147-158
-
-
Chalmers, R.M.1
Schapira, A.H.2
-
4
-
-
0029594523
-
Organization of 3 beta-hydroxysteroid dehydrogenase/isomerase and cytochrome P450scc into a catalytically active molecular complex in bovine adrenocortical mitochondria
-
Cherradi N, Chambaz EM & Defaye G (1995). Organization of 3 beta-hydroxysteroid dehydrogenase/isomerase and cytochrome P450scc into a catalytically active molecular complex in bovine adrenocortical mitochondria. J Steroid Biochem Mol Biol 55, 507-514.
-
(1995)
J. Steroid. Biochem. Mol. Biol.
, vol.55
, pp. 507-514
-
-
Cherradi, N.1
Chambaz, E.M.2
Defaye, G.3
-
5
-
-
0006877856
-
Mice overexpressing human uncoupling protein-3 in skeletal muscle are hyperphagic and lean
-
Clapham JC, Arch JR, Chapman H, Haynes A, Lister C, Moore GB, Piercy V, Carter SA, Lehner I, Smith SA, Beeley LJ, Godden RJ, Herrity N, Skehel M, Changani KK, Hockings PD, Reid DG, Squires SM, Hatcher J, Trail B, Latcham J, Rastan S, Harper AJ, Cadenas S, Buckingham JA, Brand MD & Abuin A (2000). Mice overexpressing human uncoupling protein-3 in skeletal muscle are hyperphagic and lean. Nature 406, 415-418.
-
(2000)
Nature
, vol.406
, pp. 415-418
-
-
Clapham, J.C.1
Arch, J.R.2
Chapman, H.3
Haynes, A.4
Lister, C.5
Moore, G.B.6
Piercy, V.7
Carter, S.A.8
Lehner, I.9
Smith, S.A.10
Beeley, L.J.11
Godden, R.J.12
Herrity, N.13
Skehel, M.14
Changani, K.K.15
Hockings, P.D.16
Reid, D.G.17
Squires, S.M.18
Hatcher, J.19
Trail, B.20
Latcham, J.21
Rastan, S.22
Harper, A.J.23
Cadenas, S.24
Buckingham, J.A.25
Brand, M.D.26
Abuin, A.27
more..
-
6
-
-
0030707553
-
Threshold effects in synaptosomal and nonsynaptic mitochondria from hippocampal CA1 and paramedian neocortex brain regions
-
Davey GP, Canevari L & Clark JB (1997). Threshold effects in synaptosomal and nonsynaptic mitochondria from hippocampal CA1 and paramedian neocortex brain regions. J Neurochem 69, 2564-2570.
-
(1997)
J. Neurochem.
, vol.69
, pp. 2564-2570
-
-
Davey, G.P.1
Canevari, L.2
Clark, J.B.3
-
7
-
-
0032557511
-
Energy threshold in brain mitochondria. Potential involvement in neurodegeneration
-
Davey GP, Peuchen S & Clark JB (1998). Energy threshold in brain mitochondria. Potential involvement in neurodegeneration. J Biol Chem 273, 12753-12757.
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 12753-12757
-
-
Davey, G.P.1
Peuchen, S.2
Clark, J.B.3
-
8
-
-
0345355149
-
Transcription of the adenine nucleotide translocase isoforms in various types of tissues in the rat
-
1417
-
Dörner A, Olesch M, Giessen S, Pauschinger M & Schultheiss HP (1999). Transcription of the adenine nucleotide translocase isoforms in various types of tissues in the rat. Biochim Biophys Acta 1417, 16-24.
-
(1999)
Biochim. Biophys. Acta
, pp. 16-24
-
-
Dörner, A.1
Olesch, M.2
Giessen, S.3
Pauschinger, M.4
Schultheiss, H.P.5
-
9
-
-
0031559959
-
Tissue-specific transcription pattern of the adenine nucleotide translocase isoforms in humans
-
Dörner A, Pauschinger M, Badorff A, Noutsias M, Giessen S, Schulze K, Bilger J, Rauch U & Schultheiss HP (1997). Tissue-specific transcription pattern of the adenine nucleotide translocase isoforms in humans. FEBS Lett 414, 258-262.
-
(1997)
FEBS Lett.
