-
1
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan JM, Rommens JM, Kerem BS, Alon N, Rozmahel R, Grzelvak Z, Zeilenski J, Lok S, Plavsic N & Chou JL (1989). Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science, 245: 1066-1073.
-
(1989)
Science
, vol.245
, pp. 1066-1073
-
-
Riordan, J.M.1
Rommens, J.M.2
Kerem, B.S.3
Alon, N.4
Rozmahel, R.5
Grzelvak, Z.6
Zeilenski, J.7
Lok, S.8
Plavsic, N.9
Chou, J.L.10
-
2
-
-
0024453308
-
Identification of the cystic fibrosis gene: Chromosome walking and jumping
-
Rommens JM, lannuzzi MC, Kerem B, Drumm ML, Melmer G, Dean M, Rozmahel R, Cole JL, Kennedy D, Hidaka N, Zsiga M, Buckwald M, Riordam JR, Tsui L & Collins FS (1989). Identification of the cystic fibrosis gene: chromosome walking and jumping. Science, 245: 1059-1065.
-
(1989)
Science
, vol.245
, pp. 1059-1065
-
-
Rommens, J.M.1
Lannuzzi, M.C.2
Kerem, B.3
Drumm, M.L.4
Melmer, G.5
Dean, M.6
Rozmahel, R.7
Cole, J.L.8
Kennedy, D.9
Hidaka, N.10
Zsiga, M.11
Buckwald, M.12
Riordam, J.R.13
Tsui, L.14
Collins, F.S.15
-
3
-
-
0026523829
-
Cystic fibrosis: Molecular biology and therapeutic implications
-
Collins FS (1992). Cystic fibrosis: molecular biology and therapeutic implications. Science, 256: 774-779.
-
(1992)
Science
, vol.256
, pp. 774-779
-
-
Collins, F.S.1
-
4
-
-
0002314552
-
Cystic fibrosis
-
Scriver CR, Beaudet AL, Sly WS & Valle D (Editors), McGraw-Hill, New York
-
Boat TF, Welsh MJ & Beaudet AL (1989). Cystic fibrosis. In: Scriver CR, Beaudet AL, Sly WS & Valle D (Editors), The Metabolic Basis of Inherited Disease. McGraw-Hill, New York, 2649-2680.
-
(1989)
The Metabolic Basis of Inherited Disease
, pp. 2649-2680
-
-
Boat, T.F.1
Welsh, M.J.2
Beaudet, A.L.3
-
5
-
-
0025863209
-
Generation of cAMP-activated chloride currents by expression of CFTR
-
Anderson MP, Rich DP, Gregory RJ, Smith AE & Welsh MJ (1991). Generation of cAMP-activated chloride currents by expression of CFTR. Science, 251: 679-682.
-
(1991)
Science
, vol.251
, pp. 679-682
-
-
Anderson, M.P.1
Rich, D.P.2
Gregory, R.J.3
Smith, A.E.4
Welsh, M.J.5
-
6
-
-
0026532895
-
Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)
-
Bear CE, Li C, Kartner N, Bridges RJ, Jensen TJ, Ramjeesingh M & Riordan JR (1992). Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR). Cell, 68: 809-818.
-
(1992)
Cell
, vol.68
, pp. 809-818
-
-
Bear, C.E.1
Li, C.2
Kartner, N.3
Bridges, R.J.4
Jensen, T.J.5
Ramjeesingh, M.6
Riordan, J.R.7
-
7
-
-
0025374695
-
Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport
-
Hyde SC, Emsley P, Hartshorn MJ, Mimmack MM, Gileadi U, Pearce SR, Gallagher MP, Gill DR, Hubbard RE & Higgins CF (1990). Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport. Nature, 346: 362-365.
-
(1990)
Nature
, vol.346
, pp. 362-365
-
-
Hyde, S.C.1
Emsley, P.2
Hartshorn, M.J.3
Mimmack, M.M.4
Gileadi, U.5
Pearce, S.R.6
Gallagher, M.P.7
Gill, D.R.8
Hubbard, R.E.9
Higgins, C.F.10
-
8
-
-
0025942250
-
Immunocytochemical localization of the cystic fibrosis gene product CFTR
-
Crawford I, Maloney PC, Zeitlin PL, Guggino WB, Hyde SC, Turley H, Gatter KC, Harris A & Higgins CF (1991). Immunocytochemical localization of the cystic fibrosis gene product CFTR. Proceedings of the National Academy of Sciences, USA, 88: 9262-9266.
