-
5
-
-
0032007565
-
-
Reche, P., Li, Y. L., Fuller, C., Eichhorn, K., and Perham, R. N. (1998) Biochem. J. 329, 589-596
-
(1998)
Biochem. J.
, vol.329
, pp. 589-596
-
-
Reche, P.1
Li, Y.L.2
Fuller, C.3
Eichhorn, K.4
Perham, R.N.5
-
7
-
-
0029593413
-
-
Val, D. L., Chapman-Smith, A., Walker, M. E., Cronan, J. E., Jr., and Wallace, J. C. (1995) Biochem. J. 312, 817-825
-
(1995)
Biochem. J.
, vol.312
, pp. 817-825
-
-
Val, D.L.1
Chapman-Smith, A.2
Walker, M.E.3
Cronan J.E., Jr.4
Wallace, J.C.5
-
10
-
-
0030668421
-
-
Yao, X., Wei, D., Soden, C. J., Summers, M. F., and Beckett, D. (1997) Biochemistry 36, 15089-15100
-
(1997)
Biochemistry
, vol.36
, pp. 15089-15100
-
-
Yao, X.1
Wei, D.2
Soden, C.J.3
Summers, M.F.4
Beckett, D.5
-
11
-
-
0000041171
-
-
Reddy, D. V., Shenoy, B. C., Carey, P. R., and Sönnichsen, F. D. (2000) Biochemistry 39, 2509-2516
-
(2000)
Biochemistry
, vol.39
, pp. 2509-2516
-
-
Reddy, D.V.1
Shenoy, B.C.2
Carey, P.R.3
Sönnichsen, F.D.4
-
12
-
-
0033586767
-
-
Roberts, E. L., Shu, N., Howard, M. J., Broadhurst, R. W., Chapman-Smith, A., Wallace, J. C., Morris, T., Cronan, J. E. Jr., and Perham, R. N. (1999) Biochemistry 38, 5045-5053
-
(1999)
Biochemistry
, vol.38
, pp. 5045-5053
-
-
Roberts, E.L.1
Shu, N.2
Howard, M.J.3
Broadhurst, R.W.4
Chapman-Smith, A.5
Wallace, J.C.6
Morris, T.7
Cronan J.E., Jr.8
Perham, R.N.9
-
13
-
-
0026666377
-
-
Wilson, K. P., Shewchuk, L. M., Brennan, R. G., Otsuka, A. J., and Matthews, B. W. (1992) Proc. Natl. Acad. Sci. U. S. A. 89, 9257-9261
-
(1992)
Proc. Natl. Acad. Sci. U. S. A.
, vol.89
, pp. 9257-9261
-
-
Wilson, K.P.1
Shewchuk, L.M.2
Brennan, R.G.3
Otsuka, A.J.4
Matthews, B.W.5
-
15
-
-
0022535750
-
-
Buoncristiani, M. R., Howard, P. K., and Otsuka, A. J. (1986) Gene 44, 255-261
-
(1986)
Gene
, vol.44
, pp. 255-261
-
-
Buoncristiani, M.R.1
Howard, P.K.2
Otsuka, A.J.3
-
17
-
-
0029064585
-
-
Leon-Del-Rio, A., Leclerc, D., Akerman, B., Wakamatsu, N., and Gravel, R. A. (1995) Proc. Natl. Acad. Sci. U. S. A. 92, 4626-4630
-
(1995)
Proc. Natl. Acad. Sci. U. S. A.
, vol.92
, pp. 4626-4630
-
-
Leon-Del-Rio, A.1
Leclerc, D.2
Akerman, B.3
Wakamatsu, N.4
Gravel, R.A.5
-
18
-
-
0029002446
-
-
Bower, S., Perkins, J., Yocum, R. R., Serror, P., Sorokin, A., Rahaim, P., Howitt, C. L., Prasad, N., Ehrlich, S. D., and Pero, J. (1995) J. Bacteriol. 177, 2572-2575
-
(1995)
J. Bacteriol.
, vol.177
, pp. 2572-2575
-
-
Bower, S.1
Perkins, J.2
Yocum, R.R.3
Serror, P.4
Sorokin, A.5
Rahaim, P.6
Howitt, C.L.7
Prasad, N.8
Ehrlich, S.D.9
Pero, J.10
-
20
-
-
0030906456
-
-
Tissot, G., Douce, R., and Alban, C. (1997) Biochem. J. 323, 179-188
-
(1997)
Biochem. J.
, vol.323
, pp. 179-188
-
-
Tissot, G.1
Douce, R.2
Alban, C.3
-
21
-
-
0032403883
-
-
Tissot, G., Pepin, R., Job, D., Douce, R., and Alban, C. (1998) Eur. J. Biochem. 258, 586-596
-
(1998)
Eur. J. Biochem.
