Severe and Rapid Progression in Very Early-Onset Chronic Granulomatous Disease-Associated Colitis

Journal of Clinical Immunology

Volumn 35, Issue 6, 2015, Pages 583-588

  Kawai, Toshinao ^a   Arai, Katsuhiro ^a   Harayama, Shizuko ^b   Nakazawa, Yumiko ^a   Goto, Fumihiro ^a   Maekawa, Takanobu ^a   Tamura, Eiichiro ^b   Uchiyama, Toru ^a   Onodera, Masafumi ^a  

^a NATIONAL CENTER FOR CHILD HEALTH AND DEVELOPMENT   (Japan)

^b JIKEI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

CGD colitis; Chronic granulomatous disease; granuloma; inflammation; pediatric ulcerative colitis activity index; very early onset CGD colitis

Indexed keywords

AZATHIOPRINE; C REACTIVE PROTEIN; CORTICOSTEROID; CYCLOSPORIN A; GAMMA INTERFERON; IMMUNOMODULATING AGENT; IMMUNOSUPPRESSIVE AGENT; MESALAZINE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE PHOSPHATE OXIDASE; THALIDOMIDE;

ADOLESCENT; ARTICLE; ASSESSMENT OF HUMANS; BACTERIAL INFECTION; CHILD; CHRONIC GRANULOMATOUS DISEASE; CHRONIC GRANULOMATOUS DISEASE ASSOCIATED COLITIS; CLINICAL ARTICLE; CLINICAL FEATURE; COLITIS; CONTROLLED STUDY; CORTICOSTEROID THERAPY; DISEASE ACTIVITY; DISEASE COURSE; DISEASE SEVERITY; ENTERITIS; ENZYME ACTIVITY; ERYTHROCYTE SEDIMENTATION RATE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMAN; LYMPHADENITIS; MEDICAL RECORD REVIEW; NEUTROPHIL; PEDIATRIC ULCERATIVE COLITIS ACTIVITY INDEX; PRESCHOOL CHILD; PRIORITY JOURNAL; RECTUM HEMORRHAGE; SCHOOL CHILD; THERAPY EFFECT; CHRONIC DISEASE; COMPLICATION; CROHN DISEASE; FEMALE; INFANT; JAPAN; MALE; ONSET AGE; RETROSPECTIVE STUDY;

ADOLESCENT; AGE OF ONSET; CHILD; CHILD, PRESCHOOL; CHRONIC DISEASE; COLITIS; CROHN DISEASE; DISEASE PROGRESSION; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; INFANT; JAPAN; MALE; RETROSPECTIVE STUDIES;

EID: 84942194604     PISSN: 02719142     EISSN: 15732592     Source Type: Journal    
DOI: 10.1007/s10875-015-0180-2     Document Type: Article

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