Interstitial lung disease caused by STING-associated vasculopathy with onset in infancy

American Journal of Respiratory and Critical Care Medicine

Volumn 194, Issue 5, 2016, Pages 639-642

  Clarke, Sarah L N ^a,b   Pellowe, Elizabeth J ^a   De Jesus, Adriana A ^c   Goldbach Mansky, Raphaela ^c   Hilliard, Tom N ^a   Ramanan, Athimalaipet V ^a  

^a BRISTOL ROYAL HOSPITAL FOR CHILDREN   (United Kingdom)

^b UNIVERSITY OF BRISTOL   (United Kingdom)

^c NATIONAL INSTITUTES OF HEALTH   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ADAPTOR PROTEIN; ANTIBIOTIC AGENT; IMMUNOGLOBULIN; METHYLPREDNISOLONE; STING PROTEIN; UNCLASSIFIED DRUG; MEMBRANE PROTEIN;

ANTIBIOTIC THERAPY; AUTOIMMUNE DISEASE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; COUGHING; ELECTRON MICROSCOPY; EPITHELIUM HYPERPLASIA; ERYTHEMA; FAILURE TO THRIVE; FEVER; GENETIC ANALYSIS; GENETIC SCREENING; HUMAN; IMMUNOLOGICAL PROCEDURES; INFANT; INFANT DISEASE; INTERSTITIAL LUNG DISEASE; KIDNEY FUNCTION TEST; LABORATORY TEST; LETTER; LEUKOCYTE COUNT; LIVER FUNCTION TEST; LUNG BIOPSY; LUNG LAVAGE; LYMPHOCYTIC INFILTRATION; MACULOPAPULAR RASH; MALE; MICROCYTIC ANEMIA; NOSE FEEDING; OXYGEN THERAPY; PRIORITY JOURNAL; RESPIRATORY DISTRESS; SKIN BIOPSY; STING ASSOCIATED VASCULOPATHY WITH ONSET IN INFANCY; TACHYPNEA; THORAX RADIOGRAPHY; THYROID FUNCTION TEST; VASCULAR DISEASE; VASCULITIS; GENETICS; INFLAMMATION; MUTATION; PASSIVE IMMUNIZATION; PROCEDURES;

HUMANS; IMMUNIZATION, PASSIVE; INFANT; INFLAMMATION; LUNG DISEASES, INTERSTITIAL; MALE; MEMBRANE PROTEINS; MUTATION; VASCULAR DISEASES;

EID: 84988883129     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.201510-2102LE     Document Type: Letter

References (11)

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