, vol.258
, pp. 586-596
-
-
Tissot, G.1
Pepin, R.2
Job, D.3
Douce, R.4
Alban, C.5
-
25
-
-
0024287682
-
-
Samols, D., Thornton, C. G., Murtif, V. L., Kumar, G. K., Haase, F. C., and Wood, H. G. (1988) J. Biol. Chem. 263, 6461-6464
-
(1988)
J. Biol. Chem.
, vol.263
, pp. 6461-6464
-
-
Samols, D.1
Thornton, C.G.2
Murtif, V.L.3
Kumar, G.K.4
Haase, F.C.5
Wood, H.G.6
-
26
-
-
0028108943
-
-
Chapman-Smith, A., Turner, D. L., Cronan, J. E. Jr., Morris, T. W., and Wallace, J. C. (1994) Biochem. J. 302, 881-887
-
(1994)
Biochem. J.
, vol.302
, pp. 881-887
-
-
Chapman-Smith, A.1
Turner, D.L.2
Cronan J.E., Jr.3
Morris, T.W.4
Wallace, J.C.5
-
27
-
-
0003114965
-
-
(Scriver, C. R., Beaudet. A. L., Sly, W. S., and Valle, D., eds), McGraw-Hill, New York
-
Wolf, B. (1995) in The Metabolic and Molecular Bases of Inherited Disease (Scriver, C. R., Beaudet. A. L., Sly, W. S., and Valle, D., eds) pp. 3151-3177, McGraw-Hill, New York
-
(1995)
The Metabolic and Molecular Bases of Inherited Disease
, pp. 3151-3177
-
-
Wolf, B.1
-
28
-
-
0018639436
-
-
Saunders, M., Sweetman, L., Robinson, B., Roth, R., Cohn, R., and Gravel, R. A. (1979) J. Clin. Invest. 64, 1695-1702
-
(1979)
J. Clin. Invest.
, vol.64
, pp. 1695-1702
-
-
Saunders, M.1
Sweetman, L.2
Robinson, B.3
Roth, R.4
Cohn, R.5
Gravel, R.A.6
-
29
-
-
0019954922
-
-
Saunders, M. E., Sherwood, W. G., Duthie, M., Surh, L., and Gravel, R. A. (1982) Am. J. Hum. Genet. 34, 590-601
-
(1982)
Am. J. Hum. Genet.
, vol.34
, pp. 590-601
-
-
Saunders, M.E.1
Sherwood, W.G.2
Duthie, M.3
Surh, L.4
Gravel, R.A.5
-
30
-
-
0019792634
-
-
Burri, B. J., Sweetman, L., and Nyhan, W. L. (1981) J. Clin. Invest. 68, 1491-1495
-
(1981)
J. Clin. Invest.
, vol.68
, pp. 1491-1495
-
-
Burri, B.J.1
Sweetman, L.2
Nyhan, W.L.3
-
32
-
-
0030983707
-
-
Suormala, T., Fowler, B., Duran, M., Burtscher, A., Fuchshuber, A., Tratzmuller, R., Lenze, M. J., Raab, K., Baur, B., Wick, H., and Baumgartner, R. (1997) Pediatr. Res. 41, 666-673
-
(1997)
Pediatr. Res.
, vol.41
, pp. 666-673
-
-
Suormala, T.1
Fowler, B.2
Duran, M.3
Burtscher, A.4
Fuchshuber, A.5
Tratzmuller, R.6
Lenze, M.J.7
Raab, K.8
Baur, B.9
Wick, H.10
Baumgartner, R.11
-
33
-
-
0030055368
-
-
Dupuis, L., Leon-Del-Rio, A., Leclerc, D., Campeau, E., Sweetman, L., Saudubray, J. M., Herman, G., Gibson, K. M., and Gravel, R. A. (1996) Hum. Mol. Genet. 5, 1011-1016
-
(1996)
Hum. Mol. Genet.
, vol.5
, pp. 1011-1016
-
-
Dupuis, L.1
Leon-Del-Rio, A.2
Leclerc, D.3
Campeau, E.4
Sweetman, L.5
Saudubray, J.M.6
Herman, G.7
Gibson, K.M.8
Gravel, R.A.9
-
34
-
-
0033049264
-
-
Aoki, Y., Li, X., Sakamoto, O., Hiratsuka, M., Akaishi, H., Xu, L., Briones, P., Suormala, T., Baumgartner, E. R., Suzuki, Y., and Narisawa, K. (1999) Hum. Genet. 104, 143-148
-
(1999)
Hum. Genet.