, vol.414
, pp. 258-262
-
-
Dörner, A.1
Pauschinger, M.2
Badorff, A.3
Noutsias, M.4
Giessen, S.5
Schulze, K.6
Bilger, J.7
Rauch, U.8
Schultheiss, H.P.9
-
10
-
-
18244379331
-
Superoxide activates mitochondrial uncoupling proteins
-
Echtay KS, Roussel D, St-Pierre J, Jekabsons MB, Cadenas S, Stuart JA, Harper JA, Roebuck SJ, Morrison A, Pickering S, Clapham JC & Brand MD (2002). Superoxide activates mitochondrial uncoupling proteins. Nature 415, 96-99.
-
(2002)
Nature
, vol.415
, pp. 96-99
-
-
Echtay, K.S.1
Roussel, D.2
St-Pierre, J.3
Jekabsons, M.B.4
Cadenas, S.5
Stuart, J.A.6
Harper, J.A.7
Roebuck, S.J.8
Morrison, A.9
Pickering, S.10
Clapham, J.C.11
Brand, M.D.12
-
11
-
-
0029670481
-
+/e-stoichiometry of cytochrome c oxidase from bovine heart by intramitochondrial ATP/ADP ratios
-
+/e-stoichiometry of cytochrome c oxidase from bovine heart by intramitochondrial ATP/ADP ratios. FEBS Lett 382, 121-124.
-
(1996)
FEBS Lett.
, vol.382
, pp. 121-124
-
-
Frank, V.1
Kadenbach, B.2
-
12
-
-
0021106617
-
Control of mitochondrial respiration. The contribution of the adenine nucleotide translocator depends on the ATP- and ADP-consuming enzymes
-
Gellerich FN, Bohnensack R & Kunz W (1983). Control of mitochondrial respiration. The contribution of the adenine nucleotide translocator depends on the ATP- and ADP-consuming enzymes. Biochim Biophys Acta 722, 381-391.
-
(1983)
Biochim. Biophys. Acta
, vol.722
, pp. 381-391
-
-
Gellerich, F.N.1
Bohnensack, R.2
Kunz, W.3
-
13
-
-
0022877497
-
Control of gluconeogenesis in rat liver cells. Flux control coefficients of the enzymes in the gluconeogenic pathway in the absence and presence of glucagon
-
Groen AK, van Roermund CW, Vervoorn RC & Tager JM (1986). Control of gluconeogenesis in rat liver cells. Flux control coefficients of the enzymes in the gluconeogenic pathway in the absence and presence of glucagon. Biochem J 237, 379-389.
-
(1986)
Biochem. J.
, vol.237
, pp. 379-389
-
-
Groen, A.K.1
van Roermund, C.W.2
Vervoorn, R.C.3
Tager, J.M.4
-
14
-
-
0020490497
-
Quantification of the contribution of various steps to the control of mitochondrial respiration
-
Groen AK, Wanders RJ, Westerhoff HV, van der Meer R & Tager JM (1982). Quantification of the contribution of various steps to the control of mitochondrial respiration. J Biol Chem 257, 2754-2757.
-
(1982)
J. Biol. Chem.
, vol.257
, pp. 2754-2757
-
-
Groen, A.K.1
Wanders, R.J.2
Westerhoff, H.V.3
van der Meer, R.4
Tager, J.M.5
-
16
-
-
0026027545
-
Use of NAD(P)H and flavoprotein fluorescence signals to characterize the redox state of pyrimidine nucleotides in epididymal bull spermatozoa
-
1056
-
Halangk W & Kunz WS (1991). Use of NAD(P)H and flavoprotein fluorescence signals to characterize the redox state of pyrimidine nucleotides in epididymal bull spermatozoa. Biochim Biophys Acta 1056, 273-278.
-
(1991)
Biochim. Biophys. Acta
, pp. 273-278
-
-
Halangk, W.1
Kunz, W.S.2
-
17
-
-
0015949374
-
A linear steady-state treatment of enzymatic chains. Critique of the crossover theorem and a general procedure to identify interaction sites with an effector
-
Heinrich R & Rapoport TA (1974). A linear steady-state treatment of enzymatic chains. Critique of the crossover theorem and a general procedure to identify interaction sites with an effector. Eur J Biochem 42, 97-105.
-
(1974)
Eur. J. Biochem.
, vol.42
, pp. 97-105
-
-
Heinrich, R.1
Rapoport, T.A.2
-
18
-
-
0035804655
-
Mammalian subunit IV isoforms of cytochrome c oxidase
-
Hüttemann M, Kadenbach B & Grossman LI (2001). Mammalian subunit IV isoforms of cytochrome c oxidase. Gene 267, 111-123.
