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Volumn 47, Issue 2, 2000, Pages 271-277

Formation of L-alloisoleucine in vivo: An L-[13C]isoleucine study in man

Author keywords

[No Author keywords available]

Indexed keywords

ALLOISOLEUCINE; CARBON 13; ISOLEUCINE;

EID: 0033973996     PISSN: 00313998     EISSN: None     Source Type: Journal    
DOI: 10.1203/00006450-200002000-00020     Document Type: Article
Times cited : (11)

References (37)
  • 2
    • 0001106274 scopus 로고
    • Disorders of branched chain amino acid and keto acid metabolism
    • Scriver CR, Beaudet AL, Sly WS, Valle D (eds) McGraw Hill, New York
    • Chuang DT, Shih VE 1995 Disorders of branched chain amino acid and keto acid metabolism. In: Scriver CR, Beaudet AL, Sly WS, Valle D (eds) The Metabolic and Molecular Bases of Inherited Disease. McGraw Hill, New York, pp 1239-1277
    • (1995) The Metabolic and Molecular Bases of Inherited Disease , pp. 1239-1277
    • Chuang, D.T.1    Shih, V.E.2
  • 3
    • 0010757820 scopus 로고
    • Maple syrup urine disease: Branched-chain keto-aciduria
    • Dancis J, Levitz M, Westall RG 1960 Maple syrup urine disease: branched-chain keto-aciduria. Pediatrics 25:72-79
    • (1960) Pediatrics , vol.25 , pp. 72-79
    • Dancis, J.1    Levitz, M.2    Westall, R.G.3
  • 5
    • 0014869286 scopus 로고
    • The configuration of the alloisoleucine present in maple syrup urine disease plasma
    • Halpern B, Pollock GE 1970 The configuration of the alloisoleucine present in maple syrup urine disease plasma. Biochem Med 4:352-356
    • (1970) Biochem Med , vol.4 , pp. 352-356
    • Halpern, B.1    Pollock, G.E.2
  • 6
    • 0017029194 scopus 로고
    • Investigation of the metabolic pattern in maple syrup urine disease by means of glass capillary gas chromatography and mass spectrometry
    • Jakobs C, Solem E, Ek J, Halvorsen K, Jellum E 1977 Investigation of the metabolic pattern in maple syrup urine disease by means of glass capillary gas chromatography and mass spectrometry. J Chromatogr 143:31-38
    • (1977) J Chromatogr , vol.143 , pp. 31-38
    • Jakobs, C.1    Solem, E.2    Ek, J.3    Halvorsen, K.4    Jellum, E.5
  • 7
    • 0018954107 scopus 로고
    • Origin of the two peaks for 2-keto-3-methylvaleric acid produced by the oxidation of the keto acids occurring in maple syrup urine disease
    • Mamer OA, Montgomery JA, Taguchi VY 1980 Origin of the two peaks for 2-keto-3-methylvaleric acid produced by the oxidation of the keto acids occurring in maple syrup urine disease. J Chromatogr 182:221-225
    • (1980) J Chromatogr , vol.182 , pp. 221-225
    • Mamer, O.A.1    Montgomery, J.A.2    Taguchi, V.Y.3
  • 8
    • 0030581167 scopus 로고    scopus 로고
    • Determination of R-and S-3-methyl-2-oxopentanoate enantiomers in human plasma: Suitable method for label enrichment analysis
    • Schadewaldt P, Wendel U, Hammen H-W 1996 Determination of R-and S-3-methyl-2-oxopentanoate enantiomers in human plasma: suitable method for label enrichment analysis. J Chromatogr B 682:209-218
    • (1996) J Chromatogr B , vol.682 , pp. 209-218
    • Schadewaldt, P.1    Wendel, U.2    Hammen, H.-W.3
  • 9
    • 0017085714 scopus 로고
    • Demonstration of a new mammalian isoleucine catabolic pathway yielding an R series of metabolites
    • Mamer OA, Tjoa SS, Scriver CR, Klassen GA 1976 Demonstration of a new mammalian isoleucine catabolic pathway yielding an R series of metabolites. Biochem J 160:417-426
    • (1976) Biochem J , vol.160 , pp. 417-426
    • Mamer, O.A.1    Tjoa, S.S.2    Scriver, C.R.3    Klassen, G.A.4
  • 10
    • 0017154417 scopus 로고
    • Long-term management of a case of carbamyl phosphate synthetase deficiency using ketoanalogues and hydroxyanalogues of essential amino acids
    • Batshaw ML, Brusilow S, Walser M 1976 Long-term management of a case of carbamyl phosphate synthetase deficiency using ketoanalogues and hydroxyanalogues of essential amino acids. Pediatrics 58:227-235
    • (1976) Pediatrics , vol.58 , pp. 227-235
    • Batshaw, M.L.1    Brusilow, S.2    Walser, M.3
  • 11
    • 0000516952 scopus 로고
    • Growth response of the rat to the keto analogues of leucine and isoleucine
    • Meister A, White J 1951 Growth response of the rat to the keto analogues of leucine and isoleucine. J Biol Chem 191:211-216
