Functional defects in lysosomal enzymes in autosomal dominant polycystic kidney disease (ADPKD): Abnormalities in synthesis, molecular processing, polarity, and secretion

Biochemical and Molecular Medicine

Volumn 60, Issue 1, 1997, Pages 8-26

  Hartz, Patricia A ^a   Wilson, Patricia D ^a,b  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

LYSOSOME ENZYME;

ADULT; AGED; ARTICLE; AUTOSOMAL DOMINANT DISORDER; BASEMENT MEMBRANE; ENZYME ANALYSIS; ENZYME DEFECT; ENZYME RELEASE; ENZYME SYNTHESIS; HUMAN; HUMAN TISSUE; KIDNEY POLYCYSTIC DISEASE; PROTEIN PROCESSING; PROTEIN TARGETING; PROTEIN TRANSPORT;

EID: 0031080747     PISSN: 10773150     EISSN: None     Source Type: Journal    
DOI: 10.1006/bmme.1996.2542     Document Type: Article

References (56)

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