76th ENMC International Workshop: Pathophysiology and therapy in the mdx mouse 21-23 January 2000, Naarden, The Netherlands

Neuromuscular Disorders

Volumn 12, Issue 4, 2002, Pages 415-420

  Rudel R ^a   Brinkmeier, H ^a  

^a UNIVERSITY OF ULM   (Germany)

Author keywords

Duchenne muscular dystrophy; Gene therapy; mdx Mouse; Pathophysiology; Pharmacotherapy

Indexed keywords

ADOPTIVE IMMUNOTHERAPY; CALCIUM CELL LEVEL; CELL DEATH; CONFERENCE PAPER; CYTOLOGY; DUCHENNE MUSCULAR DYSTROPHY; ELECTROSTIMULATION; GENE THERAPY; GENOTYPE; MEDICAL LITERATURE; MEDICAL RESEARCH; MOLECULAR BIOLOGY; MUSCLE CELL; MUSCLE DEVELOPMENT; MUSCLE RELAXATION; NETHERLANDS; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; PUBLISHING; SARCOLEMMA; STEM CELL;

ANIMALS; DISEASE MODELS, ANIMAL; MICE; MICE, INBRED MDX; MUSCULAR DYSTROPHY, ANIMAL; MUSCULAR DYSTROPHY, DUCHENNE;

EID: 0036223817     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(01)00327-3     Document Type: Conference Paper

References (30)

1. The animal models of Duchenne muscular dystrophy: Windows on the pathophysiological consequences of dystrophin deficiency
2. Understanding dystrophinopathies: An inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse
3. Recruitment of bone-marrow-derived cells by skeletal and cardiac muscle in adult dystrophic mdx mice
4. Mutual interference of myotonia and muscular dystrophy in the mouse: A study on ADR-MDX double mutants
5. Factors inducing mast cell accumulation in skeletal muscle
6. Regulation of cytosolic calcium in skeletal muscle cells of the mdx mouse under conditions of stress
7. New light on mitochondrial calcium
8. Increased calcium entry into dystrophin-deficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers
9. Tetanus relaxation of fast skeletal muscles of the mouse made parvalbumin deficient by gene inactivation
10. Myotonic ADR-MDX mutant mice show less severe muscular dystrophy than MDX mice
11. Age-related changes in muscle calcium content in dystrophin-deficient mdx mice
12. Time course of changes in plasma membrane permeability in the dystrophin-deficient mdx mouse
13. Apoptosis in multinucleated skeletal muscle myotubes
14. mdx-βgeo: A new allele for the mouse dystrophin gene
15. Dynamics of myoblast transplantation reveal a discrete minority of precursors with stem cell-like properties as the myogenic source
16. Evidence for a myogenic stem cell that is exhausted in dystrophic muscle
17. Skeletal myogenic progenitors originating from embryonic dorsal aorta coexpress endothelial and myogenic markers and contribute to postnatal muscle growth and regeneration
18. Muscle regeneration by bone marrow-derived myogenic progenitors
19. 2+ handling and survival in mdx skeletal muscle cells
20. Effect of propylthiouracil-induced hypothyroidism on the onset of skeletal muscle necrosis in dystrophin-deficient mdx mice
21. Pre-clinical screening of drugs using the mdx mouse
22. Electrical properties of diaphragm and EDL muscles during the life of dystrophic mice
23. Nuclear magnetic resonance spectroscopy study of muscle growth, mdx dystrophy and glucocorticoid treatments: Correlation with repair
24. Expression of full-length utrophin prevents muscular dystrophy in mdx mice
25. Skeletal muscle-specific expression of a utrophin transgene rescues utrophin-dystrophin deficient mice
26. Prevention of the dystrophic phenotype in dystrophin/utrophin-deficient muscle following adenovirus-mediated transfer of a utrophin minigene
27. Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice
28. Dystrophin expression in muscles of mdx mice after adenovirus-mediated in vivo gene transfer
29. Transient immunosuppression by FK506 permits a sustained high-level dystrophin expression after adenovirus-mediated dystrophin minigene transfer to skeletal muscles of adult dystrophic (mdx) mice
30. Adenovirus-mediated dystrophin minigene transfer improves muscle strength in adult dystrophic (MDX) mice