Lung disease in mice with cystic fibrosis

Journal of Clinical Investigation

Volumn 100, Issue 12, 1997, Pages 3060-3069

  Kent, Geraldine ^a   Iles, Richard ^a,b   Bear, Christine E ^b   Huan, Ling Jun ^b   Griesenbach, Uta ^a,c   McKerlie, Colin ^d   Frndova, Helena ^a   Ackerley, Cameron ^c   Gosselin, Diane ^e   Radzioch, Danuta ^e   O'Brodovich, Hugh ^a,b   Tsui, Lap Chee ^a,c   Buchwald, Manuel ^a,c   Tanswell, A Keith ^a,b,f  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

^c UNIVERSITY OF TORONTO   (Canada)

^d SUNNYBROOK RESEARCH INSTITUTE   (Canada)

^e MONTREAL GENERAL HOSPITAL   (Canada)

^f HOSPITAL FOR SICK CHILDREN   (Canada)

Author keywords

Chloride channels; Ion transport; Lung mechanics; Obstructive airway disease; Pulmonary fibrosis

Indexed keywords

CHLORIDE CHANNEL;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CYSTIC FIBROSIS; DISEASE SEVERITY; INBRED STRAIN; ION TRANSPORT; LUNG DISEASE; LUNG FIBROSIS; LUNG FUNCTION TEST; LUNG MECHANICS; MOUSE; MUCOCILIARY TRANSPORT; NONHUMAN; OBSTRUCTIVE AIRWAY DISEASE; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL;

EID: 0031438318     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI119861     Document Type: Article

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