-
(1991)
Proceedings of the National Academy of Sciences, USA
, vol.88
, pp. 9262-9266
-
-
Crawford, I.1
Maloney, P.C.2
Zeitlin, P.L.3
Guggino, W.B.4
Hyde, S.C.5
Turley, H.6
Gatter, K.C.7
Harris, A.8
Higgins, C.F.9
-
9
-
-
0032484636
-
Cystic fibrosis transmembrane conductance regulator expression in human hypothalamus
-
Mulberg AE, Weyler RT, Altschuler SM & Hyde TM (1998). Cystic fibrosis transmembrane conductance regulator expression in human hypothalamus. Neuroreport, 9: 141-144.
-
(1998)
Neuroreport
, vol.9
, pp. 141-144
-
-
Mulberg, A.E.1
Weyler, R.T.2
Altschuler, S.M.3
Hyde, T.M.4
-
10
-
-
0024436699
-
Altered electrical potential profile of human reabsorptive sweat duct cells in cystic fibrosis
-
Cell Physiology, 26
-
Reddy MM & Quinton PM (1989). Altered electrical potential profile of human reabsorptive sweat duct cells in cystic fibrosis. American Journal of Physiology, 257 (Cell Physiology, 26): C722-C726.
-
(1989)
American Journal of Physiology
, vol.257
-
-
Reddy, M.M.1
Quinton, P.M.2
-
11
-
-
0023213846
-
Permeability properties of cell membranes and tight junctions of normal and cystic fibrosis sweat ducts
-
Bijman J & Quinten P (1987). Permeability properties of cell membranes and tight junctions of normal and cystic fibrosis sweat ducts. Pflügers Archiv, 408: 505-510.
-
(1987)
Pflügers Archiv
, vol.408
, pp. 505-510
-
-
Bijman, J.1
Quinten, P.2
-
12
-
-
0029846003
-
Both the wild type and a functional isoform of CFTR are expressed in kidney
-
Renal, Fluid and Electrolyte Physiology, 39
-
Morales MM, Carroll TP, Morita T, Schwiebert EM, Devuyst O, Wilson PD, Lopes AG, Stanton BA, Dietz HC, Cutting GR & Guggino WB (1996). Both the wild type and a functional isoform of CFTR are expressed in kidney. American Journal of Physiology, 270 (Renal, Fluid and Electrolyte Physiology, 39): F1038-F1048.
-
(1996)
American Journal of Physiology
, vol.270
-
-
Morales, M.M.1
Carroll, T.P.2
Morita, T.3
Schwiebert, E.M.4
Devuyst, O.5
Wilson, P.D.6
Lopes, A.G.7
Stanton, B.A.8
Dietz, H.C.9
Cutting, G.R.10
Guggino, W.B.11
-
13
-
-
0022413731
-
A polymorphic DNA marker linked to cystic fibrosis is located on chromosome 7
-
Knowlton RG, Cohen-Haguenauer O, Van Cong N, Frezal J, Brown VA, Barker D, Braman JC, Schumm JW, Tsui LC, Buchwald M & Donis-Keller H (1985). A polymorphic DNA marker linked to cystic fibrosis is located on chromosome 7. Nature, 318: 380-382.
-
(1985)
Nature
, vol.318
, pp. 380-382
-
-
Knowlton, R.G.1
Cohen-Haguenauer, O.2
Van Cong, N.3
Frezal, J.4
Brown, V.A.5
Barker, D.6
Braman, J.C.7
Schumm, J.W.8
Tsui, L.C.9
Buchwald, M.10
Donis-Keller, H.11
-
15
-
-
0025633562
-
MHC class II region encoding proteins related to the multidrug resistance family of transmembrane transporters
-
Deversen EV, Gow IR, Coadwell WJ, Monaco JJ, Butcher GW & Howard JC (1990). MHC class II region encoding proteins related to the multidrug resistance family of transmembrane transporters. Nature, 348: 738-741.