-
(2001)
Gene
, vol.267
, pp. 111-123
-
-
Hüttemann, M.1
Kadenbach, B.2
Grossman, L.I.3
-
19
-
-
0030995458
-
Light and electron microscopic immunohistochemistry of the localization of adrenal steroidogenic enzymes
-
Ishimura K & Fujita H (1997). Light and electron microscopic immunohistochemistry of the localization of adrenal steroidogenic enzymes. Microsc Res Tech 36, 445-453.
-
(1997)
Microsc. Res. Tech.
, vol.36
, pp. 445-453
-
-
Ishimura, K.1
Fujita, H.2
-
20
-
-
15644370475
-
Progressive myoclonus epilepsy associated with mutations in the tRNA (Ser(UCN)) gene
-
Jaksch M, Klopstock T & Kurlemann G (1998). Progressive myoclonus epilepsy associated with mutations in the tRNA (Ser(UCN)) gene. Ann Neurol 44, 635-640.
-
(1998)
Ann. Neurol.
, vol.44
, pp. 635-640
-
-
Jaksch, M.1
Klopstock, T.2
Kurlemann, G.3
-
21
-
-
0026757115
-
An ND-6 mitochondrial DNA mutation associated with Leber hereditary optic neuropathy
-
Johns DR, Neufeld MJ & Park RD (1992). An ND-6 mitochondrial DNA mutation associated with Leber hereditary optic neuropathy. Biochem Biophys Res Commun 187, 1551-1557.
-
(1992)
Biochem. Biophys. Res. Commun.
, vol.187
, pp. 1551-1557
-
-
Johns, D.R.1
Neufeld, M.J.2
Park, R.D.3
-
23
-
-
0029853166
-
Theoretical studies on the control of oxidative phosphorylation in muscle mitochondria: Application to mitochondrial deficiencies
-
Korzeniewski B & Mazat JP (1996). Theoretical studies on the control of oxidative phosphorylation in muscle mitochondria: application to mitochondrial deficiencies. Biochem J 319, 143-148.
-
(1996)
Biochem. J.
, vol.319
, pp. 143-148
-
-
Korzeniewski, B.1
Mazat, J.P.2
-
24
-
-
0014797650
-
Conditions for activity of glutaminase in kidney mitochondria
-
Kovacevic Z, McGivan JD & Chappel JB (1970). Conditions for activity of glutaminase in kidney mitochondria. Biochem J 118, 265-274.
-
(1970)
Biochem. J.
, vol.118
, pp. 265-274
-
-
Kovacevic, Z.1
McGivan, J.D.2
Chappel, J.B.3
-
25
-
-
0036042116
-
Differences in flux control and reserve capacity of cytochrome c oxidase (COX) in human skeletal muscle and brain suggest different metabolic effects of mild COX deficiencies
-
Kudin A, Vielhaber S, Elger CE & Kunz WS (2002). Differences in flux control and reserve capacity of cytochrome c oxidase (COX) in human skeletal muscle and brain suggest different metabolic effects of mild COX deficiencies. Mol Biol Rep 29, 89-92.
-
(2002)
Mol. Biol. Rep.
, vol.29
, pp. 89-92
-
-
Kudin, A.1
Vielhaber, S.2
Elger, C.E.3
Kunz, W.S.4
-
26
-
-
0027267866
-
Quantification of the content of fluorescent flavoproteins in mitochondria from liver, kidney cortex, skeletal muscle, and brain
-
Kunz WS & Gellerich FN (1993). Quantification of the content of fluorescent flavoproteins in mitochondria from liver, kidney cortex, skeletal muscle, and brain. Biochem Med Metab Biol 50, 103-110.
-
(1993)
Biochem. Med. Metab. Biol.
, vol.50
, pp. 103-110
-
-
Kunz, W.S.1
Gellerich, F.N.2
-
27
-
-
0026763490
-
Glutamine affects glutamate metabolism in isolated rat kidney mitochondria
-
1100
-
Kunz WS, Krinelke L & Gellerich FN (1992). Glutamine affects glutamate metabolism in isolated rat kidney mitochondria. Biochim Biophys Acta 1100, 329-331.
