Clinical and pathophysiological clues of respiratory dysfunction in late-onset Pompe disease: New insights from a comparative study by MRI and respiratory function assessment

Neuromuscular Disorders

Volumn 25, Issue 11, 2015, Pages 852-858

  Gaeta, Michele ^a   Musumeci, Olimpia ^a   Mondello, Stefania ^a   Ruggeri, Paolo ^a   Montagnese, Federica ^a   Cucinotta, Maria ^a   Vinci, Sergio ^a   Milardi, Demetrio ^a   Toscano, Antonio ^a  

^a UNIVERSITY OF MESSINA   (Italy)

Author keywords

Diaphragm; Pompe disease; Respiratory muscles MRI

Indexed keywords

ADULT; ARTICLE; BREATHING MUSCLE; CLINICAL ARTICLE; CLINICAL FEATURE; COMPARATIVE STUDY; CONTROLLED STUDY; CORRELATION ANALYSIS; DIAPHRAGM MOVEMENT; DIAPHRAGM MUSCLE; EXPIRATORY FLOW; FEMALE; FORCED EXPIRATORY VOLUME; FORCED VITAL CAPACITY; GLYCOGEN STORAGE DISEASE TYPE 2; HUMAN; INSPIRATORY CAPACITY; INTERCOSTAL MUSCLE; LUNG FUNCTION; LUNG FUNCTION TEST; LUNG VOLUME; MALE; MUSCLE WEAKNESS; NUCLEAR MAGNETIC RESONANCE IMAGING; NUCLEAR MAGNETIC RESONANCE SCANNER; OUTCOME ASSESSMENT; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RELIABILITY; REPRODUCIBILITY; RESPIRATORY FAILURE; ONSET AGE; PATHOLOGY;

ADULT; AGE OF ONSET; FEMALE; GLYCOGEN STORAGE DISEASE TYPE II; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; RESPIRATORY FUNCTION TESTS; RESPIRATORY INSUFFICIENCY; RESPIRATORY MUSCLES;

EID: 84962359819     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2015.09.003     Document Type: Article

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