    • (1951) J Biol Chem , vol.191 , pp. 211-216
    • Meister, A.1    White, J.2
  • 12
    • 0001760204 scopus 로고
    • Maple syrup urine disease with particular reference to dietotherapy
    • Snyderman SE, Norton PM, Roitman E, Holt Jr LE 1964 Maple syrup urine disease with particular reference to dietotherapy. Pediatrics 34:454-462
    • (1964) Pediatrics , vol.34 , pp. 454-462
    • Snyderman, S.E.1    Norton, P.M.2    Roitman, E.3    Holt L.E., Jr.4
  • 13
    • 0026564150 scopus 로고
    • On the mechanism of the formation of L-alloisoleucine and the 2-hydroxy-3-methylvaleric acid stereoisomers from L-isoleucine in maple syrup urine disease patients and in normal humans
    • Mamer OA, Reimer MLJ 1992 On the mechanism of the formation of L-alloisoleucine and the 2-hydroxy-3-methylvaleric acid stereoisomers from L-isoleucine in maple syrup urine disease patients and in normal humans. J Biol Chem 267:22141-22147
    • (1992) J Biol Chem , vol.267 , pp. 22141-22147
    • Mamer, O.A.1    Reimer, M.L.J.2
  • 14
    • 0018904353 scopus 로고
    • Alloisoleucine formation in maple syrup urine disease: Isotopic evidence for the mechanism
    • Matthews DE, Ben-Galim E, Haymond MW, Bier DM 1980 Alloisoleucine formation in maple syrup urine disease: isotopic evidence for the mechanism. Pediatr Res 14:854-857
    • (1980) Pediatr Res , vol.14 , pp. 854-857
    • Matthews, D.E.1    Ben-Galim, E.2    Haymond, M.W.3    Bier, D.M.4
  • 15
    • 0028979695 scopus 로고
    • Human branched-chain L-amino acid aminotransferase: Activity and subcellular localization in cultured skin fibroblasts
    • Schadewaldt P, Wendel U, Hammen H-W 1995 Human branched-chain L-amino acid aminotransferase: activity and subcellular localization in cultured skin fibroblasts. Amino Acids 9:147-160
    • (1995) Amino Acids , vol.9 , pp. 147-160
    • Schadewaldt, P.1    Wendel, U.2    Hammen, H.-W.3
  • 16
    • 0004837247 scopus 로고
    • Studies on D-and L-α-keto-β-methylvaleric acids
    • Meister A 1951 Studies on D-and L-α-keto-β-methylvaleric acids. J Biol Chem 190:269-276
    • (1951) J Biol Chem , vol.190 , pp. 269-276
    • Meister, A.1
  • 17
    • 0017355846 scopus 로고
    • Racemization and amination of the keto-analog of isoleucine in the intact dog
    • Weinberg RB, Walser M 1977 Racemization and amination of the keto-analog of isoleucine in the intact dog. Biochem Med 17:164-172
    • (1977) Biochem Med , vol.17 , pp. 164-172
    • Weinberg, R.B.1    Walser, M.2
  • 19
    • 0025307367 scopus 로고
    • On the mechanism of L-alloisoleucine formation: Studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease
    • Schadewaldt P, Hammen H-W, Dalle-Feste C, Wendel U 1990 On the mechanism of L-alloisoleucine formation: studies on a healthy subject and in fibroblasts from normals and patients with maple syrup urine disease. J Inher Metab Dis 13:137-150
    • (1990) J Inher Metab Dis , vol.13 , pp. 137-150
    • Schadewaldt, P.1    Hammen, H.-W.2    Dalle-Feste, C.3    Wendel, U.4
  • 20
    • 0022460782 scopus 로고
    • Resolution of D-and L-amino acids after precolumn derivatization with 0-phthalaldehyde by mixed chelation with Cu(II)-L-proline
    • Lam S 1986 Resolution of D-and L-amino acids after precolumn derivatization with 0-phthalaldehyde by mixed chelation with Cu(II)-L-proline. J Chromatogr 355:157-164
    • (1986) J Chromatogr , vol.355 , pp. 157-164
    • Lam, S.1
  • 21
    • 0026010306 scopus 로고
    • Oral L-alloisoleucine loading studies in healthy subjects and in patients with maple syrup urine disease
    • Schadewaldt P, Dalle-Feste C, Langenbeck U, Wendel U 1991 Oral L-alloisoleucine loading studies in healthy subjects and in patients with maple syrup urine disease. Pediatr Res 30:430-434
    • (1991) Pediatr Res , vol.30 , pp. 430-434
    • Schadewaldt, P.1    Dalle-Feste, C.2    Langenbeck, U.3    Wendel, U.4
  • 24
    • 0024545076 scopus 로고
    • Interrelation between the metabolism of L-isoleucine and L-allo-isoleucine in patients with maple syrup urine disease
    • Wendel U, Langenbeck U, Seakins JWT 1989 Interrelation between the metabolism of L-isoleucine and L-allo-isoleucine in patients with maple syrup urine disease. Pediatr Res 25:11-14
