Leber hereditary optic neuropathy: How do mitochondrial DNA mutations cause degeneration of the optic nerve?

Journal of Bioenergetics and Biomembranes

Volumn 29, Issue 2, 1997, Pages 165-173

  Howell, Neil ^a  

^a University of Texas Medical Branch School of Medicine   (United States)

Author keywords

Complex I; Leber hereditary optic neuropathy (LHON); Maternal inheritance; Mitochondrial DNA; Neurodegeneration; Optic nerve

Indexed keywords

MITOCHONDRIAL DNA;

ARTICLE; EXTRACHROMOSOMAL INHERITANCE; GENE MUTATION; HEREDITARY OPTIC ATROPHY; HUMAN; MITOCHONDRIAL RESPIRATION; NERVE DEGENERATION; NEUROLOGIC DISEASE; NEUROPATHOLOGY; OPTIC NERVE; RESPIRATORY CHAIN;

DNA, MITOCHONDRIAL; ELECTRON TRANSPORT; HUMANS; MODELS, BIOLOGICAL; MUTATION; NERVE DEGENERATION; NERVOUS SYSTEM DISEASES; OPTIC ATROPHIES, HEREDITARY; OPTIC NERVE;

EID: 0030788483     PISSN: 0145479X     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1022690030664     Document Type: Article

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