Idiopathic hyperammonemia following an unrelated cord blood transplant for mucopolysaccharidosis I

Pediatric and Developmental Pathology

Volumn 6, Issue 1, 2003, Pages 78-83

  Snyder, Matthew J ^a   Bradford, William D ^a   Kishnani, Priya S ^a   Hale, Laura P ^a  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

Author keywords

Bone marrow transplantation; Cord blood transplantation; Hurler syndrome; Hyperammonemia; Liver pathology; Mucopolysaccharidosis I

Indexed keywords

AMINO ACID ANALYSIS; ARTICLE; BLOOD TRANSFUSION; BONE MARROW TRANSPLANTATION; CASE REPORT; CELL PROLIFERATION; ENZYME DEFICIENCY; ENZYME METABOLISM; HISTOPATHOLOGY; HUMAN; HYPERAMMONEMIA; HYPERVENTILATION; IDIOPATHIC DISEASE; INFANT; MALE; MUCOPOLYSACCHARIDOSIS; PRIORITY JOURNAL; TISSUE SECTION; UMBILICAL CORD BLOOD;

AMMONIA; CORD BLOOD STEM CELL TRANSPLANTATION; FATAL OUTCOME; FATTY LIVER; FETAL BLOOD; HUMANS; HYPERAMMONEMIA; INFANT; LIVER; MALE; MUCOPOLYSACCHARIDOSIS I;

EID: 0037229804     PISSN: 10935266     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10024-001-0271-3     Document Type: Article

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