-
(1990)
Nature
, vol.348
, pp. 738-741
-
-
Deversen, E.V.1
Gow, I.R.2
Coadwell, W.J.3
Monaco, J.J.4
Butcher, G.W.5
Howard, J.C.6
-
16
-
-
0027532282
-
Putative X-linked adrenoleukodystropy gene shares unexpected homology with ABC transporters
-
Moser J, Douar AM, Sarde CO, Kioschis P, Feil R, Moser H, Poutska AM, Mandel JL & Aubourg P (1993). Putative X-linked adrenoleukodystropy gene shares unexpected homology with ABC transporters. Nature, 361: 726-730.
-
(1993)
Nature
, vol.361
, pp. 726-730
-
-
Moser, J.1
Douar, A.M.2
Sarde, C.O.3
Kioschis, P.4
Feil, R.5
Moser, H.6
Poutska, A.M.7
Mandel, J.L.8
Aubourg, P.9
-
17
-
-
0027465595
-
Penetrating the peroxisome
-
Valle D & Gartner J (1993). Penetrating the peroxisome. Nature, 361: 682-683.
-
(1993)
Nature
, vol.361
, pp. 682-683
-
-
Valle, D.1
Gartner, J.2
-
20
-
-
0026699623
-
Cyclic AMP-dependent protein kinase activation of cystic fibrosis transmembrane conductance regulator chloride channels in planar lipid bilayers
-
Tilly BC, Winter MC, Ostedgaard LS, O'Riordan C, Smith AE & Welsh MJ (1992). Cyclic AMP-dependent protein kinase activation of cystic fibrosis transmembrane conductance regulator chloride channels in planar lipid bilayers. Journal of Biological Chemistry, 267: 9470-9473.
-
(1992)
Journal of Biological Chemistry
, vol.267
, pp. 9470-9473
-
-
Tilly, B.C.1
Winter, M.C.2
Ostedgaard, L.S.3
O'Riordan, C.4
Smith, A.E.5
Welsh, M.J.6
-
21
-
-
0027860357
-
Inhibition of the cystic fibrosis transmembrane conductance regulator by ATP-sensitive potassium channel regulators
-
Sheppard DN & Welsh MJ (1993). Inhibition of the cystic fibrosis transmembrane conductance regulator by ATP-sensitive potassium channel regulators. Annals of the New York Academy of Sciences, 707: 275-284.
-
(1993)
Annals of the New York Academy of Sciences
, vol.707
, pp. 275-284
-
-
Sheppard, D.N.1
Welsh, M.J.2
-
22
-
-
0023687235
-
Phosphorylation-activated chloride channels in human skin fibroblasts
-
Bear CE (1988). Phosphorylation-activated chloride channels in human skin fibroblasts. FEBS Letters, 237: 145-149.
-
(1988)
FEBS Letters
, vol.237
, pp. 145-149
-
-
Bear, C.E.1
-
24
-
-
0029063956
-
Alternate translation initiation codons can create functional forms of cystic fibrosis transmembrane conductance regulator
-
Piazza-Carrol T, Morales MM, Fulmer SB, Allen SS, Flotte TR, Cutting GR & Guggino WB (1995). Alternate translation initiation codons can create functional forms of cystic fibrosis transmembrane conductance regulator. Journal of Biological Chemistry, 270: 11941-11946.
-
(1995)
Journal of Biological Chemistry
, vol.270
, pp. 11941-11946
-
-
Piazza-Carrol, T.1
Morales, M.M.2
Fulmer, S.B.3
Allen, S.S.4
Flotte, T.R.5
Cutting, G.R.6
Guggino, W.B.7
-
25
-
-
0028058184
-
Identification of an ion channel-forming motif in the primary structure of CFTR, the cystic fibrosis chloride channel
-
Oblatt-Montal M, Reddy GL, Iwamoto T, Tomich JM & Montai M (1994). Identification of an ion channel-forming motif in the primary structure of CFTR, the cystic fibrosis chloride channel. Proceedings of the National Academy of Sciences, USA, 91: 1495-1499.
-
(1994)
Proceedings of the National Academy of Sciences, USA
, vol.91
, pp. 1495-1499
-
-
Oblatt-Montal, M.1
Reddy, G.L.2
Iwamoto, T.3
Tomich, J.M.4
Montai, M.5
-
26
-
-
0028111941
-
Novel pore-lining residues in CFTR that govern permeation and open-channel block
-
McDonough S, Davidson N, Lester HA & McCarty NA (1994). Novel pore-lining residues in CFTR that govern permeation and open-channel block. Neuron, 13: 623-634.
