Hematopoietic stem cell transplantation outcomes for 11 patients with dedicator of cytokinesis 8 deficiency

Journal of Allergy and Clinical Immunology

Volumn 138, Issue 3, 2016, Pages 852-859.e3

  Al Herz, Waleed ^a,b   Chu, Julia I ^c,d   van der Spek, Jet ^c   Raghupathy, Raj ^a   Massaad, Michel J ^c   Keles, Sevgi ^c   Biggs, Catherine M ^c   Cockerton, Lucinda ^e   Chou, Janet ^c   Dbaibo, Ghassan ^f   Elisofon, Scott A ^c   Hanna Wakim, Rima ^f   Kim, Heung Bae ^c   Lehmann, Leslie E ^c,d   McDonald, Douglas R ^c   Notarangelo, Luigi D ^c   Veys, Paul ^e   Chatila, Talal A ^c   Geha, Raif S ^c   Gaspar, H Bobby ^e,g   Pai, Sung Yun ^c,d   more..

^a KUWAIT UNIVERSITY   (Kuwait)

^b AL SABAH HOSPITAL   (Kuwait)

^c BOSTON CHILDREN S HOSPITAL   (United States)

^d DANA FARBER CANCER INSTITUTE   (United States)

^e GREAT ORMOND STREET HOSPITAL   (United Kingdom)

^f AMERICAN UNIVERSITY OF BEIRUT   (Lebanon)

^g UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

conditioning; dedicator of cytokinesis 8 deficiency; hematopoietic stem cell transplantation; mixed chimerism; Primary immunodeficiency

Indexed keywords

IMMUNOGLOBULIN E; CYTOKINE; DOCK8 PROTEIN, HUMAN; GUANINE NUCLEOTIDE EXCHANGE FACTOR;

ANTIBODY RESPONSE; ARTICLE; ASTHMA; CANDIDIASIS; CD8+ T LYMPHOCYTE; CHILD; CHIMERA; CHRONIC GRAFT VERSUS HOST DISEASE; CLINICAL ARTICLE; COMBINED IMMUNODEFICIENCY; CYTOKINE PRODUCTION; CYTOMEGALOVIRUS INFECTION; DEDICATOR OF CYTOKINESIS 8 DEFICIENCY; DISEASE REGISTRY; DISEASE SEVERITY; ECZEMA; EOSINOPHILIA; EPSTEIN BARR VIRUS INFECTION; FEMALE; FLOW CYTOMETRY; FOOD ALLERGY; GENE MUTATION; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HERPES SIMPLEX; HERPES ZOSTER; HUMAN; HUMORAL IMMUNITY; LIVER TRANSPLANTATION; LYMPHOCYTE SUBPOPULATION; LYMPHOCYTOPENIA; MALE; MEDICAL RECORD REVIEW; MEMORY CELL; MOLLUSCUM CONTAGIOSUM; OPPORTUNISTIC INFECTION; OUTCOME ASSESSMENT; PAPILLOMAVIRUS INFECTION; PERIPHERAL BLOOD MONONUCLEAR CELL; PRIORITY JOURNAL; RESEARCH; RETROSPECTIVE STUDY; SURVIVAL; TH1 CELL; TH2 CELL; UNRELATED DONORS; VACCINATION; B LYMPHOCYTE; DEFICIENCY; IMMUNE DEFICIENCY; IMMUNOLOGY; MONONUCLEAR CELL; PRESCHOOL CHILD; T LYMPHOCYTE; TREATMENT OUTCOME;

B-LYMPHOCYTES; CHILD; CHILD, PRESCHOOL; CYTOKINES; FEMALE; GUANINE NUCLEOTIDE EXCHANGE FACTORS; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; LEUKOCYTES, MONONUCLEAR; MALE; T-LYMPHOCYTES; TREATMENT OUTCOME;

EID: 84964691178     PISSN: 00916749     EISSN: 10976825     Source Type: Journal    
DOI: 10.1016/j.jaci.2016.02.022     Document Type: Article

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