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Volumn 35, Issue 11, 1999, Pages 835-848

Cystic fibrosis: A decade of progress

Author keywords

[No Author keywords available]

Indexed keywords

ANTIBIOTIC AGENT; DORNASE ALFA; IBUPROFEN; TOBRAMYCIN; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 0033388777     PISSN: 16993993     EISSN: 16994019     Source Type: Journal    
DOI: 10.1358/dot.1999.35.11.562557     Document Type: Review
Times cited : (4)

References (71)
  • 1
    • 0000471085 scopus 로고
    • Cystic fibrosis of the pancreas and its relation to celiac disease
    • Andersen, D.H. Cystic fibrosis of the pancreas and its relation to celiac disease. Am J Dis Child 1938, 56: 344-99.
    • (1938) Am J Dis Child , vol.56 , pp. 344-399
    • Andersen, D.H.1
  • 2
    • 84920211040 scopus 로고
    • Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas
    • di Sant'Agnese, P.A., Darling, R.C., Perera, G.A., Shea, E. Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas. Pediatrics 1953, 12: 549-63.
    • (1953) Pediatrics , vol.12 , pp. 549-563
    • Di Sant'Agnese, P.A.1    Darling, R.C.2    Perera, G.A.3    Shea, E.4
  • 5
    • 0032433707 scopus 로고    scopus 로고
    • Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
    • Matsui, H., Grubb, B.R., Tarran, R. et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 1998, 95: 1005-15.
    • (1998) Cell , vol.95 , pp. 1005-1015
    • Matsui, H.1    Grubb, B.R.2    Tarran, R.3
  • 6
    • 0033525780 scopus 로고    scopus 로고
    • Cystic fibrosis and the salt controversy
    • Guggino, W.B. Cystic fibrosis and the salt controversy. Cell 1999, 96: 607-10.
    • (1999) Cell , vol.96 , pp. 607-610
    • Guggino, W.B.1
  • 7
    • 0029934215 scopus 로고    scopus 로고
    • Management of pulmonary disease in patients with cystic fibrosis
    • Ramsey, B.W. Management of pulmonary disease in patients with cystic fibrosis. N Engl J Med 1996, 335: 179-88.
    • (1996) N Engl J Med , vol.335 , pp. 179-188
    • Ramsey, B.W.1
  • 8
    • 0031707429 scopus 로고    scopus 로고
    • Basic therapies in cystic fibrosis. Does standard therapy work?
    • Marshall, B.C., Samuelson, W.M. Basic therapies in cystic fibrosis. Does standard therapy work? Clin Chest Med 1998, 19: 487-504.
    • (1998) Clin Chest Med , vol.19 , pp. 487-504
    • Marshall, B.C.1    Samuelson, W.M.2
  • 10
    • 0026048329 scopus 로고
    • New insights on gastro-oesophageal reflux in cystic fibrosis by longitudinal follow up
    • Malfroot, A., Dab, I. New insights on gastro-oesophageal reflux in cystic fibrosis by longitudinal follow up. Arch Dis Child 1991, 66: 1339-45.
    • (1991) Arch Dis Child , vol.66 , pp. 1339-1345
    • Malfroot, A.1    Dab, I.2
  • 12
    • 0029928073 scopus 로고    scopus 로고
    • Clinical significance of the recovery of Aspergillus species from the respiratory secretions of cystic fibrosis patients
    • Milla, C.E., Wielinski, C.L., Regelmann, W.E. Clinical significance of the recovery of Aspergillus species from the respiratory secretions of cystic fibrosis patients. Pediatr Pulmonol 1996, 21: 6-10.
    • (1996) Pediatr Pulmonol , vol.21 , pp. 6-10
    • Milla, C.E.1    Wielinski, C.L.2    Regelmann, W.E.3
  • 13
    • 0005671362 scopus 로고    scopus 로고
    • Allergic bronchopulmonary aspergillosis in cystic fibrosis: Hole of atopy and response to itraconazole
    • Mepomuceno, I.B., Esrig, S., Moss, R.B. Allergic bronchopulmonary aspergillosis in cystic fibrosis: Hole of atopy and response to itraconazole. Chest 1999, 115: 364-70.
