The human peroxisomal multifunctional protein involved in bile acid synthesis: Activity measurement, deficiency in Zellweger syndrome and chromosome mapping

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1360, Issue 3, 1997, Pages 229-240

  Novikov, Dmitry ^a   Dieuaide Noubhani, Martine ^a   Vermeesch, Joris R ^a   Fournier, Beatrice ^a   Mannaerts, Guy P ^a   Van Veldhoven, Paul P ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

Author keywords

Oxidation; 3 Hydroxyacyl CoA dehydrogenase; Bile acid intermediate; Enoyl CoA hydratase; Peroxisome; Steroid

Indexed keywords

3 HYDROXYACYL COENZYME A DEHYDROGENASE; ACYL COENZYME A OXIDASE; OXIDOREDUCTASE;

ARTICLE; BILE ACID SYNTHESIS; CHROMOSOME 5Q; CONTROLLED STUDY; DISORDERS OF PEROXISOMAL FUNCTIONS; ENZYME ACTIVITY; ENZYME ANALYSIS; GENE MAPPING; HUMAN; HUMAN TISSUE; IMMUNOBLOTTING; LIVER; PEROXISOME; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEIN PURIFICATION; ZELLWEGER SYNDROME;

3-HYDROXYACYL COA DEHYDROGENASES; ANIMALS; BASE SEQUENCE; BILE ACIDS AND SALTS; CHROMATOGRAPHY, ION EXCHANGE; CHROMOSOME MAPPING; ENOYL-COA HYDRATASE; HUMANS; ISOMERASES; LIVER; MOLECULAR SEQUENCE DATA; MULTIENZYME COMPLEXES; RATS; STEREOISOMERISM; SUBCELLULAR FRACTIONS; ZELLWEGER SYNDROME;

EID: 0030976855     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0925-4439(97)00003-3     Document Type: Article

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