Reduced cholesterol accumulation and improved deficient peroxisomal functions in a murine model of niemann-pick type C disease upon treatment with peroxisomal proliferators

Biochemical Pharmacology

Volumn 56, Issue 9, 1998, Pages 1195-1199

  Schedin, Sophia ^a   Pentchev, Peter ^c   Dallner, Gustav ^a,b  

^a STOCKHOLM UNIVERSITY   (Sweden)

^b KAROLINSKA INSTITUTE   (Sweden)

^c NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

Author keywords

Cholesterol; Dolichol; Lipid metabolism; Niemann Pick; Peroxisomal proliferation; Peroxisomes

Indexed keywords

3 HYDROXY 3 METHYLGLUTARYL COENZYME A; CATALASE; CHOLESTEROL; CLOFIBRATE; GENE PRODUCT; MEMBRANE PROTEIN; PERFLUOROOCTANOIC ACID; PEROXISOME PROLIFERATOR; UBIQUINONE;

AMINO ACID SEQUENCE; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOACCUMULATION; CELL FUNCTION; CONTROLLED STUDY; ENZYME ACTIVITY; FATTY ACID OXIDATION; GENE MUTATION; HOMEOSTASIS; LYSOSOME; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PEROXISOME; PRIORITY JOURNAL; SEQUENCE HOMOLOGY;

ANIMALS; CHOLESTEROL; FLUOROCARBONS; MICE; MICE, INBRED BALB C; MICROBODIES; NIEMANN-PICK DISEASES; OCTANOIC ACIDS; PEROXISOME PROLIFERATORS;

EID: 0031792786     PISSN: 00062952     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0006-2952(98)00234-2     Document Type: Article

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