    • (1999) Chest , vol.115 , pp. 364-370
    • Mepomuceno, I.B.1    Esrig, S.2    Moss, R.B.3
  • 14
    • 0029758131 scopus 로고    scopus 로고
    • A 12-year longitudinal study of Aspergillus sensitivity in patients with cystic fibrosis
    • Hutcheson, P.S., Knutsen, A.P., Rejent, A.J., Slavin, R.G. A 12-year longitudinal study of Aspergillus sensitivity in patients with cystic fibrosis. Chest 1996, 110: 363-6.
    • (1996) Chest , vol.110 , pp. 363-366
    • Hutcheson, P.S.1    Knutsen, A.P.2    Rejent, A.J.3    Slavin, R.G.4
  • 15
    • 0031660253 scopus 로고    scopus 로고
    • Burkholderia cepacia management issues and new insights
    • LiPuma, J.J. Burkholderia cepacia management issues and new insights. Clin Chest Med 1998, 19: 473-86.
    • (1998) Clin Chest Med , vol.19 , pp. 473-486
    • LiPuma, J.J.1
  • 16
    • 0027564769 scopus 로고
    • Cystic fibrosis foundation consensus conference report on pulmonary complications of cystic fibrosis
    • Schidlow, D.V., Taussig, L.M., Knowles, M.R. Cystic fibrosis foundation consensus conference report on pulmonary complications of cystic fibrosis. Pediatr Pulmonol 1993, 15: 187-98.
    • (1993) Pediatr Pulmonol , vol.15 , pp. 187-198
    • Schidlow, D.V.1    Taussig, L.M.2    Knowles, M.R.3
  • 17
    • 0026760116 scopus 로고
    • Impact of sinusitis in cystic fibrosis
    • Ramsey, B., Richardson, M.A. Impact of sinusitis in cystic fibrosis. J Allergy Clin Immunol 1992, 90(3, Pt 2): 547-52.
    • (1992) J Allergy Clin Immunol , vol.90 , Issue.3 PT 2 , pp. 547-552
    • Ramsey, B.1    Richardson, M.A.2
  • 19
    • 0031766338 scopus 로고    scopus 로고
    • Management of chronic sinusitis in the adult cystic fibrosis patient
    • Halvorson, D.J., Dupree, J.R., Porubsky, E.S. Management of chronic sinusitis in the adult cystic fibrosis patient. Ann Otol Rhinol Laryngol 1998, 107: 946-52.
    • (1998) Ann Otol Rhinol Laryngol , vol.107 , pp. 946-952
    • Halvorson, D.J.1    Dupree, J.R.2    Porubsky, E.S.3
  • 20
    • 0031415196 scopus 로고    scopus 로고
    • Gastrointestinal manifestations of cystic fibrosis
    • Riedel, B.D. Gastrointestinal manifestations of cystic fibrosis. Pediatr Ann 1997, 26: 235-41.
    • (1997) Pediatr Ann , vol.26 , pp. 235-241
    • Riedel, B.D.1
  • 21
    • 0030008416 scopus 로고    scopus 로고
    • Fibrosing colonopathy in cystic fibrosis
    • Smyth, R.L. Fibrosing colonopathy in cystic fibrosis. Arch Dis Child 1996, 74: 164-8.
    • (1996) Arch Dis Child , vol.74 , pp. 164-168
    • Smyth, R.L.1
  • 23
    • 0030061325 scopus 로고    scopus 로고
    • Nutritional management of cystic fibrosis
    • MacDonald, A. Nutritional management of cystic fibrosis. Arch Dis Child 1996, 74: 81-7.
