Congenital Hemophagocytic Lymphohistiocytosis Presenting as Thrombocytopenia in a Newborn

Journal of Pediatric Hematology/Oncology

Volumn 37, Issue 4, 2015, Pages 300-303

  Hinson, Ashley ^a   Owen, William ^b   Prose, Neil ^a   Parikh, Suhag ^a   Thornburg, Courtney ^c  

^a DUKE UNIVERSITY MEDICAL CENTER   (United States)

^b EASTERN VIRGINIA MEDICAL SCHOOL   (United States)

^c RADY CHILDREN'S HOSPITAL   (United States)

Author keywords

congenital; Griscelli; hemophagocytic lymphohistiocytosis; thrombocytopenia

Indexed keywords

ALEMTUZUMAB; CYCLOSPORIN A; DEXAMETHASONE; ETOPOSIDE; FLUDARABINE; HYDROXYUREA; IMMUNOGLOBULIN G; MELPHALAN; PHOSPHOLIPID ANTIBODY; PREDNISONE; SOLUBLE INTERLEUKIN 2 RECEPTOR; RAB PROTEIN; RAB27A PROTEIN, HUMAN;

ADULT; ARTICLE; CASE REPORT; CORD BLOOD STEM CELL TRANSPLANTATION; DESQUAMATION; DIFFERENTIAL DIAGNOSIS; DISEASE ASSOCIATION; DRUG TOLERABILITY; EDEMA; FEMALE; FERTILIZATION IN VITRO; FEVER; GRISCELLI SYNDROME; HEMODYNAMICS; HEMOPHAGOCYTIC SYNDROME; HEPATOMEGALY; HEPATOSPLENOMEGALY; HUMAN; HYPERBILIRUBINEMIA; HYPERFERRITINEMIA; HYPERPIGMENTATION; HYPERSPLENISM; IMMUNE DEFICIENCY; INFANT; JUVENILE MYELOMONOCYTIC LEUKEMIA; MYELOID METAPLASIA; NEONATAL ALLOIMMUNE THROMBOCYTOPENIA; NEPHROTOXICITY; NEWBORN; PETECHIA; POSTOPERATIVE PERIOD; PREGNANCY; PRIORITY JOURNAL; REDUCED INTENSITY CONDITIONING; RESPIRATORY FAILURE; SEPSIS; SPLENECTOMY; SPONTANEOUS ABORTION; THROMBOCYTE TRANSFUSION; GENETICS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; PIEBALDISM; THROMBOCYTOPENIA;

ADULT; FEMALE; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT, NEWBORN; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; PIEBALDISM; RAB GTP-BINDING PROTEINS; THROMBOCYTOPENIA;

EID: 84937965866     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0000000000000234     Document Type: Article

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