-
(1994)
Neuron
, vol.13
, pp. 623-634
-
-
McDonough, S.1
Davidson, N.2
Lester, H.A.3
McCarty, N.A.4
-
27
-
-
0028980536
-
CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP
-
Schwiebert EM, Egan ME, Hwang T-H, Fulmar SB, Allen SS, Cutting GR & Guggino WB (1995). CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP. Cell, 81: 1063-1073.
-
(1995)
Cell
, vol.81
, pp. 1063-1073
-
-
Schwiebert, E.M.1
Egan, M.E.2
Hwang, T.-H.3
Fulmar, S.B.4
Allen, S.S.5
Cutting, G.R.6
Guggino, W.B.7
-
28
-
-
0027937589
-
The cystic fibrosis transmembrane conductance regulator is a dual ATP and chloride channel
-
Reisin IL, Prat AG, Abrahan EH, Amara JF, Gregory RJ, Ausiello DA & Cantielo HF (1994). The cystic fibrosis transmembrane conductance regulator is a dual ATP and chloride channel. Journal of Biological Chemistry, 269: 20584-20591.
-
(1994)
Journal of Biological Chemistry
, vol.269
, pp. 20584-20591
-
-
Reisin, I.L.1
Prat, A.G.2
Abrahan, E.H.3
Amara, J.F.4
Gregory, R.J.5
Ausiello, D.A.6
Cantielo, H.F.7
-
29
-
-
0031056556
-
Cystic fibrosis transmembrane conductance regulator and adenosine triphosphate
-
Abrahan EH, Okunieff P, Scala S, Vos P, Oosterveld MJS, Chen AY & Shrivastav B (1997). Cystic fibrosis transmembrane conductance regulator and adenosine triphosphate. Science, 275: 1324-1325.
-
(1997)
Science
, vol.275
, pp. 1324-1325
-
-
Abrahan, E.H.1
Okunieff, P.2
Scala, S.3
Vos, P.4
Oosterveld, M.J.S.5
Chen, A.Y.6
Shrivastav, B.7
-
30
-
-
0029998981
-
Failure of the cystic fibrosis transmembrane conductance regulator to conduct ATP
-
Reddy MM, Quinton PM, Haws C, Wine JJ, Grygorczyk R, Tabcharani JA, Hanrahan JW, Gunderson KL & Kopito RR (1996). Failure of the cystic fibrosis transmembrane conductance regulator to conduct ATP. Science, 271: 1876-1879.
-
(1996)
Science
, vol.271
, pp. 1876-1879
-
-
Reddy, M.M.1
Quinton, P.M.2
Haws, C.3
Wine, J.J.4
Grygorczyk, R.5
Tabcharani, J.A.6
Hanrahan, J.W.7
Gunderson, K.L.8
Kopito, R.R.9
-
32
-
-
15844392129
-
Purified cystic fibrosis transmembrane conductance regulator (CFTR) does not function as an ATP channel
-
Canhui L, Mohabir R & Bear CE (1995). Purified cystic fibrosis transmembrane conductance regulator (CFTR) does not function as an ATP channel. Journal of Biological Chemistry, 271: 11623-11626.
-
(1995)
Journal of Biological Chemistry
, vol.271
, pp. 11623-11626
-
-
Canhui, L.1
Mohabir, R.2
Bear, C.E.3
-
33
-
-
0031056556
-
Cystic fibrosis transmembrane conductance regulator and adenosine triphosphate
-
Grygorczyk R & Hanrahan JW (1997). Cystic fibrosis transmembrane conductance regulator and adenosine triphosphate. Science, 275: 1325-1326,
-
(1997)
Science
, vol.275
, pp. 1325-1326
-
-
Grygorczyk, R.1
Hanrahan, J.W.2
-
34
-
-
0030860084
-
The cystic fibrosis transmembrane conductance regulator and ATP
-
Devidas S & Guggino WB (1997). The cystic fibrosis transmembrane conductance regulator and ATP. Current Opinion in Cell Biology, 9: 547-552.
-
(1997)
Current Opinion in Cell Biology
, vol.9
, pp. 547-552
-
-
Devidas, S.1
Guggino, W.B.2
-
35
-
-
0032478144
-
Chloride channel and chloride conductance regulator domains of CFTR, the cystic fibrosis transmembrane conductance regulator. Proceedings
-
Schwiebert EM, Morales MM, Devidas S, Egan ME & Guggino WB (1998). Chloride channel and chloride conductance regulator domains of CFTR, the cystic fibrosis transmembrane conductance regulator. Proceedings of the National Academy of Sciences, USA, 95: 2674-2679.
