-
1
-
-
84937594869
-
-
2nd Edn. London, Cystic Fibrosis Trust
-
Cystic Fibrosis Trust. Standards for the Clinical Care of Children and Adults with Cystic Fibrosis in the UK. 2nd Edn. London, Cystic Fibrosis Trust, 2011. www.cysticfibrosis.org.uk/media/82070/CD_Standards_of_Care_Dec_11.pdf
-
(2011)
-
-
-
2
-
-
69549135253
-
Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensus
-
Heijermann H, Westerman E, Conway S, et al. Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: a European consensus. J Cyst Fibros 2009; 8: 295-315
-
(2009)
J Cyst Fibros
, vol.8
, pp. 295-315
-
-
Heijermann, H.1
Westerman, E.2
Conway, S.3
-
3
-
-
84937594870
-
Physiotherapy
-
In: Bush A, Alton EWFW, Davies JC, et al. eds., Basel, Karger
-
Pryor JA, Main E, Agent P, et al. Physiotherapy. In: Bush A, Alton EWFW, Davies JC, et al. eds. Cystic Fibrosis in the 21st Century. Progress in respiratory research, Vol 34. Basel, Karger, 2006; p. 303
-
(2006)
Cystic Fibrosis in the 21St Century. Progress in Respiratory Research
, vol.34
-
-
Pryor, J.A.1
Main, E.2
Agent, P.3
-
4
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
Ramsey BW, Davies J, McElvaney NG, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011; 365: 1663-1672
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
-
5
-
-
61349198184
-
Adherence to nebulised antibiotics in cystic fibrosis
-
Latchford G, Duff A, Quinn J, et al. Adherence to nebulised antibiotics in cystic fibrosis. Patient Educ Couns 2009; 75: 141-144
-
(2009)
Patient Educ Couns
, vol.75
, pp. 141-144
-
-
Latchford, G.1
Duff, A.2
Quinn, J.3
-
6
-
-
84869626743
-
Delivering a concentrated dose of colistin using adaptiveaerosol delivery reduces treatment time
-
Langman H, Orr A, McVean R, et al. Delivering a concentrated dose of colistin using adaptiveaerosol delivery reduces treatment time. J Cyst Fibros 2004; 3: S57
-
(2004)
J Cyst Fibros
, vol.3
, pp. S57
-
-
Langman, H.1
Orr, A.2
McVean, R.3
-
7
-
-
77950610703
-
Evaluation of the Target Inhalation Mode (TIM) breathing maneuver in simulated nebulizer therapy in patients with cystic fibrosis
-
Denyer J, Prince I, Dixon E, et al. Evaluation of the Target Inhalation Mode (TIM) breathing maneuver in simulated nebulizer therapy in patients with cystic fibrosis. J Aerosol Med Pulm Drug Deliv 2010; 23: Suppl. 1, S29-S36
-
(2010)
J Aerosol Med Pulm Drug Deliv
, vol.23
, pp. S29-S36
-
-
Denyer, J.1
Prince, I.2
Dixon, E.3
-
8
-
-
77950618366
-
Comparison and compliance in cystic fibrosis patients using either a halolite AAD system or a conventional high output nebuliser
-
Conway S, Dodd M, Marsden R, et al. Comparison and compliance in cystic fibrosis patients using either a halolite AAD system or a conventional high output nebuliser. J Cyst Fibros 2002; S67
-
(2002)
J Cyst Fibros
, pp. S67
-
-
Conway, S.1
Dodd, M.2
Marsden, R.3
-
9
-
-
84937573809
-
Inhalation therapy can be improved in CF patients by controlling the breathing pattern during inspiration
-
Mullinger B, Sommerer K, Herpich C, et al. Inhalation therapy can be improved in CF patients by controlling the breathing pattern during inspiration. J Cyst Fibros 2004; 3: S65
-
(2004)
J Cyst Fibros
, vol.3
, pp. S65
-
-
Mullinger, B.1
Sommerer, K.2
Herpich, C.3
-
10
-
-
0030995361
-
Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis
-
Frederiksen B, Koch C, Høiby N. Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis. Pediatr Pulmonol 1997; 23: 330-335
-
(1997)
Pediatr Pulmonol
, vol.23
, pp. 330-335
-
