Prevalence, pathophysiology, diagnosis, and treatment of Willebrand syndrome in orthopedic-trauma patients;Pravalenz, pathophysiologie, diagnostik und therapie des von-Willebrand- syndroms bei orthopadisch-trauma-tologischen patienten

Orthopade

Volumn 28, Issue 4, 1999, Pages 366-374

  Kurth, A A ^a,b   Ludwig, G ^a   Scharrer, I ^a  

^a UNIVERSITY HOSPITAL FRANKFURT   (Germany)

^b Stiftung Friedrichsheim   (Germany)

Author keywords

Diagnosis; Pathophysiology; Prevalence; Therapy; Willebrand's Disease

Indexed keywords

BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR 8 CONCENTRATE; DESMOPRESSIN; RISTOCETIN; THROMBOPLASTIN; VON WILLEBRAND FACTOR;

BLEEDING; BLEEDING TIME; DISEASE SEVERITY; EPISTAXIS; HUMAN; HYPERMENORRHEA; INJURY; ORTHOPEDIC SURGERY; PARTIAL THROMBOPLASTIN TIME; PATHOPHYSIOLOGY; PRACTICE GUIDELINE; PREVALENCE; REVIEW; THROMBOCYTE ADHESION; VON WILLEBRAND DISEASE; ANIMAL; ARTICLE; BLOOD CLOTTING DISORDER; CLASSIFICATION; MOUSE; ORTHOPEDICS; THROMBOCYTE ADHESIVENESS;

ANIMALS; BLOOD COAGULATION DISORDERS; BLOOD LOSS, SURGICAL; HUMANS; MICE; ORTHOPEDICS; PARTIAL THROMBOPLASTIN TIME; PLATELET ADHESIVENESS; PREVALENCE; VON WILLEBRAND DISEASE; VON WILLEBRAND FACTOR; WOUNDS AND INJURIES;

EID: 85047677091     PISSN: 00854530     EISSN: None     Source Type: Journal    
DOI: 10.1007/PL00003619     Document Type: Review

References (25)

1. Aledort LM (1991) Treatment of von Willebrand's disease. Mayo Clin Proc 66: 841-846
2. Berntrop E, Nilson IM (1989) Use of high purity factor VIII concentrate (Hemate P) in von Willebrand disease. Vox Sang 56: 212-217
3. Bloom AL (1991) von Willebrand factor: Clinical features of inherited and acquired disorders. Mayo Clin Proc 66: 743-751
4. Federici AB (1998) Diagnosis of von Willebrand disease. Haemophilia 4: 654-660
5. Forster PA (1995) A perspective on the use of FVIII concentrates and cryocrepitate prophylactically in surgery and therapeutically in severe bleeds in patients with von Willebrand disease unresponsive to DDAVP: results of an international survey. Thromb Haemost 74: 1370-1378
6. Furlan M (1996) von Willebrand factor: molecular size and functional activity. Ann Hematol 72: 341-348
7. Holmberg L, Nilson IM (1985) von Willebrand disease. Clin Haematol 14: 461-488
8. Humphreis JE, Siragy H (1993) Significant hyponatremia following DDAVP administration in a healthy adult. Am J Haematol 44: 12-15
9. Mannucci PM (1998) Treatment of von Willebrand disease. Haemophilia 4: 661-664
10. Mannucci PM, Bettega D, Cattaneo M (1992) Patterns of development of tachyphylaxis in patients with haemophilia and von Willebrand disease after repeated doses of desmopressin (DDAVP). Br J Haematolo 82: 87-93
11. Mazurier C (1996) Molecular genetics of von Willebrand disease. Haemophilia 2 [Supp 1]: 9
12. Miller C, Lenzi R, Breen (1987) Prevalence of von Willebrand's disease among U. S. adults. Blood 70: 377
13. Murray EW, Lillicrap D (1996) von Willebrand disease: Pathogenesis, classification and management. Trans Med Rev 10: 93-110
14. Nischino M, Girma J-P, Rothschild C, Fressinaud E, Meyer D (1989) New variant of von Willebrand disease with defective binding to factor VII. Blood 74: 1591-1599
15. Rodeghiero F, Castaman G, Dini E (1987) Epidemiological investigation of the prevalence of von Willebrand's disease. Blood 69: 454-459
16. Rodeghiero F, Castaman G, Mannucci PM (1991) Clinical indications for desmopressin (DDAVP) in congenital and acquired von Willebrand disease. Blood Rev 5: 155-161
17. Ruggeri Z, Zimmerman T (1987) von Willebrand factor and von Willebrand disease. Blood 70: 895-904
18. Ruggeri ZM (1994) Pathogenesis and classification of von Willebrand disease. Haemostasis 24: 265-275
19. Ruggeri ZM, Ware J (1992) The structure and function of von Willebrand factor. Thromb Haemost 67: 594-599
20. Sadler EJ (1994) A revised classification of von Willebrand disease. Thromb Haemostas 71: 520-525
21. Scharrer I (1991) The treatment of von Willebrand's disease. In: Lusher JM Kessler CM (eds) Hemophilia and von Willebrand disease in the 1990's. Elsevier, Amsterdam New York
22. Scharrer I, Vigh T, Aygörön-Pürsün E (1994) Experience with Hemate P in v. Willebrand's disease in adults. Haemostasis 24: 298-303
23. Scott JR Gill JC, Rock A et al. (1993) The effect of ABO type on the synthesis, release, and platelet bindings of von Willebrand factor (vWF). Thromb Haemost 69: 946
24. Triplett DA (1991) Laboratory diagnosis of von Willebrand's disease. Mayo Clin Proc 66: 832-840
25. von Willebrand EA (1926) Hereditar pseudohemophili. Finska Lakarsallskapets Handlingar 67: 7-112