Favism, the commonest form of severe hemolytic anemia in Palestinian children, varies in severity with three different variants of G6PD deficiency within the same community

Blood Cells, Molecules, and Diseases

Volumn 60, Issue , 2016, Pages 58-64

  Reading, N Scott ^a,b   Sirdah, Mahmoud M ^b,c   Shubair, Mohammad E ^d   Nelson, Benjamin E ^a   Al Kahlout, Mustafa S ^e   Al Tayeb, Jamal M ^e   Aboud, Lina N ^e   Shaban, Maysaa Abu ^f   Luzzatto, Lucio ^g   Prchal, Josef T ^a,b  

^a ARUP INSTITUTE FOR CLINICAL AND EXPERIMENTAL PATHOLOGY   (United States)

^b UNIVERSITY OF UTAH SCHOOL OF MEDICINE   (United States)

^c AL AZHAR UNIVERSITY   (Palestine)

^d Islamic University Gaza   (Palestine)

^e Al Nasser Pediatric Hospital   (Palestine)

^f Maternity Hospital   (Palestine)

^g MUHIMBILI UNIVERSITY OF HEALTH AND ALLIED SCIENCES   (Tanzania)

Author keywords

Favism; G6PD Cairo; G6PD deficiency; Gaza; Palestine

Indexed keywords

BILIRUBIN; HEMOGLOBIN; GLUCOSE 6 PHOSPHATE DEHYDROGENASE; GLUCOSE-6-PHOSPHATE DEHYDROGENASE A-;

ADULT; ARTICLE; BILIRUBIN BLOOD LEVEL; BLOOD TRANSFUSION; CHILD; COMMUNITY ASSESSMENT; COMPARATIVE STUDY; CONTROLLED STUDY; DELAYED RECOVERY; DISEASE SEVERITY; FAVISM; FEMALE; GENE FREQUENCY; GENE MUTATION; GENETIC VARIABILITY; GENOTYPE; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY A; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY CAIRO; GLUCOSE 6 PHOSPHATE DEHYDROGENASE DEFICIENCY MEDITERRANEAN; HEALING IMPAIRMENT; HEMOGLOBINURIA; HEMOLYTIC ANEMIA; HETEROZYGOTE DETECTION; HUMAN; HYPERBILIRUBINEMIA; MAJOR CLINICAL STUDY; MALE; NEWBORN; PALESTINIAN; PREVALENCE; PRIORITY JOURNAL; RETICULOCYTE COUNT; RETICULOCYTOSIS; ARAB; BLOOD SAMPLING; DNA SEQUENCE; GENETIC VARIATION; GENETICS; PATHOLOGY; PRESCHOOL CHILD;

ANEMIA, HEMOLYTIC; ARABS; BLOOD SPECIMEN COLLECTION; CHILD; CHILD, PRESCHOOL; FAVISM; FEMALE; GENETIC VARIATION; GLUCOSEPHOSPHATE DEHYDROGENASE; GLUCOSEPHOSPHATE DEHYDROGENASE DEFICIENCY; HUMANS; MALE; SEQUENCE ANALYSIS, DNA;

EID: 84978484183     PISSN: 10799796     EISSN: 10960961     Source Type: Journal    
DOI: 10.1016/j.bcmd.2016.07.001     Document Type: Article

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