    • (1996) Arch Dis Child , vol.74 , pp. 81-87
    • MacDonald, A.1
  • 24
    • 0032938704 scopus 로고    scopus 로고
    • Atypical presentation of clostridium difficile colitis in patients with cystic fibrosis
    • Binkovitz, L.A., Allen, E., Bloom, D. et al. Atypical presentation of Clostridium difficile colitis in patients with cystic fibrosis. AJR Am J Roentgenol 1999, 172: 517-21.
    • (1999) AJR Am J Roentgenol , vol.172 , pp. 517-521
    • Binkovitz, L.A.1    Allen, E.2    Bloom, D.3
  • 25
    • 0031893534 scopus 로고    scopus 로고
    • Severe Clostridium difficile-associated colitis in young patients with cystic fibrosis
    • Rivlin, J., Lemer, A., Augarten, A., Wilschansid, M., Kerem, E., Ephros, M.A. Severe Clostridium difficile-associated colitis in young patients with cystic fibrosis. J Pediatr 1998, 132: 177-9.
    • (1998) J Pediatr , vol.132 , pp. 177-179
    • Rivlin, J.1    Lemer, A.2    Augarten, A.3    Wilschansid, M.4    Kerem, E.5    Ephros, M.A.6
  • 27
    • 0029174342 scopus 로고
    • Microfertilization techniques: The Swedish experience
    • Hamberger, L., Sjogren, A., Lundin, K. et al. Microfertilization techniques: The Swedish experience. Reprod Fertil Dev 1995, 7: 263-7.
    • (1995) Reprod Fertil Dev , vol.7 , pp. 263-267
    • Hamberger, L.1    Sjogren, A.2    Lundin, K.3
  • 28
    • 0031857361 scopus 로고    scopus 로고
    • Cystic fibrosis and reproduction
    • Phillipson, G. Cystic fibrosis and reproduction. Reprod Fertil Dev 1998, 10: 113-19.
    • (1998) Reprod Fertil Dev , vol.10 , pp. 113-119
    • Phillipson, G.1
  • 29
    • 0015885904 scopus 로고
    • Water and electrolytes in cervical mucus from patients with CF
    • Kopito, L.E., Kosasky, H.J., Shwachman, H. Water and electrolytes in cervical mucus from patients with CF. Fertil Steril 1973, 24: 512-6.
    • (1973) Fertil Steril , vol.24 , pp. 512-516
    • Kopito, L.E.1    Kosasky, H.J.2    Shwachman, H.3
  • 30
    • 0031666951 scopus 로고    scopus 로고
    • Female patients with cystic fibrosis suffer from reproductive endocrinological disorders despite good clinical status
    • Johannesson, M., Landgren, B.M., Csemiczky, G., Hjelte, L., Gottleib. C. Female patients with cystic fibrosis suffer from reproductive endocrinological disorders despite good clinical status. Hum Reprod 1998, 13: 2092-7.
    • (1998) Hum Reprod , vol.13 , pp. 2092-2097
    • Johannesson, M.1    Landgren, B.M.2    Csemiczky, G.3    Hjelte, L.4    Gottleib, C.5
  • 32
    • 0027991656 scopus 로고
    • Diabetes mellitus in cystic fibrosis: Effect of insulin therapy on lung function and infections
    • Lanng, S., Thorsteinsson, B., Nerup, J., Koch, C. Diabetes mellitus in cystic fibrosis: Effect of insulin therapy on lung function and infections. Acta Paediatr 1994, 83: 849-53.
    • (1994) Acta Paediatr , vol.83 , pp. 849-853
    • Lanng, S.1    Thorsteinsson, B.2    Nerup, J.3    Koch, C.4
  • 33
    • 0031903084 scopus 로고    scopus 로고
    • Abnormal glucose metabolism in cystic fibrosis
    • Moran, A., Doherty, L., Wang, X., Thomas, W. Abnormal glucose metabolism in cystic fibrosis. J Pediatr 1998, 133: 10-7.