-
(1998)
Of the National Academy of Sciences, USA
, vol.95
, pp. 2674-2679
-
-
Schwiebert, E.M.1
Morales, M.M.2
Devidas, S.3
Egan, M.E.4
Guggino, W.B.5
-
36
-
-
0032481418
-
- channel and CFTR-associated ATP channel: Distinct pores regulated by common gates
-
- channel and CFTR-associated ATP channel: distinct pores regulated by common gates. EMBO Journal, 17: 898-908.
-
(1998)
EMBO Journal
, vol.17
, pp. 898-908
-
-
Sugita, M.1
Yue, Y.2
Foskett, J.K.3
-
37
-
-
0026337305
-
Chloride conductance expressed by ΔF508 and other mutant CFTRs in Xenopus oocytes
-
Drumm ML, Wilkinson DJ & Smith WS (1992). Chloride conductance expressed by ΔF508 and other mutant CFTRs in Xenopus oocytes. Science, 254: 1797-1799.
-
(1992)
Science
, vol.254
, pp. 1797-1799
-
-
Drumm, M.L.1
Wilkinson, D.J.2
Smith, W.S.3
-
38
-
-
85034150965
-
Two cystic fibrosis transmembrane conductance regulator mutations have different effects on both pulmonary phenotype and regulation of outwardly rectifying chloride currents
-
Fulmer SB, Schwibert EM, Morales M, Guggino WB & Cutting GR (1995). Two cystic fibrosis transmembrane conductance regulator mutations have different effects on both pulmonary phenotype and regulation of outwardly rectifying chloride currents. Proceedings of the National Academy of Sciences, USA, 81: 1063-1073.
-
(1995)
Proceedings of the National Academy of Sciences, USA
, vol.81
, pp. 1063-1073
-
-
Fulmer, S.B.1
Schwibert, E.M.2
Morales, M.3
Guggino, W.B.4
Cutting, G.R.5
-
40
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
Stutts MJ, Canessa CM, Olsen JC, Hamrick M, Cohn JA, Bossier BC & Boucher RC (1995). CFTR as a cAMP-dependent regulator of sodium channels. Science, 269: 847-850.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
Bossier, B.C.6
Boucher, R.C.7
-
41
-
-
0029912194
-
Regulation of epithelial sodium channels by the cystic fibrosis transmembrane conductance regulator
-
Ismailov II, Wayda A, Jovov MS, Beadiev BK, Fuller CM, Didman JR, Koetzel M & Benos DJ (1996). Regulation of epithelial sodium channels by the cystic fibrosis transmembrane conductance regulator. Journal of Biological Chemistry, 271: 4725-4732.
-
(1996)
Journal of Biological Chemistry
, vol.271
, pp. 4725-4732
-
-
Ismailov, I.I.1
Wayda, A.2
Jovov, M.S.3
Beadiev, B.K.4
Fuller, C.M.5
Didman, J.R.6
Koetzel, M.7
Benos, D.J.8
-
42
-
-
0030912066
-
Role of actin in regulation of epithelial sodium channels by CFTR
-
Ismailov II, Berdiev BK, Shlyonsky VG, Fuller CM, Prat AG, Jovov B, Cantiello HF, Ausiello DA & Benos DJ (1997). Role of actin in regulation of epithelial sodium channels by CFTR. American Journal of Physiology, 272 (Part 1): C1077-C1086.
-
(1997)
American Journal of Physiology
, vol.272
, Issue.1 PART
-
-
Ismailov, I.I.1
Berdiev, B.K.2
Shlyonsky, V.G.3
Fuller, C.M.4
Prat, A.G.5
Jovov, B.6
Cantiello, H.F.7
Ausiello, D.A.8
Benos, D.J.9
-
43
-
-
0031024767
-
Inhibition of epithelial sodium currents by intracellular domains of the cystic fibrosis transmembrane conductance regulator
-
Kunzelman K, Kiser G, Schreiber R & Riordan JR (1997). Inhibition of epithelial sodium currents by intracellular domains of the cystic fibrosis transmembrane conductance regulator. FEBS Letters, 400: 341-344.
