Structure-function analysis of a double-mutant cystic fibrosis transmembrane conductance regulator protein occurring in disorders related to cystic fibrosis

FEBS Letters

Volumn 452, Issue 3, 1999, Pages 371-374

  Fanen, Pascale ^a   Clain, Jérôme ^a   Labarthe, Régis ^a   Hulin, Philippe ^a   Girodon, Emmanuelle ^a   Pagesy, Patrick ^a   Goossens, Michel ^a   Edelman, Aleksander ^a  

^a INSERM   (France)

Author keywords

Cystic fibrosis transmembrane conductance regulator; Double mutant; Heterologous expression; R74W D1270N

Indexed keywords

TRANSMEMBRANE CONDUCTANCE REGULATOR;

AGENESIS; ARTICLE; CONTROLLED STUDY; CYSTIC FIBROSIS; GENE EXPRESSION; HELA CELL; IMMUNOPRECIPITATION; MEMBRANE CONDUCTANCE; MUTANT; NONHUMAN; PRIORITY JOURNAL; STRUCTURE ACTIVITY RELATION; VAS DEFERENS;

ALLELES; AMINO ACID SUBSTITUTION; ANIMALS; CELL LINE; CYCLIC AMP-DEPENDENT PROTEIN KINASES; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GENOTYPE; HELA CELLS; HUMANS; MAMMALS; POINT MUTATION; POLYMORPHISM, GENETIC; RECOMBINANT PROTEINS; STRUCTURE-ACTIVITY RELATIONSHIP; TRANSFECTION;

EID: 0032966132     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0014-5793(99)00647-X     Document Type: Article

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