Simple models of threshold curves in the expression of inborn errors of metabolism: Application to some experimental observations

Developmental Neuroscience

Volumn 22, Issue 5-6, 2000, Pages 399-403

  Mazat, Jean Pierre ^a   Rossignol, Rodrigue ^a   Malgat, Monique ^a   Letellier, Thierry ^a  

^a INSERM   (France)

Author keywords

Inborn errors of metabolism; Mathematical modelling; Metabolic control theory; Mitochondria; Mitochondrial diseases; Oxidative phosphorylation

Indexed keywords

ARTICLE; ENZYME ACTIVITY; ENZYME METABOLISM; GENE EXPRESSION; INBORN ERROR OF METABOLISM; MATHEMATICAL ANALYSIS; MATHEMATICAL MODEL; MITOCHONDRION; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; PROTEIN TRANSPORT; RESPIRATORY CHAIN;

COMPUTER SIMULATION; ELECTRON TRANSPORT; ELECTRON TRANSPORT COMPLEX I; HUMANS; KINETICS; METABOLISM, INBORN ERRORS; MITOCHONDRIA; MITOCHONDRIAL MYOPATHIES; MODELS, BIOLOGICAL; NADH, NADPH OXIDOREDUCTASES; OXIDATIVE PHOSPHORYLATION;

EID: 0033668115     PISSN: 03785866     EISSN: None     Source Type: Journal    
DOI: 10.1159/000017469     Document Type: Article

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