Specific substrate for CLN2 protease/tripeptidyl-peptidase I assay

European Journal of Paediatric Neurology

Volumn 5, Issue SUPPL. A, 2001, Pages 63-68

  Junaid, M A ^a   Brooks, S S ^a   Pullarkat, R K ^a  

^a NEW YORK STATE INSTITUTE FOR BASIC RESEARCH IN DEVELOPMENTAL DISABILITIES   (United States)

Author keywords

Acid protease; CLN2 protease; Late infantile neuronal ceroid lipofuscinosis; Pepstatin insensitive; Tripeptidyl peptidase I

Indexed keywords

ALANYLALANYLPHENYLALANYL 7 AMINO 4 METHYLCOUMARIN; AMINO ACID; CLN 2 PROTEASE; COUMARIN DERIVATIVE; FLUORESCEIN ISOTHIOCYANATE; GLYCYLPHENYLALANYLPHENYLALANYLLEUCYL 7 AMINO 4 METHYLCOUMARIN; LYSOSOME ENZYME; PEPTIDASE; PROTEINASE; TRIPEPTIDE; TRIPEPTIDYL PEPTIDASE I; UNCLASSIFIED DRUG;

AMINO TERMINAL SEQUENCE; ARTICLE; CHEMICAL BOND; CONTROLLED STUDY; DEGENERATIVE DISEASE; DIAGNOSIS; ENZYME ACTIVITY; ENZYME ASSAY; ENZYME SPECIFICITY; ENZYME SUBSTRATE; FATALITY; GENE MUTATION; GENETIC CODE; HETEROZYGOTE; HUMAN; HUMAN CELL; HUMAN TISSUE; LEUKOCYTE; NEURONAL CEROID LIPOFUSCINOSIS; ONSET AGE; PERINATAL PERIOD; PRENATAL DIAGNOSIS; PRIORITY JOURNAL; PROTEIN DEGRADATION; SYMPTOM;

EID: 0034921961     PISSN: 10903798     EISSN: None     Source Type: Journal    
DOI: 10.1053/ejpn.2000.0437     Document Type: Article

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