-
Frederiksen, B.1
Koch, C.2
Høiby, N.3
-
11
-
-
0014863955
-
Aerosol therapy in cystic fibrosis
-
Mearns MB. Aerosol therapy in cystic fibrosis. Arch Dis Child 1970; 45: 605-607
-
(1970)
Arch Dis Child
, vol.45
, pp. 605-607
-
-
Mearns, M.B.1
-
12
-
-
0019511799
-
Aerosol carbenicillin and gentamicin treatment of Pseudomonas aeruginosa in patients with cystic fibrosis
-
Hodson ME, Penketh ARL, Batten JC. Aerosol carbenicillin and gentamicin treatment of Pseudomonas aeruginosa in patients with cystic fibrosis. Lancet 1981; 2: 1137-1139
-
(1981)
Lancet
, vol.2
, pp. 1137-1139
-
-
Hodson, M.E.1
Penketh, A.2
Batten, J.C.3
-
13
-
-
84937594871
-
-
Annual Data Report 2013. Bromley, Cystic Fibrosis Trust
-
UK Cystic Fibrosis Registry. Annual Data Report 2013. Bromley, Cystic Fibrosis Trust, 2014. www.cysticfibrosis. org.uk/media/598466/annual-data-report-2013-jul14.pdf
-
(2014)
-
-
-
14
-
-
0033531143
-
Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis inhaled Tobramycin Study Group
-
Ramsey BW, Pepe MS, Quan JM, et al. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis inhaled Tobramycin Study Group. N Engl J Med 1999; 340: 23-30
-
(1999)
N Engl J Med
, vol.340
, pp. 23-30
-
-
Ramsey, B.W.1
Pepe, M.S.2
Quan, J.M.3
-
15
-
-
0036157901
-
Long-term benefits of inhaled tobramycin in adolescent patients with cystic fibrosis
-
Moss RB. Long-term benefits of inhaled tobramycin in adolescent patients with cystic fibrosis. Chest 2002; 121: 55-63
-
(2002)
Chest
, vol.121
, pp. 55-63
-
-
Moss, R.B.1
-
16
-
-
78449294500
-
An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis
-
Oermann CM, Retsch-Bogart GZ, Quittner AL, et al. An 18-month study of the safety and efficacy of repeated courses of inhaled aztreonam lysine in cystic fibrosis. Pediatr Pulmonol 2010; 45: 1121-1134
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 1121-1134
-
-
Oermann, C.M.1
Retsch-Bogart, G.Z.2
Quittner, A.L.3
-
17
-
-
55549137086
-
Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis
-
McCoy KS, Quittner AL, Oermann CM, et al. Inhaled aztreonam lysine for chronic airway Pseudomonas aeruginosa in cystic fibrosis. Am J Respir Crit Care Med 2008; 178: 921-928
-
(2008)
Am J Respir Crit Care Med
, vol.178
, pp. 921-928
-
-
McCoy, K.S.1
Quittner, A.L.2
Oermann, C.M.3
-
18
-
-
0029877773
-
Nebulised antipseudomonal antibiotic therapy in cystic fibrosis: A meta-analysis of benefits and risks
-
Mukhopadhyay S, Singh M, Cater JI, et al. Nebulised antipseudomonal antibiotic therapy in cystic fibrosis: a meta-analysis of benefits and risks. Thorax 1996; 51: 364-368
-
(1996)
Thorax
, vol.51
, pp. 364-368
-
-
Mukhopadhyay, S.1
Singh, M.2
Cater, J.I.3
-
19
-
-
0036785981
-
Transmission of colistin-resistant Pseudomonas aeruginosa between patients attending a paediatric cystic fibrosis center
-
Denton M, Kerr K, Mooney L, et al. Transmission of colistin-resistant Pseudomonas aeruginosa between patients attending a paediatric cystic fibrosis center. Pediatr Pulmonol 2002; 34: 257-261
-
(2002)
Pediatr Pulmonol
, vol.34
, pp. 257-261
-
-
Denton, M.1
Kerr, K.2
Mooney, L.3
-
20
-
-
0036890364
-
Insights into cystic fibrosis microbiology from the European tobramycin trial in cystic fibrosis
-
Govan JR. Insights into cystic fibrosis microbiology from the European tobramycin trial in cystic fibrosis. J Cyst Fibros 2002; 1: Suppl. 2, 203-208
-
(2002)
J Cyst Fibros
, vol.1
, pp. 203-208
-
-
Govan, J.R.1
-
21
-
-
79951840468
-
