Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype-phenotype correlations

EMBO Journal

Volumn 15, Issue 5, 1996, Pages 955-963

  Delaney, Stephen J ^a   Alton, Eric W F W ^b   Smith, Stephen N ^b   Lunn, Dominic P ^a   Farley, Ray ^b   Lovelock, Paul K ^a   Thomson, Scott A ^a   Hume, David A ^a   Lamb, David ^d   Porteous, David J ^c   Dorin, Julia R ^c   Wainwright, Brandon J ^a  

^a UNIVERSITY OF QUEENSLAND   (Australia)

^b NATIONAL HEART AND LUNG INSTITUTE   (United Kingdom)

^c WESTERN GENERAL HOSPITAL   (United Kingdom)

^d UNIVERSITY OF EDINBURGH   (United Kingdom)

Author keywords

Animal models; Cystic fibrosis; Gene targeting; Genotype phenotype correlations; Meconium ileus

Indexed keywords

CHLORIDE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHLORIDE TRANSPORT; CONTROLLED STUDY; CYSTIC FIBROSIS; EMBRYO; GENE MUTATION; GENE TARGETING; GENOTYPE; INCIDENCE; INTESTINE OBSTRUCTION; MALE; MECONIUM ILEUS; MISSENSE MUTATION; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; RISK; SURVIVAL;

ANIMALIA;

EID: 9044236531     PISSN: 02614189     EISSN: None     Source Type: Journal    
DOI: 10.1002/j.1460-2075.1996.tb00432.x     Document Type: Article

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