Functional hyperactivity of hepatic glutamate dehydrogenase as a cause of the hyperinsulinism/hyperammonemia syndrome: Effect of treatment

Pediatrics

Volumn 106, Issue 3, 2000, Pages 596-600

  Huijmans, Jan G M ^a   Duran, Marinus ^a,b   De Klerk, Johannis B C ^a,c   Rovers, Marinus J ^d   Scholte, Hans R ^a  

^a ERASMUS UNIVERSITY ROTTERDAM   (Netherlands)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c SOPHIA CHILDREN S HOSPITAL   (Netherlands)

^d Department of Surgery   (Netherlands)

Author keywords

Glutamate dehydrogenase; Hyperammonemia; Hyperinsulinism; Plasma glutamine

Indexed keywords

2 OXOGLUTARIC ACID; AMMONIA; DIAZOXIDE; GLUCOSE; GLUTAMATE AMMONIA LIGASE; GLUTAMATE DEHYDROGENASE; GLUTAMIC ACID; GLUTAMIC ACID DERIVATIVE; GLUTAMINE; GUANOSINE TRIPHOSPHATE; INSULIN; N ACETYLGLUTAMIC ACID; N CARBAMYLGLUTAMIC ACID; UNCLASSIFIED DRUG;

AMMONIA BLOOD LEVEL; ARTICLE; CASE REPORT; ENZYME ACTIVITY; FEMALE; GLUCOSE BLOOD LEVEL; HUMAN; HUMAN CELL; HUMAN TISSUE; HYPERAMMONEMIA; HYPERINSULINISM; HYPOGLYCEMIA; INSULIN BLOOD LEVEL; LIVER BIOPSY; LYMPHOCYTE; PRIORITY JOURNAL; PROTEIN INTAKE; SCHOOL CHILD; UREA CYCLE;

EID: 0033842369     PISSN: 00314005     EISSN: None     Source Type: Journal    
DOI: 10.1542/peds.106.3.596     Document Type: Article

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