Pathological features of glycogen storage disease type II highlighted in the knockout mouse model

Journal of Pathology

Volumn 189, Issue 3, 1999, Pages 416-424

  Bijvoet, Agnes G A ^a,b   Van Hirtum, Hans ^a,b   Vermey, Marcel ^a   Van Leenen, Dik ^a   Van Der Ploeg, Ans T ^b   Mooi, Wolter J ^a   Reuser, Arnold J J ^a  

^a ERASMUS UNIVERSITY ROTTERDAM   (Netherlands)

^b SOPHIA CHILDREN S HOSPITAL   (Netherlands)

Author keywords

Glucosidase; Acid maltase; Glycogenosis; Mouse model; Pompe's disease

Indexed keywords

GLUCAN 1,4 ALPHA GLUCOSIDASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CENTRAL NERVOUS SYSTEM; CLINICAL FEATURE; DISEASE SEVERITY; GLYCOGEN STORAGE DISEASE; GLYCOGEN STORAGE DISEASE TYPE 2; HEART MUSCLE; KNOCKOUT MOUSE; LIFESPAN; MODEL; MOUSE; NONHUMAN; PRIORITY JOURNAL; SKELETAL MUSCLE; SYMPTOMATOLOGY;

ANIMALS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; FEMALE; GLYCOGEN STORAGE DISEASE TYPE II; KIDNEY; MALE; MICE; MICE, KNOCKOUT; MUSCLE, SKELETAL; MUSCLE, SMOOTH; MYOCARDIUM;

EID: 0032834144     PISSN: 00223417     EISSN: None     Source Type: Journal    
DOI: 10.1002/(SICI)1096-9896(199911)189:3<416::AID-PATH445>3.0.CO;2-6     Document Type: Article

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