Tobramycin inhalation powder for P. Aeruginosa infection in cystic fibrosis: The EVOLVE trial
-
Konstan MW, Geller DE, Minic P, et al. Tobramycin inhalation powder for P. aeruginosa infection in cystic fibrosis: the EVOLVE trial. Pediatr Pulmonol 2011; 46: 230-238
-
(2011)
Pediatr Pulmonol
, vol.46
, pp. 230-238
-
-
Konstan, M.W.1
Geller, D.E.2
Minic, P.3
-
22
-
-
78651412529
-
Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trial
-
Konstan MW, Flume PA, Kappler M, et al. Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: the EAGER trial. J Cyst Fibros 2011; 10: 54-61
-
(2011)
J Cyst Fibros
, vol.10
, pp. 54-61
-
-
Konstan, M.W.1
Flume, P.A.2
Kappler, M.3
-
23
-
-
84875215401
-
Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in patients with cystic fibrosis: A randomised study
-
Schuster A, Haliburn C, Doring G, et al. Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in patients with cystic fibrosis: a randomised study. Thorax 2013; 68: 344-350
-
(2013)
Thorax
, vol.68
, pp. 344-350
-
-
Schuster, A.1
Haliburn, C.2
Doring, G.3
-
24
-
-
84878695314
-
Inhalation of a dry powder ciprofloxacin formulation in healthy subjects: A phase I study
-
Stass H, Nagelschmitz J, Willmann S, et al. Inhalation of a dry powder ciprofloxacin formulation in healthy subjects: a phase I study. Clin Drug Investig 2013; 33: 419-427
-
(2013)
Clin Drug Investig
, vol.33
, pp. 419-427
-
-
Stass, H.1
Nagelschmitz, J.2
Willmann, S.3
-
25
-
-
79957942626
-
Levofloxacin inhalation solution (MP-376) in patients with cystic fibrosis with Pseudomonas aeruginosa
-
Geller DE, Flume PA, Staab D, et al. Levofloxacin inhalation solution (MP-376) in patients with cystic fibrosis with Pseudomonas aeruginosa. Am J Respir Crit Care Med 2011; 183: 1510-1516
-
(2011)
Am J Respir Crit Care Med
, vol.183
, pp. 1510-1516
-
-
Geller, D.E.1
Flume, P.A.2
Staab, D.3
-
26
-
-
84881542878
-
Phase II studies of nebulised Arikace in CF patients with Pseudomonas aeruginosa infection
-
Clancy JP, Dupont L, Konstan MW, et al. Phase II studies of nebulised Arikace in CF patients with Pseudomonas aeruginosa infection. Thorax 2013; 68: 818-825
-
(2013)
Thorax
, vol.68
, pp. 818-825
-
-
Clancy, J.P.1
Dupont, L.2
Konstan, M.W.3
-
27
-
-
84921154784
-
A summary of the results of the phase III multicenter clinical trial: Aerosol administration of recombinant human DNase reduces the risk ofrespiratory tract infections and improves pulmonary function in patients with cystic fibrosis
-
Pulmozyme (rhDNase) Study Group
-
Ramsey B, Pulmozyme (rhDNase) Study Group. A summary of the results of the phase III multicenter clinical trial: aerosol administration of recombinant human DNase reduces the risk ofrespiratory tract infections and improves pulmonary function in patients with cystic fibrosis. Pediatr Pulmonol 1993; Suppl 9: 152-153
-
(1993)
Pediatr Pulmonol
, pp. 152-153
-
-
Ramsey, B.1
-
28
-
-
0028129568
-
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group
-
Fuchs HJ, Borowitz D, Christiansen D, et al. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group. N Engl J Med 1994; 331: 637-642
-
(1994)
N Engl J Med
, vol.331
, pp. 637-642
-
-
Fuchs, H.J.1
Borowitz, D.2
Christiansen, D.3
-
29
-
-
0035666058
-
A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities
-
Quan JM, Tiddens HA, Sy JP, et al. A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities. J Pediatr 2001; 139: 813-820
-
(2001)
J Pediatr
, vol.139
, pp. 813-820
-
-
Quan, J.M.1
Tiddens, H.A.2
Sy, J.P.3
-
30
-
-
33644676982
-
