Secondary reduction of α7B integrin in laminin α2 deficient congenital muscular dystrophy supports an additional transmembrane link in skeletal muscle

Journal of the Neurological Sciences

Volumn 163, Issue 2, 1999, Pages 140-152

  Cohn, Ronald D ^a   Mayer, Ulrike ^b   Saher, Gesine ^b   Herrmann, Ralf ^a   Van Der Flier, Arjan ^c   Sonnenberg, Arnoud ^c   Sorokin, Lydia ^d   Voit, Thomas ^a  

^a UNIVERSITY OF DUISBURG ESSEN   (Germany)

^b MAX PLANCK INSTITUTE OF BIOCHEMISTRY   (Germany)

^c NETHERLANDS CANCER INSTITUTE   (Netherlands)

^d UNIVERSITY OF ERLANGEN NUREMBERG   (Germany)

Author keywords

7 Integrin; Extracellular matrix; Muscle function; Muscular dystrophy

Indexed keywords

INTEGRIN; LAMININ; ALPHA INTEGRIN; ALPHA7 INTEGRIN; ANTIBODY; CYTOSKELETON PROTEIN; DAG1 PROTEIN, HUMAN; DYSTROGLYCAN; DYSTROPHIN; ISOPROTEIN; LAMININ ALPHA2; LEUKOCYTE ANTIGEN; MEMBRANE PROTEIN; SARCOGLYCAN;

ADOLESCENT; ADULT; ARTICLE; BECKER MUSCULAR DYSTROPHY; CELL MEMBRANE; CHILD; CONTROLLED STUDY; DUCHENNE MUSCULAR DYSTROPHY; EMERY DREIFUSS MUSCULAR DYSTROPHY; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; INFANT; KNOCKOUT MOUSE; LIMB GIRDLE MUSCULAR DYSTROPHY; MUSCLE BIOPSY; NEWBORN; PRIORITY JOURNAL; PROTEIN DETERMINATION; PROTEIN EXPRESSION; SARCOLEMMA; SKELETAL MUSCLE; WALKER WARBURG SYNDROME; AGING; AMINO ACID SEQUENCE; ANIMAL; FETUS; GENE EXPRESSION REGULATION; GENETICS; GROWTH, DEVELOPMENT AND AGING; MOLECULAR GENETICS; MOUSE; MOUSE MUTANT; MUSCLE DEVELOPMENT; MUSCULAR DYSTROPHY; PATHOPHYSIOLOGY; PHYSIOLOGY; PRENATAL DEVELOPMENT; PRESCHOOL CHILD;

ADOLESCENT; ADULT; AGING; AMINO ACID SEQUENCE; ANIMALS; ANTIBODIES; ANTIGENS, CD; CHILD; CHILD, PRESCHOOL; CYTOSKELETAL PROTEINS; DYSTROGLYCANS; DYSTROPHIN; EMBRYONIC AND FETAL DEVELOPMENT; FETUS; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HUMANS; INFANT; INFANT, NEWBORN; INTEGRIN ALPHA CHAINS; INTEGRINS; LAMININ; MEMBRANE GLYCOPROTEINS; MICE; MICE, KNOCKOUT; MOLECULAR SEQUENCE DATA; MUSCLE DEVELOPMENT; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; PROTEIN ISOFORMS; SARCOGLYCANS;

EID: 0033084217     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-510X(99)00012-X     Document Type: Article

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