Familial amyotrophic lateral sclerosis and Cu/Zn superoxide dismutase mutation

Neuropathology

Volumn 17, Issue 4, 1997, Pages 255-262

  Shibata, Noriyuki ^a   Kobayashi, Makio ^a  

^a TOKYO WOMEN'S MEDICAL UNIVERSITY   (Japan)

Author keywords

Amyotrophic lateral sclerosis; Biochemistry; Immunocytochemistry; Molecular genetics; Superoxide dismutase; Transgenic mouse model

Indexed keywords

COPPER ION; COPPER ZINC SUPEROXIDE DISMUTASE; PEROXIDASE; PEROXYNITRITE; TYROSINE; ZINC ION;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; APOPTOSIS; AUTOSOMAL DOMINANT INHERITANCE; BIOCHEMISTRY; CELL VACUOLE; DEGENERATIVE DISEASE; DISEASE COURSE; DISEASE SEVERITY; ENZYME ACTIVITY; FAMILIAL DISEASE; GENE MUTATION; HOMOZYGOTE; IMMUNOCYTOCHEMISTRY; LEWY BODY; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NERVE CELL; NITRATION; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; REVIEW; TRANSGENIC MOUSE;

EID: 0031474385     PISSN: 09196544     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1440-1789.1997.tb00050.x     Document Type: Review

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