A crossover, randomized, controlled trial of dornase alfa before versus after physiotherapy in cystic fibrosis
-
Fitzgerald DA, Hilton J, Jepson B, et al. A crossover, randomized, controlled trial of dornase alfa before versus after physiotherapy in cystic fibrosis. Pediatrics 2005; 116: e549-e554
-
(2005)
Pediatrics
, vol.116
, pp. e549-e554
-
-
Fitzgerald, D.A.1
Hilton, J.2
Jepson, B.3
-
31
-
-
36849037377
-
Is a longer time interval between recombinant human deoxyribonuclease (Dornase alpha) and chest physiotherapy better? A multi-center, randomized crossover trial
-
Wilson CJ, Robbins LJ, Murphy JM, et al. Is a longer time interval between recombinant human deoxyribonuclease (dornase alpha) and chest physiotherapy better? A multi-center, randomized crossover trial. Pediatr Pulmonol 2007; 42: 1110-1116
-
(2007)
Pediatr Pulmonol
, vol.42
, pp. 1110-1116
-
-
Wilson, C.J.1
Robbins, L.J.2
Murphy, J.M.3
-
32
-
-
30944466084
-
A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
-
Elkins MR, Robinson M, Rose BR, et al. A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. N Engl J Med 2006; 354: 229-240
-
(2006)
N Engl J Med
, vol.354
, pp. 229-240
-
-
Elkins, M.R.1
Robinson, M.2
Rose, B.R.3
-
33
-
-
84861325392
-
Timing of hypertonic saline inhalation for cystic fibrosis
-
CD008816
-
Elkins M, Dentice R. Timing of hypertonic saline inhalation for cystic fibrosis. Cochrane Database Syst Rev 2012; 2: CD008816
-
(2012)
Cochrane Database Syst Rev
, pp. 2
-
-
Elkins, M.1
Dentice, R.2
-
34
-
-
84891709285
-
Timing of dornase alfa inhalation for cystic fibrosis
-
CD007923
-
Dentice R, Elkins M. Timing of dornase alfa inhalation for cystic fibrosis. Cochrane Database Syst Rev 2013; 6: CD007923
-
(2013)
Cochrane Database Syst Rev
, pp. 6
-
-
Dentice, R.1
Elkins, M.2
-
35
-
-
80355127141
-
Inhaled dry powder mannitol in cystic fibrosis: An efficacy and safety study
-
Bilton D, Robinson P, Cooper P, et al. Inhaled dry powder mannitol in cystic fibrosis: an efficacy and safety study. Eur Respir J 2011; 38: 1071-1080
-
(2011)
Eur Respir J
, vol.38
, pp. 1071-1080
-
-
Bilton, D.1
Robinson, P.2
Cooper, P.3
-
36
-
-
84878360064
-
Pooled analysis of two large randomised phase III inhaled mannitol studies in cystic fibrosis
-
Bilton D, Bellon G, Charlton B, et al. Pooled analysis of two large randomised phase III inhaled mannitol studies in cystic fibrosis. J Cyst Fibros 2013; 12: 367-376
-
(2013)
J Cyst Fibros
, vol.12
, pp. 367-376
-
-
Bilton, D.1
Bellon, G.2
Charlton, B.3
-
37
-
-
84858234304
-
Long-term inhaled dry powder mannitol in cystic fibrosis: An international randomised study
-
Aitken ML, Bellon G, De Boeck K, et al. Long-term inhaled dry powder mannitol in cystic fibrosis: an international randomised study. Am J Respir Crit Care Med 2012; 185: 645-652
-
(2012)
Am J Respir Crit Care Med
, vol.185
, pp. 645-652
-
-
Aitken, M.L.1
Bellon, G.2
De Boeck, K.3
-
38
-
-
0030859951
-
Effect of tonicity of nebulised colistin on chest tightness and pulmonary function in adults with cystic fibrosis
-
Dodd ME, Abbott J, Maddison J, et al. Effect of tonicity of nebulised colistin on chest tightness and pulmonary function in adults with cystic fibrosis. Thorax 1997; 52: 656-658
-
(1997)
Thorax
, vol.52
, pp. 656-658
-
-
Dodd, M.E.1
Abbott, J.2
Maddison, J.3
-
39
-
-
84937594872
-
-
2nd Edn. London, Cystic Fibrosis Trust
-
