-
1
-
-
0028284779
-
Motor neuron degeneration in mice that express a human Cu, Zn superoxide dismutase mutation
-
Gurney ME, Pu H, Chiu AY, et al. Motor neuron degeneration in mice that express a human Cu, Zn superoxide dismutase mutation. Science 1994;264:1772-1775.
-
(1994)
Science
, vol.264
, pp. 1772-1775
-
-
Gurney, M.E.1
Pu, H.2
Chiu, A.Y.3
-
2
-
-
0027946294
-
Development of central nervous system pathology in a murine transgenic model of human amyotrophic lateral sclerosis
-
Dal Canto MC, Gurney ME. Development of central nervous system pathology in a murine transgenic model of human amyotrophic lateral sclerosis. Am J Pathol 1994;145:1271-1280.
-
(1994)
Am J Pathol
, vol.145
, pp. 1271-1280
-
-
Dal Canto, M.C.1
Gurney, M.E.2
-
3
-
-
0029053881
-
An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria
-
Wong PC, Pardo CA, Borchelt DR, et al. An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria. Neuron 1995;14:1105-1116.
-
(1995)
Neuron
, vol.14
, pp. 1105-1116
-
-
Wong, P.C.1
Pardo, C.A.2
Borchelt, D.R.3
-
4
-
-
0029966363
-
Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions
-
Tu PH, Raju P, Robinson KA, Gurney ME, Trojanowski JQ, Lee VM-Y. Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions. Proc Natl Acad Sci USA 1996;93:3155-3160.
-
(1996)
Proc Natl Acad Sci USA
, vol.93
, pp. 3155-3160
-
-
Tu, P.H.1
Raju, P.2
Robinson, K.A.3
Gurney, M.E.4
Trojanowski, J.Q.5
Lee, V.M.-Y.6
-
5
-
-
0031051485
-
ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions
-
Bruijn LI, Becher MW, Lee MK, et al. ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions. Neuron 1997;18:327-338.
-
(1997)
Neuron
, vol.18
, pp. 327-338
-
-
Bruijn, L.I.1
Becher, M.W.2
Lee, M.K.3
-
6
-
-
0028106044
-
Familial amyotrophic lateral sclerosis with a mutation in the Cu/Zn superoxide dismutase gene
-
Takahashi H, Makifuchi T, Nakano R, et al. Familial amyotrophic lateral sclerosis with a mutation in the Cu/Zn superoxide dismutase gene. Acta Neuropathol 1994;88:185-188.
-
(1994)
Acta Neuropathol
, vol.88
, pp. 185-188
-
-
Takahashi, H.1
Makifuchi, T.2
Nakano, R.3
-
7
-
-
0029840428
-
Familial amyotrophic lateral sclerosis with a two base pair deletion in superoxide dismutase 1 gene: Multisystem degeneration with intracytoplasmic hyaline inclusions in astrocytes
-
Kato S, Shimoda M, Watanabe Y, Nakashima K, Takahashi K, Ohama E. Familial amyotrophic lateral sclerosis with a two base pair deletion in superoxide dismutase 1 gene: multisystem degeneration with intracytoplasmic hyaline inclusions in astrocytes. J Neuropathol Exp Neurol 1996;55:1089-1101.
-
(1996)
J Neuropathol Exp Neurol
, vol.55
, pp. 1089-1101
-
-
Kato, S.1
Shimoda, M.2
Watanabe, Y.3
Nakashima, K.4
Takahashi, K.5
Ohama, E.6
-
8
-
-
0029792449
-
Familial amyotrophic lateral sclerosis with a mutation in exon 4 of the Cu/Zn superoxide dismutase gene: Pathological and immunocytochemical changes
-
Ince PG, Shaw PJ, Slade JY, Jones C, Hudgson P. Familial amyotrophic lateral sclerosis with a mutation in exon 4 of the Cu/Zn superoxide dismutase gene: pathological and immunocytochemical changes. Acta Neuropathol 1996;92:395-403.
-
(1996)
Acta Neuropathol
, vol.92
, pp. 395-403
-
-
Ince, P.G.1
Shaw, P.J.2
Slade, J.Y.3
Jones, C.4
Hudgson, P.5
-
9
-
-
0015107911
-
Clinical and pathological findings in an unusual infantile motor neuron disease
-
Kohn R. Clinical and pathological findings in an unusual infantile motor neuron disease. J Neurol Neurosurg Psychiatry 1971;34:427-431.
-
(1971)
J Neurol Neurosurg Psychiatry
, vol.34
, pp. 427-431
-
-
Kohn, R.1
-
10
-
-
0031933163
-
Presence of Cu/Zn superoxide dismutase (SOD) immunoreactivity in neuronal hyaline inclusions in spinal cords from mice carrying a transgene for Gly 93 Ala mutant human Cu/Zn SOD
-
Shibata N, Hirano A, Kobayashi M, et al. Presence of Cu/Zn superoxide dismutase (SOD) immunoreactivity in neuronal hyaline inclusions in spinal cords from mice carrying a transgene for Gly 93 Ala mutant human Cu/Zn SOD. Acta Neuropathol 1998;95:136-142.
-
(1998)
Acta Neuropathol
, vol.95
, pp. 136-142
-
-
Shibata, N.1
Hirano, A.2
Kobayashi, M.3
|