Macrophage activation syndrome in Still’s disease: analysis of clinical characteristics and survival in paediatric and adult patients

Clinical Rheumatology

Volumn 36, Issue 12, 2017, Pages 2839-2845

  Ruscitti, Piero ^a   Rago, Carmela ^a   Breda, Luciana ^b   Cipriani, Paola ^a   Liakouli, Vasiliki ^a   Berardicurti, Onorina ^a   Carubbi, Francesco ^a   Di Battista, Caterina ^b   Verrotti, Alberto ^a   Giacomelli, Roberto ^a  

^a UNIVERSITY OF L'AQUILA   (Italy)

^b UNIVERSITY OF CHIETI   (Italy)

Author keywords

Adult onset Still s disease; Ferritin; Hyperferritinemic syndrome; Macrophage activation syndrome; Survival

Indexed keywords

ALANINE AMINOTRANSFERASE; ANAKINRA; ASPARTATE AMINOTRANSFERASE; C REACTIVE PROTEIN; CORTICOSTEROID; CYCLOSPORIN; CYCLOSPORIN A; DISEASE MODIFYING ANTIRHEUMATIC DRUG; FERRITIN; HEMOGLOBIN; METHOTREXATE; NONSTEROID ANTIINFLAMMATORY AGENT; TRIACYLGLYCEROL; TUMOR NECROSIS FACTOR INHIBITOR;

ABDOMINAL PAIN; ADULT; ADULT ONSET STILL DISEASE; ALANINE AMINOTRANSFERASE BLOOD LEVEL; ARTHRALGIA; ARTHRITIS; ARTICLE; ASPARTATE AMINOTRANSFERASE BLOOD LEVEL; CHILD; CLINICAL FEATURE; CLINICAL OUTCOME; COHORT ANALYSIS; COMORBIDITY; CONTROLLED STUDY; CYTOPENIA; DISEASE SEVERITY; ERYTHROCYTE COUNT; ERYTHROCYTE SEDIMENTATION RATE; FEMALE; FERRITIN BLOOD LEVEL; FEVER; FOLLOW UP; HEMOGLOBIN BLOOD LEVEL; HUMAN; IMMUNOSUPPRESSIVE TREATMENT; INFECTION; LEUKOCYTE COUNT; LEUKOCYTOSIS; LIVER FUNCTION; LYMPHADENITIS; LYMPHADENOPATHY; MACROPHAGE ACTIVATION SYNDROME; MAJOR CLINICAL STUDY; MALE; MIDDLE AGED; MULTIPLE ORGAN FAILURE; MYALGIA; PERICARDITIS; PLEURISY; PNEUMONIA; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; RASH; RESPIRATORY DISTRESS SYNDROME; RETROSPECTIVE STUDY; SCHOOL CHILD; SORE THROAT; SPLENOMEGALY; SURVIVAL; THROMBOCYTE COUNT; TRIACYLGLYCEROL BLOOD LEVEL; ADOLESCENT; COMPLICATION; JUVENILE RHEUMATOID ARTHRITIS; MORTALITY; PRESCHOOL CHILD; PROGNOSIS;

ADOLESCENT; ADULT; ARTHRITIS, JUVENILE; CHILD; CHILD, PRESCHOOL; FEMALE; HUMANS; MACROPHAGE ACTIVATION SYNDROME; MALE; MIDDLE AGED; PROGNOSIS; RETROSPECTIVE STUDIES; STILL'S DISEASE, ADULT-ONSET;

EID: 85029546064     PISSN: 07703198     EISSN: 14349949     Source Type: Journal    
DOI: 10.1007/s10067-017-3830-3     Document Type: Article

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