Analysis of x-ray diffraction patterns from amyloid of biopsied vitreous humor and kidney of transthyretin (TTR) Met30 familial amyloidotic polyneuropathy (FAP) patients: Axially arrayed TTR monomers constitute the protofilament

Amyloid

Volumn 5, Issue 3, 1998, Pages 163-174

  Inouye, Hideyo ^a   Domingues, Francisco S ^b,c   Damas, Ana M ^b,d   Saraiva, Maria J ^b,d   Lundgren, Erik ^e   Sandgren, Ola ^e   Kirschner, Daniel A ^a  

^a BOSTON COLLEGE   (United States)

^b UNIVERSITY OF PORTO   (Portugal)

^c UNIVERSITY OF SALZBURG   (Austria)

^d UNIVERSITY OF PORTO   (Portugal)

^e UMEÅ UNIVERSITY   (Sweden)

Author keywords

Amyloid; Amyloidosis; Familial amyloidotic polyneuropathy; Fiber diffraction; Fibrillogenesis; pleated sheet

Indexed keywords

AMYLOID; AMYLOID PREALBUMIN; PREALBUMIN;

AMYLOID NEUROPATHY; ARTICLE; AUDIOVISUAL EQUIPMENT; CASE REPORT; CHEMISTRY; HUMAN; KIDNEY; PROTEIN CONFORMATION; VITREOUS BODY; X RAY DIFFRACTION;

AMYLOID; AMYLOID NEUROPATHIES; HUMANS; KIDNEY; MODELS, STRUCTURAL; PREALBUMIN; PROTEIN CONFORMATION; VITREOUS BODY; X-RAY DIFFRACTION;

EID: 0032150739     PISSN: 13506129     EISSN: None     Source Type: Journal    
DOI: 10.3109/13506129809003842     Document Type: Article

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