Cystic Fibrosis Trust. Standards of Care and Good Clinical Practice for the Physiotherapy Management of Cystic Fibrosis. 2nd Edn. London, Cystic Fibrosis Trust, 2011. www.cysticfibrosis.org.uk/media/82076/ cd-standards-of-care-physio-june11.pdf
-
(2011)
-
-
-
40
-
-
34347395936
-
RhDNase before airway clearance therapy improves airway patency in children with CF
-
van der Giessen LJ, de Jongste JC, Gosselink R, et al. RhDNase before airway clearance therapy improves airway patency in children with CF. Pediatr Pulmonol 2007; 42: 624-630
-
(2007)
Pediatr Pulmonol
, vol.42
, pp. 624-630
-
-
Van Der Giessen, L.J.1
De Jongste, J.C.2
Gosselink, R.3
-
41
-
-
84937594873
-
The patient’s view of nebulised drugs: Knowledge, adherence, and difficulties
-
Miles K, Lenaghan S, Blanch L, et al. The patient’s view of nebulised drugs: knowledge, adherence, and difficulties. J Cyst Fibros 2014; 13: Suppl. 2, S90
-
(2014)
J Cyst Fibros
, vol.13
-
-
Miles, K.1
Lenaghan, S.2
Blanch, L.3
-
42
-
-
52449130639
-
Evidence based assessment of adherence to medical treatments in pediatric psychology
-
Quittner AL, Modi AC, Lemanek KL, et al. Evidence based assessment of adherence to medical treatments in pediatric psychology. J Pediatr Psychol 2008; 33: 916-936
-
(2008)
J Pediatr Psychol
, vol.33
, pp. 916-936
-
-
Quittner, A.L.1
Modi, A.C.2
Lemanek, K.L.3
-
43
-
-
84911956623
-
Inhaled versus nebulised tobramycin: A real world comparison in adult cystic fibrosis (CF)
-
Harrison MJ, McCarthy M, Fleming C, et al. Inhaled versus nebulised tobramycin: a real world comparison in adult cystic fibrosis (CF). J Cyst Fibros 2014; 13: 692-698
-
(2014)
J Cyst Fibros
, vol.13
, pp. 692-698
-
-
Harrison, M.J.1
McCarthy, M.2
Fleming, C.3
-
44
-
-
84991532304
-
An evaluation of treatment burden following initiation of TOBI Podhaler in patients with cystic fibrosis
-
Bilton D, Nash EF, Peckham D, et al. An evaluation of treatment burden following initiation of TOBI Podhaler in patients with cystic fibrosis. J Cyst Fibros 2014; 13: Suppl. 2, S65
-
(2014)
J Cyst Fibros
, vol.13
-
-
Bilton, D.1
Nash, E.F.2
Peckham, D.3
-
45
-
-
79958257149
-
Accurate assessment of adherence: Self-report vs electronic monitoring of nebulisers
-
Daniels T, Goodacre L, Sutton C, et al. Accurate assessment of adherence: self-report vs electronic monitoring of nebulisers. Chest 2011; 140: 425-432
-
(2011)
Chest
, vol.140
, pp. 425-432
-
-
Daniels, T.1
Goodacre, L.2
Sutton, C.3
-
46
-
-
67649502327
-
Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with Cystic Fibrosis
-
McNamara PS, McCormack P, McDonald AJ, et al. Open adherence monitoring using routine data download from an adaptive aerosol delivery nebuliser in children with Cystic Fibrosis. J Cyst Fibros 2009; 8: 258-263
-
(2009)
J Cyst Fibros
, vol.8
, pp. 258-263
-
-
McNamara, P.S.1
McCormack, P.2
McDonald, A.J.3
-
47
-
-
84882889590
-
Adherence to nebulised therapies in adolescents with cystic fibrosis is best on weekdays during school term-time
-
Ball R, Southern KW, McCormack P, et al. Adherence to nebulised therapies in adolescents with cystic fibrosis is best on weekdays during school term-time. J Cyst Fibros 2013; 12: 440-444
-
(2013)
J Cyst Fibros
, vol.12
, pp. 440-444
-
-
Ball, R.1
Southern, K.W.2
McCormack, P.3
-
48
-
-
84903298392
-
Pulmonary medication adherence and health-care use in cystic fibrosis
-
Quittner AL, Zhang J, Marynchenko M, et al. Pulmonary medication adherence and health-care use in cystic fibrosis. Chest 2014; 146: 142-151
-
(2014)
Chest
, vol.146
, pp. 142-151
-
-
Quittner, A.L.1
Zhang, J.2
Marynchenko, M.3
|