Management of Sickle Cell Disease in Childhood

Practical Management of Haemoglobinopathies

Volumn , Issue , 2007, Pages 76-87

  Dick, Moira ^a  

^a KING S COLLEGE HOSPITAL   (United Kingdom)

Author keywords

Haemoglobinopathy; Incentive spirometry; Neonatal screening; Penicillin prophylaxis; Sickle cell disease (SCD) mangement

Indexed keywords

EID: 84952320602     PISSN: None     EISSN: None     Source Type: Book    
DOI: 10.1002/9780470988398.ch9     Document Type: Chapter

References (30)

1. Center for Diseases Control, USA. Mortality among children with sickle cell disease identified by newborn screening during 1990-4 - California, Illinois, and New York. MMWR 1998; 47: 169-72.
2. Pegelow CH, Macklin EA, Moser FG et al. Longitudinal changes in brain magnetic resonance imaging findings in children with sickle cell disease. Blood 2002; 99: 3014-18.
3. NHS Plan. A Plan for Investment a Plan for Reform. www.nhs.uk/nhsplan.
4. Gaston MH, Verter JI, Woods G et al. Prophylaxis with oral penicillin in children with sickle cell anemia. N Engl J Med 1986; 314: 1593-9.
5. Chief Medical Officer guidance (2002) Pneumococcal vaccine for at risk under 2 year olds. http://www.doh.gov.uk/co/cmo0201.
6. Finn A, Booy R, Moxon R, Sharland M, Heath P. Should the new pneumococcal vaccine be used in high risk children? Arch Dis Child 2002; 87: 18-21.
7. Oni L, Dick M, Smalling B, Walters J. Care and Management of Your Child - Sickle Cell Disease, A Parents' Guide. Brent Sickle Cell & Thalassaemia Centre, 1997.
8. Maxwell K, Streetly A. Living with sickle cell pain. Nurs Stand 1998; 13: 33.
9. Pegelow CH, Colangelo L, Steinberg M et al. Natural history of blood pressure in sickle cell disease: risks for stroke and death associated with relative hypertension in sickle cell anaemia. Am J Med 1997; 102: 171-7.
10. Patey RA, Sylvester KP, Rafferty GF, Dick M, Greenough A. The importance of using ethnically appropriate reference ranges for growth assessment in sickle cell disease. Arch Dis Child 2002; 87: 352-3.
11. Reed JD, Redding-Lallinger R, Orringer EP. Nutrition and sickle cell disease. Am J Haematol 1987; 24: 441-55.
12. Serjeant GR, Singhal A, Hambleton IR. Sickle cell disease and age at menarche in Jamaican girls: observations from a cohort study. Arch Dis Child 2001; 85: 375-8.
13. Hall DMB, Elliman D. Health for All Children, 4th edn. Oxford: Oxford University Press, 2003.
14. Ohene-Frempong K, Weiner SJ, Sleeper LA et al. Cere-brovascular accidents in sickle cell disease and risk factors. Blood 1998; 91: 288-94.
15. Adams RJ, McKie VC, Hsu L et al. Prevention of first stroke by transfusions in children with sickle cell anaemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med 1998; 339: 5-11.
16. Platt OS, Brambilla DJ, Rosse WF et al. Mortality in sickle cell diease. Life expectancy and risk factors for early death. N Engl J Med 1994; 330: 1639-44.
17. Miller ST, Sleeper LA, Pegelow CH et al. Prediction of adverse outcomes in children with sickle cell disease. N EnglJ Med 2000; 342: 1612-31.
18. Readett DR, Morris J, Serjeant GR. Determinants of nocturnal enuresis in homozygous sickle cell disease. Arch Dis Child 1990; 65: 615-81.
19. Brooks LJ, Topol HI. Enuresis in children with sleep apnoea. J Pediatr 2003; 142: 515-18.
20. Bond LR, Hatty SR, Horn ME et al. Gall stones in sickle cell disease in the United Kingdom. BMJ 1987; 295: 234-6.
21. Mantadakis E, Ewalt DH, Cavender JD, Rogers ZR, Buchanan GR. Outpatient penile aspiration and epi-nephrine irrigation for young patients with sickle cell anaemia and prolonged priapism. Blood 2000; 95: 78-82.
22. Helps S, Fuggle P, Udwin O, Dick M. Psychosocial and neurocognitive aspects of sickle cell disease. Child and Adolescent Mental Health 2003; 8: 11-17.
23. Qureshi J, Buckingham S. A pain assessment tool for all children. Paediatr Nurs 1994; 6: 11-13.
24. Rees DC, Olujohungbe AD, Parker NE et al. Guidelines for the management of the acute painful crisis in sickle cell disease. Br J Haematol 2003; 120: 744-52.
25. Bellett PS, Kalinyak KA, Shukla R, Gelland MJ, Rucknagel DL. Incentive spirometry to prevent acute pulmonary complications in sickle cell disease. N Engl J Med 1995; 333: 699-703.
26. Hargrave DR, Wade A, Evans JP, Hewes DK, Kirkham FJ. Nocturnal oxygen saturation and painful sickle cell crises in children. Blood 2003; 101: 846-8.
27. Roberts I. The role of hydroxyurea in sickle cell disease. Br J Haematol 2003; 120: 177-86.
28. Vichinksy EP, Lubin BH. A cautionary note regarding hydroxyurea in sickle cell disease. Blood 1994; 83: 1124-8.
29. Vichinsky EP, Haberkern CM, Neumayr L et al. A comparison of conservative and aggressive transfusion regimens in the peri-operative management of sickle cell disease. N Engl J Med 1995; 333: 251-2.
30. Griffin TC, Buchanan GR. Elective surgery in children with sickle cell disease without pre-operative blood transfusion. J Pediatr Surg 1993; 28: 681-5.