Specificity of mouse G(M2) activator protein and β-N- acetylhexosaminidases A and B. Similarities and differences with their human counterparts in the catabolism of G(M2)

Journal of Biological Chemistry

Volumn 273, Issue 1, 1998, Pages 66-72

  Yuziuk, Jeffrey A ^a   Bertoni, Carmen ^a,b   Beccari, Tommaso ^b   Orlacchio, Aldo ^b   Wu, Yan Yun ^a   Li, Su Chen ^a   Li, Yu Teh ^a  

^a TULANE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF PERUGIA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE; GANGLIOSIDE GM2; GANGLIOSIDE GM2 ACTIVATOR PROTEIN; ISOENZYME; PROTEIN; RECOMBINANT PROTEIN;

ANIMAL CELL; ARTICLE; CATABOLISM; CENTRAL NERVOUS SYSTEM; ENZYME DEFICIENCY; ENZYME SPECIFICITY; GENE DISRUPTION; GENETIC RECOMBINATION; HYDROLYSIS; LYSOSOME MEMBRANE; NONHUMAN; PRIORITY JOURNAL; TAY SACHS DISEASE; ANIMAL; ENZYMOLOGY; GEL CHROMATOGRAPHY; HUMAN; ION EXCHANGE CHROMATOGRAPHY; ISOLATION AND PURIFICATION; KINETICS; LIVER; METABOLISM; MOUSE; POLYACRYLAMIDE GEL ELECTROPHORESIS; THIN LAYER CHROMATOGRAPHY;

ANIMALS; BETA-N-ACETYLHEXOSAMINIDASE; CHROMATOGRAPHY, GEL; CHROMATOGRAPHY, ION EXCHANGE; CHROMATOGRAPHY, THIN LAYER; ELECTROPHORESIS, POLYACRYLAMIDE GEL; G(M2) ACTIVATOR PROTEIN; G(M2) GANGLIOSIDE; HUMANS; HYDROLYSIS; ISOENZYMES; KINETICS; LIVER; MICE; PROTEINS; RECOMBINANT PROTEINS; SUBSTRATE SPECIFICITY;

EID: 0031594717     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.273.1.66     Document Type: Article

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