Muscle pathology, limb strength, walking gait, respiratory function and neurological impairment establish disease progression in the p.N155K canine model of X-linked myotubular myopathy

Annals of Translational Medicine

Volumn 3, Issue 18, 2015, Pages

  Goddard, Melissa A ^a   Mack, David L ^a   Czerniecki, Stefan M ^a   Kelly, Valerie E ^a   Snyder, Jessica M ^b   Grange, Robert W ^c   Lawlor, Michael W ^d   Smith, Barbara K ^e   Beggs, Alan H ^f   Childers, Martin K ^a  

^a UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF WASHINGTON   (United States)

^c VIRGINIA POLYTECHNIC INSTITUTE AND STATE UNIVERSITY   (United States)

^d MEDICAL COLLEGE OF WISCONSIN   (United States)

^e UNIVERSITY OF FLORIDA   (United States)

^f BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

Animal models; Dog; Muscle disease; Muscular dystrophy; Myopathy; Myotubular myopathy

Indexed keywords

EID: 85015501835     PISSN: 23055839     EISSN: 23055847     Source Type: Journal    
DOI: 10.3978/j.issn.2305-5839.2015.10.31     Document Type: Article

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