Copper transport and its alterations in Menkes and Wilson diseases

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1360, Issue 1, 1997, Pages 3-16

  DiDonato, Michael ^a,b   Sarkar, Bibudhendra ^a,b  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ALBUMIN; CERULOPLASMIN; COPPER; COPPER COMPLEX; DIMERCAPROL; HISTIDINE COPPER; PENICILLAMINE; TETRATHIOMOLYBDIC ACID; TRIENTINE; UNCLASSIFIED DRUG; ZINC;

CHELATION THERAPY; COPPER METABOLISM; DRUG BILE LEVEL; GASTROINTESTINAL ABSORPTION; GASTROINTESTINAL TRANSIT; HUMAN; INTRACELLULAR TRANSPORT; ION TRANSPORT; MEMBRANE TRANSPORT; MENKES SYNDROME; NONHUMAN; PRIORITY JOURNAL; PROTEIN BINDING; REVIEW; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; BIOLOGICAL TRANSPORT; CARRIER PROTEINS; CATION TRANSPORT PROTEINS; COPPER; HEPATOLENTICULAR DEGENERATION; HUMANS; INTESTINAL ABSORPTION; MENKES KINKY HAIR SYNDROME; METALLOPROTEINS; MUTATION; RECOMBINANT FUSION PROTEINS;

EID: 0031050483     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(96)00064-6     Document Type: Review

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