The structure of the N-terminal actin-binding domain of human dystrophin and how mutations in this domain may cause Duchenne or Becker muscular dystrophy

Structure

Volumn 8, Issue 5, 2000, Pages 481-491

  Norwood, Fiona L M ^a   Sutherland Smith, Andrew J ^a   Keep, Nicholas H ^a,b   Kendrick Jones, John ^a  

^a MRC LABORATORY OF MOLECULAR BIOLOGY   (United Kingdom)

^b UNIVERSITY OF LONDON   (United Kingdom)

Author keywords

Actin binding; Calponin homology domain; Dystrophin; Muscular dystrophy; Utrophin

Indexed keywords

ACTIN BINDING PROTEIN; CALPONIN; DYSTROPHIN; UTROPHIN;

AMINO TERMINAL SEQUENCE; ARTICLE; BECKER MUSCULAR DYSTROPHY; CYTOSKELETON; DUCHENNE MUSCULAR DYSTROPHY; GENE MUTATION; HUMAN; MUSCLE CELL; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN DOMAIN; SEQUENCE HOMOLOGY;

EID: 0034657791     PISSN: 09692126     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0969-2126(00)00132-5     Document Type: Article

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