Failure of short-term mannose therapy of patients with carbohydrate- deficient glycoprotein syndrome type 1A

Acta Paediatrica, International Journal of Paediatrics

Volumn 87, Issue 8, 1998, Pages 884-888

  Kjaergaard, S ^a   Kristiansson, B ^b   Stibler, H ^c   Freeze, H H ^d   Schwartz, M ^a   Martinsson, T ^b   Skovby, F ^a  

^a Rigshospitalet   (Denmark)

^b SAHLGRENSKA UNIVERSITY HOSPITAL   (Sweden)

^c KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^d BURNHAM INSTITUTE   (United States)

Author keywords

Carbohydrate deficient glycoprotein syndrome; Glycoproteins; Mannose

Indexed keywords

ALPHA 1 ANTITRYPSIN; ANTITHROMBIN; CARBOHYDRATE; GLYCOPROTEIN; MANNOSE; PROTEIN C; THYROXINE BINDING GLOBULIN; TRANSFERRIN;

ADOLESCENT; ARTICLE; CHILD; CLINICAL ARTICLE; CLINICAL TRIAL; CONGENITAL DISORDER OF GLYCOSYLATION; DIET SUPPLEMENTATION; FEMALE; HUMAN; MALE; NOSE FEEDING; ORAL DRUG ADMINISTRATION; PRIORITY JOURNAL; TREATMENT FAILURE;

ADOLESCENT; BLOOD CHEMICAL ANALYSIS; BLOTTING, WESTERN; CARBOHYDRATE-DEFICIENT GLYCOPROTEIN SYNDROME; CHILD; CHILD, PRESCHOOL; DIETARY SUPPLEMENTS; FEMALE; GLYCOPROTEINS; HUMANS; INFANT; MALE; MANNOSE; MUTATION; TREATMENT FAILURE;

EID: 0031656766     PISSN: 08035253     EISSN: None     Source Type: Journal    
DOI: 10.1080/080352598750013680     Document Type: Article

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