Respiratory muscle dysfunction in facioscapulohumeral muscular dystrophy

Neuromuscular Disorders

Volumn 25, Issue 8, 2015, Pages 632-639

  Santos, Dante Brasil ^a,b   Boussaid, Ghilas ^a   Stojkovic, Tanya ^c   Orlikowski, David ^a,d   Letilly, Nadege ^d   Behin, Anthony ^c   Butel, Sandrine ^d   Lofaso, Frédéric ^a,d   Prigent, Hélène ^a,d  

^a LABORATOIRE DES SCIENCES DU CLIMAT ET DE L ENVIRONNEMENT   (France)

^b HOSPITAL UNIVERSITÁRIO DE BRASÍLIA   (Brazil)

^c PITIÉ SALPÊTRIÈRE HOSPITAL   (France)

^d RAYMOND POINCARÉ HOSPITAL   (France)

Author keywords

Facioscapulohumeral muscular dystrophy; Mechanical ventilation; Neuromuscular respiratory dysfunction; Pulmonary function tests; Respiratory failure

Indexed keywords

ACUTE RESPIRATORY FAILURE; ADULT; AGED; ARTICLE; ARTIFICIAL VENTILATION; BODY MASS; CASE CONTROL STUDY; CHRONIC HYPERCAPNIA; CLINICAL ARTICLE; COMPARATIVE STUDY; CONTROLLED STUDY; COUGHING; DISEASE SEVERITY; EXPIRATORY MUSCLE DYSFUNCTION; EXPIRATORY RESERVE VOLUME; FACIOSCAPULOHUMERAL MUSCULAR DYSTROPHY; FEMALE; FOLLOW UP; HUMAN; HYPERCAPNIA; INEFFECTIVE COUGH; INSPIRATORY CAPACITY; LUNG CLEARANCE; MALE; MAXIMAL INSPIRATORY PRESSURE; MIDDLE AGED; MUSCLE DISEASE; OXYGEN SATURATION; PRIORITY JOURNAL; RESPIRATORY FAILURE; RESPIRATORY MUSCLE DYSFUNCTION; RESPIRATORY TRACT PARAMETERS; SCORING SYSTEM; SLEEP DISORDERED BREATHING; SUPINE VITAL CAPACITY; TREATMENT INDICATION; UPRIGHT VITAL CAPACITY; VERY ELDERLY; VITAL CAPACITY; WALTON AND GARDNER MEDWIN SCORE; YOUNG ADULT; BREATHING MUSCLE; COMPLICATION; EXHALATION; MUSCLE WEAKNESS; PATHOPHYSIOLOGY;

ADULT; AGED; AGED, 80 AND OVER; EXHALATION; FEMALE; FOLLOW-UP STUDIES; HUMANS; MALE; MIDDLE AGED; MUSCLE WEAKNESS; MUSCULAR DYSTROPHY, FACIOSCAPULOHUMERAL; RESPIRATORY INSUFFICIENCY; RESPIRATORY MUSCLES; VITAL CAPACITY; YOUNG ADULT;

EID: 84937630981     PISSN: 09608966     EISSN: 18732364     Source Type: Journal    
DOI: 10.1016/j.nmd.2015.04.011     Document Type: Article

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