Reduction of menkes mRNA and copper in leukocytes of patients with primary adult-onset dystonia

Annals of Neurology

Volumn 49, Issue 3, 2001, Pages 405-408

  Kruse, Niels ^a   Berg, Daniela ^b   Francis, Michael J ^c   Naumann, Markus ^b   Rausch, Wolf Dieter ^c   Reiners, K ^a   Rieckmann, Peter ^b   Weishaupt, Andreas ^a   Becker, Georg ^a  

^a UNIVERSITY OF WÜRZBURG   (Germany)

^b UNIVERSITY OF OXFORD   (United Kingdom)

^c UNIVERSITY OF VETERINARY MEDICINE   (Austria)

Author keywords

[No Author keywords available]

Indexed keywords

CARRIER PROTEIN; MESSENGER RNA; PROTEIN MENKES; UNCLASSIFIED DRUG;

ADULT; ARTICLE; BASAL GANGLION; BLEPHAROSPASM; CLINICAL ARTICLE; COPPER BLOOD LEVEL; COPPER METABOLISM; DYSTONIA; FEMALE; HUMAN; LEUKOCYTE; MALE; PRIORITY JOURNAL;

EID: 0035094281     PISSN: 03645134     EISSN: None     Source Type: Journal    
DOI: 10.1002/ana.80     Document Type: Article

References (15)

1. Increased tissue copper and manganese content in the lentiform nucleus in primary adult-onset dystonia
2. Changes of copper-transporting proteins and ceruloplasmin in the lentiform nuclei in primary adult-onset dystonia
3. Lenticular nucleus lesion in idiopathic dystonia detected by transcranial sonography
4. Comparison of transcranial sonography, magnetic resonance imaging, and single photon emission computed tomography findings in idiopathic spasmodic torticollis
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7. Opiare receptor: Multiple effects of meral ions
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14. Kinky hair disease: Twenty five years later
15. An X-linked disease of the nervous system with disordered copper metabolism and features differing from Menkes disease