-
(1992)
Biochim. Biophys. Acta
, pp. 329-331
-
-
Kunz, W.S.1
Krinelke, L.2
Gellerich, F.N.3
-
28
-
-
0034623157
-
Flux control of cytochrome c oxidase in human skeletal muscle
-
Kunz WS, Kudin A, Vielhaber S, Elger CE, Attardi G & Villani G (2000). Flux control of cytochrome c oxidase in human skeletal muscle. J Biol Chem 275, 27741-27745.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 27741-27745
-
-
Kunz, W.S.1
Kudin, A.2
Vielhaber, S.3
Elger, C.E.4
Attardi, G.5
Villani, G.6
-
29
-
-
0019878639
-
Influence of different energy drains on the interrelationship between the rate of respiration, proton-motive force and adenine nucleotide patterns in isolated mitochondria
-
Küster U, Letko G, Kunz W, Duszynsky J, Bogucka K & Wojtczak L (1981). Influence of different energy drains on the interrelationship between the rate of respiration, proton-motive force and adenine nucleotide patterns in isolated mitochondria. Biochim Biophys Acta 636, 32-38.
-
(1981)
Biochim. Biophys. Acta
, vol.636
, pp. 32-38
-
-
Küster, U.1
Letko, G.2
Kunz, W.3
Duszynsky, J.4
Bogucka, K.5
Wojtczak, L.6
-
30
-
-
0034702878
-
Expression and sequence analysis of the mouse adenine nucleotide translocase 1 and 2 genes
-
Levy SE, Chen YS, Graham BH & Wallace DC (2000). Expression and sequence analysis of the mouse adenine nucleotide translocase 1 and 2 genes. Gene 254, 57-66.
-
(2000)
Gene
, vol.254
, pp. 57-66
-
-
Levy, S.E.1
Chen, Y.S.2
Graham, B.H.3
Wallace, D.C.4
-
31
-
-
0027428777
-
Gene structure of human mitochondrial ATP synthase gamma-subunit. Tissue specificity produced by alternative RNA splicing
-
Matsuda C, Endo H, Ohta S & Kagawa Y (1993). Gene structure of human mitochondrial ATP synthase gamma-subunit. Tissue specificity produced by alternative RNA splicing. J Biol Chem 268, 24950-24958.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 24950-24958
-
-
Matsuda, C.1
Endo, H.2
Ohta, S.3
Kagawa, Y.4
-
32
-
-
0017374025
-
Factors affecting the redox state of bovine epididymal spermatozoa
-
Milkowski AL & Lardy HA (1977). Factors affecting the redox state of bovine epididymal spermatozoa. Arch Biochem Biophys 181, 270-277.
-
(1977)
Arch. Biochem. Biophys.
, vol.181
, pp. 270-277
-
-
Milkowski, A.L.1
Lardy, H.A.2
-
33
-
-
0017700139
-
Inhibition of acetoacetate oxidation by brain mitochondria from the suckling rat by phenylpyruvate and alpha ketoisocaproate
-
Patel TB, Booth RF & Clark JB (1977). Inhibition of acetoacetate oxidation by brain mitochondria from the suckling rat by phenylpyruvate and alpha ketoisocaproate. J Neurochem 29, 1151-1153.
-
(1977)
J. Neurochem.
, vol.29
, pp. 1151-1153
-
-
Patel, T.B.1
Booth, R.F.2
Clark, J.B.3
-
34
-
-
0034177951
-
Tissue variation in the control of oxidative phosphorylation: Implication for mitochondrial diseases
-
Rossignol R, Letellier T, Malgat M, Rocher C & Mazat JP (2000). Tissue variation in the control of oxidative phosphorylation: implication for mitochondrial diseases. Biochem J 347, 45-53.
-
(2000)
Biochem. J.
, vol.347
, pp. 45-53
-
-
Rossignol, R.1
Letellier, T.2
Malgat, M.3
Rocher, C.4
Mazat, J.P.5
-
35
-
-
0033584845
-
Threshold effect and tissue specificity. Implication for mitochondrial cytopathies
-
Rossignol R, Malgat M, Mazat JP & Letellier T (1999). Threshold effect and tissue specificity. Implication for mitochondrial cytopathies. J Biol Chem 274, 33426-33432.
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 33426-33432
-
-
Rossignol, R.1
Malgat, M.2
Mazat, J.P.3
Letellier, T.4
-
36
-
-
0031784401
-
Epilepsia partialis continua associated with a homoplasmic mitochondrial tRNA (Ser(UCN)) mutation
-
Schülke M, Bakker M & Stoltenburg G (1998). Epilepsia partialis continua associated with a homoplasmic mitochondrial tRNA (Ser(UCN)) mutation. Ann Neurol 44, 700-704.