-
(1997)
FEBS Letters
, vol.400
, pp. 341-344
-
-
Kunzelman, K.1
Kiser, G.2
Schreiber, R.3
Riordan, J.R.4
-
44
-
-
0031921269
-
+ channels (ENaCs) in Xenopus oocytes coexpressing CFTR and EnaC
-
+ channels (ENaCs) in Xenopus oocytes coexpressing CFTR and EnaC. Journal of Physiology, 508 (Part 3): 825-836.
-
(1998)
Journal of Physiology
, vol.508
, Issue.3 PART
, pp. 825-836
-
-
Briel, M.1
Greger, R.2
Kunzelmann, K.3
-
45
-
-
0009580755
-
Altered pHi regulation in 3T3/CFTR clones and their chemotherapeutic drug-selected derivatives
-
Wei LY, Hoffman MM & Roepe PD (1997). Altered pHi regulation in 3T3/CFTR clones and their chemotherapeutic drug-selected derivatives. American Journal of Physiology, 272 (Part 1): C1642-C1653.
-
(1997)
American Journal of Physiology
, vol.272
, Issue.1 PART
-
-
Wei, L.Y.1
Hoffman, M.M.2
Roepe, P.D.3
-
46
-
-
0029161044
-
Overexpression of the cystic fibrosis transmembrane conductance regulator in NIH 3T3 cells lowers membrane potential and intracellular pH and confers a multidrug resistance phenotype
-
Wei LY, Stutts MJ, Hoffman MM & Roepe PD (1995). Overexpression of the cystic fibrosis transmembrane conductance regulator in NIH 3T3 cells lowers membrane potential and intracellular pH and confers a multidrug resistance phenotype. Biophysical Journal, 69: 883-895
-
(1995)
Biophysical Journal
, vol.69
, pp. 883-895
-
-
Wei, L.Y.1
Stutts, M.J.2
Hoffman, M.M.3
Roepe, P.D.4
-
47
-
-
0030892062
-
Co-ordinate regulation of the cystic fibrosis and multidrug resistance genes in cystic fibrosis knockout mice
-
Trezise AE, Ratcliff R, Hawkins TE, Evans MJ, Freeman TC, Romano PR, Higgins CF & Colledge WH (1997). Co-ordinate regulation of the cystic fibrosis and multidrug resistance genes in cystic fibrosis knockout mice. Human Molecular Genetics, 6: 527-537.
-
(1997)
Human Molecular Genetics
, vol.6
, pp. 527-537
-
-
Trezise, A.E.1
Ratcliff, R.2
Hawkins, T.E.3
Evans, M.J.4
Freeman, T.C.5
Romano, P.R.6
Higgins, C.F.7
Colledge, W.H.8
-
48
-
-
0026451638
-
The multidrug resistance and cystic fibrosis genes have complementary patterns of epithelial expression
-
Trezise AE, Romano PR, Gill D, Hyde SC, Sepúlveda FV, Buchwald M & Higgins CF (1992). The multidrug resistance and cystic fibrosis genes have complementary patterns of epithelial expression. EMBO Journal, 11: 4291-4303.
-
(1992)
EMBO Journal
, vol.11
, pp. 4291-4303
-
-
Trezise, A.E.1
Romano, P.R.2
Gill, D.3
Hyde, S.C.4
Sepúlveda, F.V.5
Buchwald, M.6
Higgins, C.F.7
-
49
-
-
0027761180
-
Induction of multidrug resistance downregulates the expression of CFTR in colon epithelial cells
-
Cell Physiology, 34
-
Breuer W, Slotki IN, Ausiello DA & Cabantchik IZ (1993). Induction of multidrug resistance downregulates the expression of CFTR in colon epithelial cells. American Journal of Physiology, 265 (Cell Physiology, 34): C1711-C1715.
-
(1993)
American Journal of Physiology
, vol.265
-
-
Breuer, W.1
Slotki, I.N.2
Ausiello, D.A.3
Cabantchik, I.Z.4
-
50
-
-
1642466209
-
Abnormal chloride and sodium channel function in cystic fibrosis airway epithelia
-
Crystal RG & West JB (Editors), Lippincott-Raven Publishers, Philadelphia
-
Schwiebert EM & Guggino WB (1996). Abnormal chloride and sodium channel function in cystic fibrosis airway epithelia. In: Crystal RG & West JB (Editors), The Lung: Scientific Foundations. 2nd edn. Lippincott-Raven Publishers, Philadelphia, 195.1-195.17.
