Molecular characterization of the human peroxisomal branchedchain acyl-CoA oxidase: cDNA cloning, chromosomal assignment, tissue distribution, and evidence for the absence of the protein in Zellweger syndrome

Proceedings of the National Academy of Sciences of the United States of America

Volumn 93, Issue 24, 1996, Pages 13748-13753

  Baumgart, Eveline ^a   Vanhooren, Johannes C T ^a   Fransen, Mark ^a   Marynen, Peter ^a   Puype, Magda ^b   Vandekerckhove, Joël ^b   Leunissen, Jack A M ^c   Fahimi, H Dariush ^d   Mannaerts, Guy P ^a   Van Veldhoven, Paul P ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b GHENT UNIVERSITY   (Belgium)

^c RADBOUD UNIVERSITY NIJMEGEN   (Netherlands)

^d UNIVERSITY OF HEIDELBERG   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

ACYL COENZYME A OXIDASE; COMPLEMENTARY DNA;

CHROMOSOMAL LOCALIZATION; CHROMOSOME 3P; CONFERENCE PAPER; ENZYME DEFECT; ENZYME SPECIFICITY; ENZYME SUBSTRATE; FATTY ACID OXIDATION; FLUORESCENCE IN SITU HYBRIDIZATION; HEART; HUMAN; HUMAN TISSUE; KIDNEY; LIPID METABOLISM; LIVER; MOLECULAR CLONING; PEROXISOME; PRIORITY JOURNAL; TISSUE DISTRIBUTION; ZELLWEGER SYNDROME;

AMINO ACID SEQUENCE; ANIMALS; BASE SEQUENCE; CHILD; CHROMOSOME MAPPING; CHROMOSOMES, HUMAN, PAIR 3; CLONING, MOLECULAR; DNA, COMPLEMENTARY; EVOLUTION; HUMANS; IN SITU HYBRIDIZATION, FLUORESCENCE; LIVER; MICROBODIES; MOLECULAR SEQUENCE DATA; ORGAN SPECIFICITY; OXIDOREDUCTASES; RATS; TRANSCRIPTION, GENETIC; ZELLWEGER SYNDROME;

MAMMALIA;

EID: 0030462605     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.93.24.13748     Document Type: Article

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