Altered atrial, atrioventricular, and ventricular conduction in patients with the long QT syndrome caused by the ΔKPQ SCN5A sodium channel gene mutation

American Journal of Cardiology

Volumn 88, Issue 11, 2001, Pages 1311-1314

  Zareba, Wojciech ^a,b   Sattari, Mehdi N ^a   Rosero, Spencer ^a   Couderc, Jean Philippe ^a   Moss, Arthur J ^a  

^a UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

^b UNIVERSITY OF ROCHESTER   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

SODIUM CHANNEL;

ADOLESCENT; ADULT; ATRIOVENTRICULAR CONDUCTION; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; GENE EXPRESSION; GENE MUTATION; GENOTYPE; HEART ATRIUM CONDUCTION; HEART VENTRICLE CONDUCTION; HUMAN; LONG QT SYNDROME; MALE; P WAVE; PHENOTYPE; PR INTERVAL; PRIORITY JOURNAL; QRS COMPLEX; REPOLARIZATION; REVIEW; SCHOOL CHILD;

EID: 0035584772     PISSN: 00029149     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0002-9149(01)02097-5     Document Type: Article

References (15)

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4. Molecular mechanism for an inherited cardiac arrhythmia
5. Characterization of human cardiac Na+ channel mutations in the congenital long QT syndrome
6. Lidocaine block of LQT3 mutant human Na+ channels
7. Cardiac conduction defects associate with mutations in SCN5A
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9. A TTX-sensitive inward sodium current contributes to spontaneous activity in newborn rabbit sino-atrial node cells
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13. A sodium-channel mutation causes isolated cardiac conduction disease
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