    • (1998) J Pediatr , vol.133 , pp. 10-17
    • Moran, A.1    Doherty, L.2    Wang, X.3    Thomas, W.4
  • 34
    • 0028037759 scopus 로고
    • Prevalence of circulating immune complexes in patients with cystic fibrosis and arthritis
    • Wulffraat, N.K., de Graeff-Meeder, E.R., Rijkers, G.T., van der Laag, H., Kuis, W. Prevalence of circulating immune complexes in patients with cystic fibrosis and arthritis. J Pediatr 1994, 125: 374-8.
    • (1994) J Pediatr , vol.125 , pp. 374-378
    • Wulffraat, N.K.1    De Graeff-Meeder, E.R.2    Rijkers, G.T.3    Van Der Laag, H.4    Kuis, W.5
  • 35
    • 0031714774 scopus 로고    scopus 로고
    • Osteoporosis in patients with cystic fibrosis
    • Ott, S.M., Aitken, M.L. Osteoporosis in patients with cystic fibrosis. Clin Chest Med 1998, 19: 555-67.
    • (1998) Clin Chest Med , vol.19 , pp. 555-567
    • Ott, S.M.1    Aitken, M.L.2
  • 36
    • 0028129568 scopus 로고
    • Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
    • Fuchs, H.J., Borowitz, D.S., Christiansen, D.H. et al. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med 1994, 331: 637-42.
    • (1994) N Engl J Med , vol.331 , pp. 637-642
    • Fuchs, H.J.1    Borowitz, D.S.2    Christiansen, D.H.3
  • 37
    • 0030803202 scopus 로고    scopus 로고
    • Aerosolized dornase alfa in cystic fibrosis: Is there a role in the management of patients with early obstructive lung disease?
    • Geller, D.E. Aerosolized dornase alfa in cystic fibrosis: Is there a role in the management of patients with early obstructive lung disease? Pediatr Pulmonol 1997, 24: 155-8.
    • (1997) Pediatr Pulmonol , vol.24 , pp. 155-158
    • Geller, D.E.1
  • 38
    • 0028914667 scopus 로고
    • Effect of high-dose ibuprofen in patients with cystic fibrosis
    • Konstan, M.W., Byard, P.J., Hoppel, C.L., Davis, P.B. Effect of high-dose ibuprofen in patients with cystic fibrosis. N Engl J Med 1995, 332: 848-54.
    • (1995) N Engl J Med , vol.332 , pp. 848-854
    • Konstan, M.W.1    Byard, P.J.2    Hoppel, C.L.3    Davis, P.B.4
  • 39
    • 0033531143 scopus 로고    scopus 로고
    • Intermittent administration of inhaled tobramycin in patients with cystic fibrosis
    • Cystic Fibrosis Inhaled Tobramycin Study Group.
    • Ramsey, B.W., Pepe, M.S., Quan, J.M. et al. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group. N Engl J Med 1999, 340: 23-30.
    • (1999) N Engl J Med , vol.340 , pp. 23-30
    • Ramsey, B.W.1    Pepe, M.S.2    Quan, J.M.3
  • 40
    • 0031686497 scopus 로고    scopus 로고
    • Lung transplantation for cystic fibrosis
    • Zuckerman, J.B., Kotloff, R.M. Lung transplantation for cystic fibrosis. Clin Chest Med 1998, 19: 535-54.
    • (1998) Clin Chest Med , vol.19 , pp. 535-554
    • Zuckerman, J.B.1    Kotloff, R.M.2
  • 41
    • 0031973453 scopus 로고    scopus 로고
    • Lung transplantation in cystic fibrosis. Consensus conference statement
    • Yankaskas, J.R., Mallory, G.B. Jr. Lung transplantation in cystic fibrosis. Consensus conference statement. Chest 1998, 113: 217-26.
    • (1998) Chest , vol.113 , pp. 217-226
    • Yankaskas, J.R.1    Mallory G.B., Jr.2
  • 43
    • 0031950258 scopus 로고    scopus 로고
    • Risk of death in cystic fibrosis patients with severely compromised lung function
    • Milla, C.E., Warwick, W.J. Risk of death in cystic fibrosis patients with severely compromised lung function. Chest 1998, 113, 1230-34.
