Molecular basis of a progressive juvenile-onset hereditary cataract

Proceedings of the National Academy of Sciences of the United States of America

Volumn 97, Issue 5, 2000, Pages 1993-1998

  Pande, Ajay ^a   Pande, Jayanti ^a   Asherie, Neer ^a   Lomakin, Aleksey ^a   Ogun, Olutayo ^a   King, Jonathan A ^a   Lubsen, Nicolette H ^b   Walton, David ^c   Benedek, George B ^a  

^a USA   (United States)

^b RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^c MASSACHUSETTS EYE AND EAR INFIRMARY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ARGININE; CYSTEINE; DIMER; GAMMA CRYSTALLIN; MUTANT PROTEIN; RECOMBINANT PROTEIN;

AMINO ACID SUBSTITUTION; ARTICLE; CATARACT; CATARACTOGENESIS; CIRCULAR DICHROISM; DIFFERENTIAL SCANNING CALORIMETRY; DISULFIDE BOND; FETUS; FLUORESCENCE; HEREDITY; HUMAN; JUVENILE; OLIGOMERIZATION; ONSET AGE; PHASE SEPARATION; POINT MUTATION; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN STABILITY; PROTEIN STRUCTURE; SEQUENCE HOMOLOGY;

ADOLESCENT; AGE OF ONSET; ANIMALS; ARGININE; CATARACT; CATTLE; CRYSTALLINS; CYSTEINE; HUMANS; MODELS, MOLECULAR; PROTEIN STRUCTURE, SECONDARY; PROTEIN STRUCTURE, TERTIARY;

ESCHERICHIA COLI;

EID: 0034050880     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.040554397     Document Type: Article

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