Autosomal Dominant Hyper IgE Syndrome – Treatment Strategies and Clinical Outcomes

Journal of Clinical Immunology

Volumn 36, Issue 2, 2016, Pages 107-109

  Flinn, Aisling M ^a   Cant, Andrew ^b   Leahy, T Ronan ^a   Butler, Karina M ^a   Gennery, Andrew R ^b  

^a OUR LADY S CHILDREN S HOSPITAL   (Ireland)

^b NEWCASTLE UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIBIOTIC AGENT; ANTIFUNGAL AGENT; AZITHROMYCIN; COTRIMOXAZOLE; FLUCLOXACILLIN; IMMUNOGLOBULIN G; ITRACONAZOLE; STAT3 PROTEIN; VORICONAZOLE;

ADOLESCENT; ANTIBIOTIC PROPHYLAXIS; ANTIBODY RESPONSE; ASPERGILLOSIS; ASPERGILLUS FUMIGATUS; AUTOSOMAL DOMINANT DISORDER; BRONCHIECTASIS; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; EXON SKIPPING; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMAN; HYPER IGE SYNDROME; INFANT; INFECTION; LETTER; LOWER RESPIRATORY TRACT INFECTION; LUNG INJURY; MALE; OUTCOME ASSESSMENT; PNEUMATOCELE; PRESCHOOL CHILD; PRIORITY JOURNAL; SCHOOL CHILD; SKIN INFECTION; SPLICING DEFECT; DISEASE MANAGEMENT; JOB SYNDROME; TREATMENT OUTCOME;

DISEASE MANAGEMENT; HUMANS; JOB SYNDROME; TREATMENT OUTCOME;

EID: 84959217110     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-015-0231-8     Document Type: Letter

References (5)

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5. Chandesris MO, Melki I, Natividad A, Puel A, Fieschi C, Yun L, et al. Autosomal dominant STAT3 deficiency and hyper-IgE syndrome: molecular, cellular, and clinical features from a French national survey. Medicine. 2012;91:e1–e19.