    • (1998) Chest , vol.113 , pp. 1230-1234
    • Milla, C.E.1    Warwick, W.J.2
  • 44
    • 0033032660 scopus 로고    scopus 로고
    • 1 may adversely affect overall survival
    • 1 may adversely affect overall survival. Chest 1999, 115: 782-7.
    • (1999) Chest , vol.115 , pp. 782-787
    • Doershuk, C.F.1    Stem, R.C.2
  • 45
    • 0026520359 scopus 로고
    • Prediction of mortality in patients with cystic fibrosis
    • Kerem, E., Reisman, J., Corey, M., Canny, G.J., Levison, H. Prediction of mortality in patients with cystic fibrosis. N Engl J Med 1992, 326: 1187-91.
    • (1992) N Engl J Med , vol.326 , pp. 1187-1191
    • Kerem, E.1    Reisman, J.2    Corey, M.3    Canny, G.J.4    Levison, H.5
  • 46
    • 0031940696 scopus 로고    scopus 로고
    • Cystic fibrosis: Bilateral living lobar versus cadaveric lung transplantation
    • Barbers, R.G. Cystic fibrosis: Bilateral living lobar versus cadaveric lung transplantation. Am J Med Sci 1998, 315: 155-60.
    • (1998) Am J Med Sci , vol.315 , pp. 155-160
    • Barbers, R.G.1
  • 47
    • 0024453308 scopus 로고
    • Identification of the cystic fibrosis gene: Chromosome walking and jumping
    • Rommens, J.M., Iannuzzi, M.C., Kerem, B. et al. Identification of the cystic fibrosis gene: Chromosome walking and jumping. Science 1989, 245: 1059-65.
    • (1989) Science , vol.245 , pp. 1059-1065
    • Rommens, J.M.1    Iannuzzi, M.C.2    Kerem, B.3
  • 48
    • 0024424270 scopus 로고
    • Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
    • Riordan, J.R., Rommens, J.M., Kerem, B. et al. Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA. Science 1989, 245: 1066-80.
    • (1989) Science , vol.245 , pp. 1066-1080
    • Riordan, J.R.1    Rommens, J.M.2    Kerem, B.3
  • 49
    • 0031718588 scopus 로고    scopus 로고
    • Clinical implications of cystic fibrosis transmembrane conductance regulator mutations
    • Mickle, J.E., Cutting, G.R. Clinical implications of cystic fibrosis transmembrane conductance regulator mutations. Clin Chest Med 1998, 19: 443-58.
    • (1998) Clin Chest Med , vol.19 , pp. 443-458
    • Mickle, J.E.1    Cutting, G.R.2
  • 50
    • 0032912589 scopus 로고    scopus 로고
    • Structure and function of the CFTR chloride channel
    • Sheppard, D.N., Welsh, M.J. Structure and function of the CFTR chloride channel. Physiol Rev 1999, 79: S23-45.
    • (1999) Physiol Rev , vol.79
    • Sheppard, D.N.1    Welsh, M.J.2
  • 51
    • 0031686496 scopus 로고    scopus 로고
    • What we know and what we do not know about cystic fibrosis transmembrane conductance regulator
    • Ma, J., Davis, P.B. What we know and what we do not know about cystic fibrosis transmembrane conductance regulator. Clin Chest Med 1998, 19: 459-71.
    • (1998) Clin Chest Med , vol.19 , pp. 459-471
    • Ma, J.1    Davis, P.B.2
  • 52
    • 0027966771 scopus 로고
    • Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents
    • Schwiebert, E.M., Flotte, T., Cutting, C.R., Guggino, W.B. Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents. Am J Physiol 1994, 266: C1464-77.
