Impaired Ca2+-induced tyrosine phosphorylation and defective lipid scrambling in erythrocytes from a patient with scott syndrome: A study using an inhibitor for scramblase that mimics the defect in scott syndrome

Blood

Volumn 91, Issue 6, 1998, Pages 2133-2138

  Dekkers, David W C ^b   Comfurius, Paul ^b   Vuist, Wim M J ^b   Billheimer, Jeffrey T ^b   Dicker, Ira ^b   Weiss, Harvey J ^b   Zwaal, Robert F A ^b   Bevers, Edouard M ^a  

^a MAASTRICHT UNIVERSITY   (Netherlands)

^b NONE

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM ION; LIPID; PHOSPHATIDYLSERINE; PROCOAGULANT; SCRAMBLASE; TYROSINE; UNCLASSIFIED DRUG; ADENOSINE TRIPHOSPHATE; CALCIUM; CARRIER PROTEIN; DRUG DERIVATIVE; ENZYME INHIBITOR; ETHANIMIDOTHIOIC ACID N ((N BUTYLTHIO N METHYLAMINO) CARBONYLOXY) METHYLESTER; ETHANIMIDOTHIOIC ACID N-((N-BUTYLTHIO-N-METHYLAMINO)-CARBONYLOXY)-METHYLESTER; IONOPHORE; MEMBRANE LIPID; MEMBRANE PROTEIN; METHOMYL; PHOSPHOLIPID; PHOSPHOLIPID TRANSFER PROTEIN; PROTEIN TYROSINE KINASE; STAUROSPORINE; THROMBOPLASTIN;

ARTICLE; BLEEDING DISORDER; CONTROLLED STUDY; ERYTHROCYTE GHOST; HUMAN; HUMAN CELL; PHOSPHOLIPID MEMBRANE; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; SCOTT SYNDROME; THROMBOCYTE ACTIVATION; BLOOD; BLOOD CLOTTING DISORDER; CELL MEMBRANE; DRUG ANTAGONISM; DRUG EFFECT; ERYTHROCYTE MEMBRANE; GENETICS; METABOLISM; PHOSPHORYLATION; PHYSIOLOGY; PROTEIN PROCESSING; SYNDROME; THROMBOCYTE;

ADENOSINE TRIPHOSPHATE; BLOOD COAGULATION DISORDERS; BLOOD PLATELETS; CALCIUM; CARRIER PROTEINS; CELL MEMBRANE; ENZYME INHIBITORS; ERYTHROCYTE MEMBRANE; HUMANS; IONOPHORES; MEMBRANE LIPIDS; MEMBRANE PROTEINS; METHOMYL; PHOSPHATIDYLSERINES; PHOSPHOLIPID TRANSFER PROTEINS; PHOSPHOLIPIDS; PHOSPHORYLATION; PROTEIN PROCESSING, POST-TRANSLATIONAL; PROTEIN-TYROSINE KINASES; STAUROSPORINE; SYNDROME; THROMBOPLASTIN;

EID: 0032520262     PISSN: 00064971     EISSN: None     Source Type: Journal    
DOI: 10.1182/blood.v91.6.2133     Document Type: Article

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