-
(1998)
Ann. Neurol.
, vol.44
, pp. 700-704
-
-
Schülke, M.1
Bakker, M.2
Stoltenburg, G.3
-
38
-
-
0031029962
-
In vivo control of respiration by cytochrome c oxidase in wild-type and mitochondrial DNA mutation-carrying human cells
-
Villani G & Attardi G (1997). In vivo control of respiration by cytochrome c oxidase in wild-type and mitochondrial DNA mutation-carrying human cells. Proc Natl Acad Sci U S A 94, 1166-1171.
-
(1997)
Proc. Natl. Acad. Sci. U S A
, vol.94
, pp. 1166-1171
-
-
Villani, G.1
Attardi, G.2
-
39
-
-
0033610865
-
Low reserve of cytochrome c oxidase capacity in vivo in the respiratory chain of a variety of human cell types
-
Villani G, Greco M, Papa S & Attardi G (1998). Low reserve of cytochrome c oxidase capacity in vivo in the respiratory chain of a variety of human cell types. J Biol Chem 273, 31829-31836.
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 31829-31836
-
-
Villani, G.1
Greco, M.2
Papa, S.3
Attardi, G.4
-
40
-
-
0026624980
-
Diseases of the mitochondrial DNA
-
Wallace DC (1992). Diseases of the mitochondrial DNA. Annu Rev Biochem 61, 1175-1212.
-
(1992)
Annu. Rev. Biochem.
, vol.61
, pp. 1175-1212
-
-
Wallace, D.C.1
-
41
-
-
0024242545
-
Mitochondrial DNA mutation associated with Leber's hereditary optic neuropathy
-
Wallace DC, Singh G, Lott MT, Hodge JA, Schurr TG, Lezza AM, Elsas LJ & Nikoskelainen EK (1988). Mitochondrial DNA mutation associated with Leber's hereditary optic neuropathy. Science 242, 1427-1430.
-
(1988)
Science
, vol.242
, pp. 1427-1430
-
-
Wallace, D.C.1
Singh, G.2
Lott, M.T.3
Hodge, J.A.4
Schurr, T.G.5
Lezza, A.M.6
Elsas, L.J.7
Nikoskelainen, E.K.8
-
42
-
-
0014082605
-
The redox state of free nicotinamide-adenine dinucleotide in the cytoplasm and mitochondria of rat liver
-
Williamson DH, Lund P & Krebs HA (1967). The redox state of free nicotinamide-adenine dinucleotide in the cytoplasm and mitochondria of rat liver. Biochem J 103, 514-527.
-
(1967)
Biochem. J.
, vol.103
, pp. 514-527
-
-
Williamson, D.H.1
Lund, P.2
Krebs, H.A.3
-
43
-
-
0029039749
-
Distribution of flux control among the enzymes of mitochondrial oxidative phosphorylation in calcium-activated saponin-skinned rat M. soleus fibers
-
Wisniewski E, Gellerich FN & Kunz WS (1995). Distribution of flux control among the enzymes of mitochondrial oxidative phosphorylation in calcium-activated saponin-skinned rat M. soleus fibers. Eur J Biochem 230, 549-554.
-
(1995)
Eur. J. Biochem.
, vol.230
, pp. 549-554
-
-
Wisniewski, E.1
Gellerich, F.N.2
Kunz, W.S.3
-
44
-
-
0027157645
-
Phosphate affects the distribution of flux control among the enzymes of oxidative phosphorylation in rat skeletal muscle mitochondria
-
Wisniewski E, Kunz WS & Gellerich FN (1993). Phosphate affects the distribution of flux control among the enzymes of oxidative phosphorylation in rat skeletal muscle mitochondria. J Biol Chem 268, 9343-9346.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 9343-9346
-
-
Wisniewski, E.1
Kunz, W.S.2
Gellerich, F.N.3
-
45
-
-
0023665017
-
Fatty acid oxidation in rat brain is limited by the low activity of 3-ketoacyl-coenzyme A thiolase
-
Yang SY, He XY & Schulz H (1987). Fatty acid oxidation in rat brain is limited by the low activity of 3-ketoacyl-coenzyme A thiolase. J Biol Chem 262, 13027-13032.
-
(1987)
J. Biol. Chem.
, vol.262
, pp. 13027-13032
-
-
Yang, S.Y.1
He, X.Y.2
Schulz, H.3
|