    • (1994) Am J Physiol , vol.266
    • Schwiebert, E.M.1    Flotte, T.2    Cutting, C.R.3    Guggino, W.B.4
  • 53
    • 0028982894 scopus 로고
    • CFTR as a cAMP-dependent regulator of sodium channels
    • Stutts, M.J., Canessa, C.M., Olsen, J.C. et al. CFTR as a cAMP-dependent regulator of sodium channels. Science 1995, 269: 847-50.
    • (1995) Science , vol.269 , pp. 847-850
    • Stutts, M.J.1    Canessa, C.M.2    Olsen, J.C.3
  • 54
    • 0027162649 scopus 로고
    • Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis
    • Welsh, M.J., Smith, A.E. Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis. Cell 1993, 73: 1251-54.
    • (1993) Cell , vol.73 , pp. 1251-1254
    • Welsh, M.J.1    Smith, A.E.2
  • 55
    • 0030473619 scopus 로고    scopus 로고
    • Genotype-phenotype correlations in cystic fibrosis
    • Kerem, E., Kerem, B. Genotype-phenotype correlations in cystic fibrosis. Pediatr Pulmonol 1996, 22: 387-95.
    • (1996) Pediatr Pulmonol , vol.22 , pp. 387-395
    • Kerem, E.1    Kerem, B.2
  • 56
    • 0031717590 scopus 로고    scopus 로고
    • Therapies directed at the basic defect in cystic fibrosis
    • Zeitlin, P.L. Therapies directed at the basic defect in cystic fibrosis. Clin Chest Med 1998, 19: 515-25.
    • (1998) Clin Chest Med , vol.19 , pp. 515-525
    • Zeitlin, P.L.1
  • 57
    • 0025641579 scopus 로고
    • Lung injury in cystic fibrosis
    • Elborn, J.S., Shale, D.J. Lung injury in cystic fibrosis. Thorax 1990, 45: 970-3.
    • (1990) Thorax , vol.45 , pp. 970-973
    • Elborn, J.S.1    Shale, D.J.2
  • 58
    • 0029286816 scopus 로고
    • Cystic fibrosis lung inflammation: Early, sustained, and severe
    • Cantin, A. Cystic fibrosis lung inflammation: Early, sustained, and severe. Am J Respir Crit Care Med 1995, 151: 939-41.
    • (1995) Am J Respir Crit Care Med , vol.151 , pp. 939-941
    • Cantin, A.1
  • 59
    • 0030881846 scopus 로고    scopus 로고
    • Current understanding of the inflammatory process in cystic fibrosis: Onset and etiology
    • Konstan, M.W., Berger, M. Current understanding of the inflammatory process in cystic fibrosis: Onset and etiology. Pediatr Pulmonol 1997, 24: 137-42.
    • (1997) Pediatr Pulmonol , vol.24 , pp. 137-142
    • Konstan, M.W.1    Berger, M.2
  • 60
    • 0028875936 scopus 로고
    • Transfer of genes to humans: Early lessons and obstacles to success
    • Crystal, R.G. Transfer of genes to humans: Early lessons and obstacles to success. Science 1995, 270: 404-10.
    • (1995) Science , vol.270 , pp. 404-410
    • Crystal, R.G.1
  • 61
    • 0030026531 scopus 로고    scopus 로고
    • Gene therapy for cystic fibrosis
    • Rosenfeld, M.A., Collins, F.S. Gene therapy for cystic fibrosis. Chest 1996, 109: 241-52.
    • (1996) Chest , vol.109 , pp. 241-252
    • Rosenfeld, M.A.1    Collins, F.S.2
  • 62
    • 0031713164 scopus 로고    scopus 로고
    • Is DNA destiny? A cure for cystic fibrosis
    • Robinson, C.B. Is DNA destiny? A cure for cystic fibrosis. Clin Chest Med 1998, 19: 527-34.
    • (1998) Clin Chest Med , vol.19 , pp. 527-534
    • Robinson, C.B.1
  • 63
    • 0031717590 scopus 로고    scopus 로고
    • Therapies directed at the basic defect in cystic fibrosis
    • Zeitlin, P.L. Therapies directed at the basic defect in cystic fibrosis. Clin Chest Med 1998, 19: 515-25.