-
(1996)
The Lung: Scientific Foundations. 2nd Edn.
, pp. 1951-19517
-
-
Schwiebert, E.M.1
Guggino, W.B.2
-
51
-
-
0027390125
-
Effects of the ΔF508 mutation on the structure, function, and folding of the first nucleotide-binding domain of CFTR
-
Tomas PJ & Pedersen PL (1993). Effects of the ΔF508 mutation on the structure, function, and folding of the first nucleotide-binding domain of CFTR. Journal of Bioenergetics and Biomembranes, 25: 11-19.
-
(1993)
Journal of Bioenergetics and Biomembranes
, vol.25
, pp. 11-19
-
-
Tomas, P.J.1
Pedersen, P.L.2
-
52
-
-
0025310336
-
A cluster of cystic fibrosis mutations in the first nucleotide-binding fold of the cystic fibrosis conductance regulator protein
-
Cutting GR, Kasch LM, Rosestein BJ, Zielenski J, Tsui LC, Antonarakis SE & Kazazian Jr HH (1990). A cluster of cystic fibrosis mutations in the first nucleotide-binding fold of the cystic fibrosis conductance regulator protein. Nature, 346: 366-369.
-
(1990)
Nature
, vol.346
, pp. 366-369
-
-
Cutting, G.R.1
Kasch, L.M.2
Rosestein, B.J.3
Zielenski, J.4
Tsui, L.C.5
Antonarakis, S.E.6
Kazazian H.H., Jr.7
-
53
-
-
0027364318
-
Functional roles of the nucleotide-binding folds in the activation of the cystic fibrosis transmembrane conductance regulator
-
Smit LS, Wilkinson DJ, Mansoura MK, Collins FS & Dawson DC (1993). Functional roles of the nucleotide-binding folds in the activation of the cystic fibrosis transmembrane conductance regulator. Proceedings of the National Academy of Sciences, USA, 90: 9963-9967.
-
(1993)
Proceedings of the National Academy of Sciences, USA
, vol.90
, pp. 9963-9967
-
-
Smit, L.S.1
Wilkinson, D.J.2
Mansoura, M.K.3
Collins, F.S.4
Dawson, D.C.5
-
54
-
-
0029063956
-
Alternate translation initiation codons can create functional forms of cystic fibrosis transmembrane conductance regulator
-
Piazza-Carrol T, McIntosh I, Egan ME, Zeitlin PL, Cutting GR & Guggino WB (1994). Alternate translation initiation codons can create functional forms of cystic fibrosis transmembrane conductance regulator. Journal of Biological Chemistry, 270: 11941-11946.
-
(1994)
Journal of Biological Chemistry
, vol.270
, pp. 11941-11946
-
-
Piazza-Carrol, T.1
McIntosh, I.2
Egan, M.E.3
Zeitlin, P.L.4
Cutting, G.R.5
Guggino, W.B.6
-
56
-
-
0025987020
-
Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel
-
Cheng SH, Rich DP, Marshall J, Gregory RJ, Welsh MJ & Smith AE (1991). Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel. Cell, 66: 1027-1036.
-
(1991)
Cell
, vol.66
, pp. 1027-1036
-
-
Cheng, S.H.1
Rich, D.P.2
Marshall, J.3
Gregory, R.J.4
Welsh, M.J.5
Smith, A.E.6
-
57
-
-
0027311276
-
Protein kinase A (PKA) still activates CFTR chloride channels after mutagenesis of all 10 PKA consensus phosphorylation sites
-
Chang X-B, Tabcharani JA, Hou Y-X, Jensen TJ, Kartner N, Alon N, Hanrahan JW & Riordan JR (1993). Protein kinase A (PKA) still activates CFTR chloride channels after mutagenesis of all 10 PKA consensus phosphorylation sites. Journal of Biological Chemistry, 268: 11304-11311.
-
(1993)
Journal of Biological Chemistry
, vol.268
, pp. 11304-11311
-
-
Chang, X.-B.1
Tabcharani, J.A.2
Hou, Y.-X.3
Jensen, T.J.4
Kartner, N.5
Alon, N.6
Hanrahan, J.W.7
Riordan, J.R.8
|