Blood mononuclear cell coenzyme Q10 concentration and mitochondrial respiratory chain succinate cytochrome-c reductase activity in phenylketonuric patients

Journal of Inherited Metabolic Disease

Volumn 25, Issue 8, 2003, Pages 673-679

  Hargreaves, I P ^a   Heales, S J R ^a   Briddon, A ^a   Land, J M ^a   Lee, P J ^a  

^a NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ADENOSINE TRIPHOSPHATE; ENZYME PRECURSOR; ESSENTIAL AMINO ACID; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; MINERAL; PHENYLALANINE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; SUCCINATE DEHYDROGENASE; SUCCINIC ACID; TRACE ELEMENT; UBIDECARENONE; VITAMIN;

ADOLESCENT; ADULT; AMINO ACID BLOOD LEVEL; ARTICLE; BIOSYNTHESIS; CELLULAR DISTRIBUTION; CLINICAL ARTICLE; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; DIET RESTRICTION; DIET SUPPLEMENTATION; DISEASE PREDISPOSITION; ELECTRON TRANSPORT; ENZYME ACTIVITY; FEMALE; HUMAN; MALE; MITOCHONDRIAL RESPIRATION; MONONUCLEAR CELL; NUCLEIC ACID SYNTHESIS; OXIDATIVE PHOSPHORYLATION; PHENYLKETONURIA; PROTEIN FUNCTION; PROTEIN LOCALIZATION; RESPIRATORY CHAIN;

EID: 0036978239     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022881231253     Document Type: Article

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