    • (1998) Clin Chest Med , vol.19 , pp. 515-525
    • Zeitlin, P.L.1
  • 64
    • 0030896451 scopus 로고    scopus 로고
    • Correcting temperature-sensitive protein folding defects
    • Brown, C.R., Hong-Brown, L.Q., Welch, W.J. Correcting temperature-sensitive protein folding defects. J Clin Invest 1997, 99: 1432-44.
    • (1997) J Clin Invest , vol.99 , pp. 1432-1444
    • Brown, C.R.1    Hong-Brown, L.Q.2    Welch, W.J.3
  • 65
    • 0030042386 scopus 로고    scopus 로고
    • Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation
    • Sato, S., Ward, C.L., Krouse, M.E., Wine, J.J., Kopito, R.R. Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation. J Biol Chem 1996, 271: 635-8.
    • (1996) J Biol Chem , vol.271 , pp. 635-638
    • Sato, S.1    Ward, C.L.2    Krouse, M.E.3    Wine, J.J.4    Kopito, R.R.5
  • 66
    • 0013488281 scopus 로고    scopus 로고
    • Phenylbutyrate therapy for cystic fibrosis
    • Zeitlin, P.L., Rubenstein, R.C. Phenylbutyrate therapy for cystic fibrosis. Pediatr Pulmonol 1997, Suppl. 14: 132.
    • (1997) Pediatr Pulmonol , Issue.SUPPL. 14 , pp. 132
    • Zeitlin, P.L.1    Rubenstein, R.C.2
  • 67
    • 0028944377 scopus 로고
    • Functional activation of the cystic fibrosis trafficking mutant deltaF508 CFTR by overexpression
    • Cheng, S.H., Fang, S.L., Zabner, J. et al. Functional activation of the cystic fibrosis trafficking mutant deltaF508 CFTR by overexpression. Am J Physiol 1995, 268: L615-24.
    • (1995) Am J Physiol , vol.268
    • Cheng, S.H.1    Fang, S.L.2    Zabner, J.3
  • 68
    • 0025874599 scopus 로고
    • Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis
    • Knowles, M.R., Clarke, L.L., Boucher, R.C. Activation by extracellular nucleotides of chloride secretion in the airway epithelia of patients with cystic fibrosis. N Engl J Med 1991, 325: 533-8.
    • (1991) N Engl J Med , vol.325 , pp. 533-538
    • Knowles, M.R.1    Clarke, L.L.2    Boucher, R.C.3
  • 69
    • 0031299371 scopus 로고    scopus 로고
    • Vaccinations against Pseudomonas aeruginosa: Active and passive alternatives
    • Bellanti, J.A., Zeligs, B.J., Kulcyzcki, L.L. Vaccinations against Pseudomonas aeruginosa: Active and passive alternatives. Pediatr Pulmonol 1997, Suppl. 16: 269-70.
    • (1997) Pediatr Pulmonol , Issue.SUPPL. 16 , pp. 269-270
    • Bellanti, J.A.1    Zeligs, B.J.2    Kulcyzcki, L.L.3
  • 70
    • 0031664785 scopus 로고    scopus 로고
    • Therapies aimed at airway inflammation in cystic fibrosis
    • Konstan, M.W. Therapies aimed at airway inflammation in cystic fibrosis. Clin Chest Med 1998, 19: 505-13.
    • (1998) Clin Chest Med , vol.19 , pp. 505-513
    • Konstan, M.W.1
  • 71
    • 0028969594 scopus 로고
    • A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis
    • Cystic Fibrosis Foundation Prednisone Trial Group.
    • Eigen, H., Rosenstein, B.J., Fitzsimmons, S., Schidlow, D. V. A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group. J Pediatr 1995, 126: 515-23.
    • (1995) J Pediatr , vol.126 , pp. 515-523
    • Eigen, H.1    Rosenstein, B.J.2    Fitzsimmons, S.3    Schidlow, D.V.4


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