Hemolytic uremic syndrome associated with Denys-Drash syndrome

Pediatric Nephrology

Volumn 14, Issue 12, 2000, Pages 1092-1097

  Sherbotie, J R ^a   Van Heyningen, V ^b   Axton, R ^b   Williamson, K ^b   Finn, L S ^a   Kaplan, B S ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b WESTERN GENERAL HOSPITAL   (United Kingdom)

Author keywords

Denys Drash syndrome; Diffuse mesangial sclerosis; Hemolytic uremic syndrome; Pseudohermaphroditism; Wilms' tumor; WT1 mutation

Indexed keywords

DNA; ZINC FINGER PROTEIN;

ARTICLE; CASE REPORT; CHILD; CLINICAL FEATURE; DENYS DRASH SYNDROME; DISEASE ASSOCIATION; DNA DETERMINATION; GENE MUTATION; HEMOLYTIC UREMIC SYNDROME; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INFANT; KIDNEY TRANSPLANTATION; MALE; PATHOGENESIS; POINT MUTATION; PRIORITY JOURNAL; TUMOR SUPPRESSOR GENE;

BASE SEQUENCE; DNA; DNA-BINDING PROTEINS; GLOMERULAR MESANGIUM; GLOMERULOSCLEROSIS, FOCAL SEGMENTAL; HEMOLYTIC-UREMIC SYNDROME; HUMANS; INFANT; KIDNEY; KIDNEY FAILURE, CHRONIC; MALE; MOLECULAR SEQUENCE DATA; MUTATION; NEPHROTIC SYNDROME; PSEUDOHERMAPHRODITISM; SYNDROME; TRANSCRIPTION FACTORS; WILMS TUMOR; WT1 PROTEINS;

EID: 0033819394     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004670000389     Document Type: Article

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