    • (1989) Pediatr Res , vol.25 , pp. 11-14
    • Wendel, U.1    Langenbeck, U.2    Seakins, J.W.T.3
  • 25
    • 0009554232 scopus 로고
    • Studies in maple syrup urine disease
    • Dent CE, Westall RG 1961 Studies in maple syrup urine disease. Arch Dis Child 36:259-268
    • (1961) Arch Dis Child , vol.36 , pp. 259-268
    • Dent, C.E.1    Westall, R.G.2
  • 26
    • 0023635407 scopus 로고
    • Utilization of the L-and DL-isomers of α-keto-β-methylvaleric acid by rats and comparative efficacy of the keto analogs of branched-chain amino acids provided as omithine, lysine and histidine salts
    • Funk MA, Lowry KR, Baker DH 1987 Utilization of the L-and DL-isomers of α-keto-β-methylvaleric acid by rats and comparative efficacy of the keto analogs of branched-chain amino acids provided as omithine, lysine and histidine salts. J Nutr 117:1550-1555
    • (1987) J Nutr , vol.117 , pp. 1550-1555
    • Funk, M.A.1    Lowry, K.R.2    Baker, D.H.3
  • 28
    • 0017661095 scopus 로고
    • Isoenzyme patterns of branched-chain amino acid transaminase in human tissues and tumors
    • Goto M, Shinno H, Ichihara A 1977 Isoenzyme patterns of branched-chain amino acid transaminase in human tissues and tumors. Gann 68:663-667
    • (1977) Gann , vol.68 , pp. 663-667
    • Goto, M.1    Shinno, H.2    Ichihara, A.3
  • 30
    • 0024215484 scopus 로고
    • Measurement of plasma and tissue levels of branched-chain a-keto acids by gas-liquid chromatography
    • Crowell PL, Miller RH, Harper AE 1988 Measurement of plasma and tissue levels of branched-chain a-keto acids by gas-liquid chromatography. Methods Enzymol 166:39-46
    • (1988) Methods Enzymol , vol.166 , pp. 39-46
    • Crowell, P.L.1    Miller, R.H.2    Harper, A.E.3
  • 31
    • 0027314007 scopus 로고
    • Arteriovenous differences and tissue concentrations of branched-chain ketoacids
    • Matuso Y, Yagi M, Walser M 1993 Arteriovenous differences and tissue concentrations of branched-chain ketoacids J Lab Clin Med 121:779-784
    • (1993) J Lab Clin Med , vol.121 , pp. 779-784
    • Matuso, Y.1    Yagi, M.2    Walser, M.3
  • 33
    • 0030023284 scopus 로고    scopus 로고
    • Infusion of labeled K1C is more accurate than labeled leucine to determine human muscle protein synthesis
    • Chinkes D, Klein S, Zhang X-J, Wolfe RR 1996 Infusion of labeled K1C is more accurate than labeled leucine to determine human muscle protein synthesis. Am J Physiol 270:E67-E71
    • (1996) Am J Physiol , vol.270
    • Chinkes, D.1    Klein, S.2    Zhang, X.-J.3    Wolfe, R.R.4
  • 34
    • 0023863055 scopus 로고
    • Transamination and oxidative decarboxylation rates of branched-chain 2-oxo acids in cultured human skin fibroblasts
    • Schadewaldt P, Radeck W, Hammen H-W, Wendel U 1988 Transamination and oxidative decarboxylation rates of branched-chain 2-oxo acids in cultured human skin fibroblasts. Pediatr Res 23:40-44
    • (1988) Pediatr Res , vol.23 , pp. 40-44
    • Schadewaldt, P.1    Radeck, W.2    Hammen, H.-W.3    Wendel, U.4
  • 35
    • 0024340092 scopus 로고
    • Transamination and oxidative decarboxylation of L-isoleucine, L-alloisoleucine and related 2-oxo acids in perfused rat hind limb muscle
    • Schadewaldt P, Radeck W, Hammen H-W, Staib W 1989 Transamination and oxidative decarboxylation of L-isoleucine, L-alloisoleucine and related 2-oxo acids in perfused rat hind limb muscle. Biochim Biophys Acta 992:115-123
    • (1989) Biochim Biophys Acta , vol.992 , pp. 115-123
    • Schadewaldt, P.1    Radeck, W.2    Hammen, H.-W.3    Staib, W.4
  • 36
    • 0343027673 scopus 로고
    • Über das vorkommen von äthylmalonsäure im harn
    • Stalder K 1959 Über das Vorkommen von Äthylmalonsäure im Harn. Hoppe-Seyler's Z Physiol Chem 314:205-210
    • (1959) Hoppe-Seyler's Z Physiol Chem , vol.314 , pp. 205-210
    • Stalder, K.1
  • 37
    • 0032771536 scopus 로고    scopus 로고
    • Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease
    • Schadewaldt P, Hammen H-W, Ott A-C, Wendel U 1999 Renal clearance of branched-chain L-amino and 2-oxo acids in maple syrup urine disease. J Inherit Metab Dis 22:706-722
    • (1999) J Inherit Metab Dis , vol.22 , pp. 706-722
    • Schadewaldt, P.1    Hammen, H.-W.2    Ott, A.-C.3    Wendel, U.4


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