, vol.104
, pp. 143-148
-
-
Aoki, Y.1
Li, X.2
Sakamoto, O.3
Hiratsuka, M.4
Akaishi, H.5
Xu, L.6
Briones, P.7
Suormala, T.8
Baumgartner, E.R.9
Suzuki, Y.10
Narisawa, K.11
-
35
-
-
0032809640
-
-
Dupuis, L., Campeau, E., Leclerc, D., and Gravel, R. A. (1999) Mol. Genet. Metab. 66, 80-90
-
(1999)
Mol. Genet. Metab.
, vol.66
, pp. 80-90
-
-
Dupuis, L.1
Campeau, E.2
Leclerc, D.3
Gravel, R.A.4
-
36
-
-
0030702915
-
-
Aoki, Y., Suzuki, Y., Li, X., Sakamoto, O., Chikaoka, H., Takita, S., and Narisawa, K. (1997) Pediatr. Res. 42, 849-854
-
(1997)
Pediatr. Res.
, vol.42
, pp. 849-854
-
-
Aoki, Y.1
Suzuki, Y.2
Li, X.3
Sakamoto, O.4
Chikaoka, H.5
Takita, S.6
Narisawa, K.7
-
37
-
-
0032755928
-
-
Sakamoto, O., Suzuki, Y., Li, X., Aoki, Y., Hiratsuka, M., Suormala, T., Baumgartner, E. R., Gibson, K. M., and Narisawa, K. (1999) Pediatr. Res. 46, 671-676
-
(1999)
Pediatr. Res.
, vol.46
, pp. 671-676
-
-
Sakamoto, O.1
Suzuki, Y.2
Li, X.3
Aoki, Y.4
Hiratsuka, M.5
Suormala, T.6
Baumgartner, E.R.7
Gibson, K.M.8
Narisawa, K.9
-
38
-
-
0027982429
-
-
Suzuki, Y., Aoki, Y., Ishida, Y., Chiba, Y., Iwamatsu, A., Kishino, T., Niikawa, N., Matsubara, Y., and Narisawa, K. (1994) Nat. Genet. 8, 122-128
-
(1994)
Nat. Genet.
, vol.8
, pp. 122-128
-
-
Suzuki, Y.1
Aoki, Y.2
Ishida, Y.3
Chiba, Y.4
Iwamatsu, A.5
Kishino, T.6
Niikawa, N.7
Matsubara, Y.8
Narisawa, K.9
-
39
-
-
0029593595
-
-
Aoki, Y., Suzuki, Y., Sakamoto, O., Li, X., Takahashi, K., Ohtake, A., Sakuta, R., Ohura, T., Miyabayashi, S., and Narisawa, K. (1995) Biochim. Biophys. Acta 1272, 168-174
-
(1995)
Biochim. Biophys. Acta
, vol.1272
, pp. 168-174
-
-
Aoki, Y.1
Suzuki, Y.2
Sakamoto, O.3
Li, X.4
Takahashi, K.5
Ohtake, A.6
Sakuta, R.7
Ohura, T.8
Miyabayashi, S.9
Narisawa, K.10
-
40
-
-
0026022605
-
-
Elledge, S. J., Mulligan, J. T., Ramer, S. W., Spottswood, M., and Davis, R. W. (1991) Proc. Natl. Acad. Sci. U. S. A. 88, 1731-1735
-
(1991)
Proc. Natl. Acad. Sci. U. S. A.
, vol.88
, pp. 1731-1735
-
-
Elledge, S.J.1
Mulligan, J.T.2
Ramer, S.W.3
Spottswood, M.4
Davis, R.W.5
-
43
-
-
0032731352
-
-
Polyak, S. W., Chapman-Smith, A., Brautigan, P. J., and Wallace, J. C. (1999) J. Biol. Chem. 274, 32847-32854
-
(1999)
J. Biol. Chem.
, vol.274
, pp. 32847-32854
-
-
Polyak, S.W.1
Chapman-Smith, A.2
Brautigan, P.J.3
Wallace, J.C.4
-
45
-
-
0029565346
-
-
Xu, Y., Nenortas, E., and Beckett, D. (1995) Biochemistry 34, 16624-16631
-
(1995)
Biochemistry
, vol.34
, pp. 16624-16631
-
-
Xu, Y.1
Nenortas, E.2
Beckett, D.3
-
52
-
-
0030586243
-
-
Suzuki, Y., Aoki, Y., Sakamoto, O., Li, X., Miyabayashi, S., Kazuta, Y., Kondo, H., and Narisawa, K. (1996) Clin. Chim. Acta 251, 41-52
-
(1996)
Clin. Chim. Acta
, vol.251
, pp. 41-52
-
-
Suzuki, Y.1
Aoki, Y.2
Sakamoto, O.3
Li, X.4
Miyabayashi, S.5
Kazuta, Y.6
Kondo, H.7
Narisawa, K.8
|