Skeletal muscle metabolism is impaired during exercise in glycogen storage disease type III

Neurology

Volumn 84, Issue 17, 2015, Pages 1767-1771

  Preisler, Nicolai ^a   Laforêt, Pascal ^b   Madsen, Karen Lindhardt ^a   Prahm, Kira Philipsen ^a   Hedermann, Gitte ^a   Vissing, Christoffer Rasmus ^a   Galbo, Henrik ^a   Vissing, John ^a  

^a UNIVERSITY OF COPENHAGEN   (Denmark)

^b ASSISTANCE PUBLIQUE HÔPITAUX DE PARIS   (France)

Author keywords

[No Author keywords available]

Indexed keywords

FATTY ACID; FRUCTOSE; GLUCOSE; GLYCEROL; LACTIC ACID; PALMITIC ACID;

ADULT; ARTICLE; BICYCLE ERGOMETRY; CALORIMETRY; CASE REPORT; CONTROLLED STUDY; EXERCISE TOLERANCE; FATTY ACID OXIDATION; GLUCOSE BLOOD LEVEL; GLYCOGEN STORAGE DISEASE TYPE 3; GLYCOGEN STORAGE DISEASE TYPE 5; GLYCOGENOLYSIS; HEART RATE; HUMAN; KETOGENESIS; LACTATE BLOOD LEVEL; LUNG GAS EXCHANGE; MUSCLE METABOLISM; PRIORITY JOURNAL; SKELETAL MUSCLE; YOUNG ADULT; ADOLESCENT; DIET THERAPY; ENERGY METABOLISM; EXERCISE; METABOLISM; MUSCLE WEAKNESS; PATHOPHYSIOLOGY; PHYSIOLOGY;

ADOLESCENT; ADULT; ENERGY METABOLISM; EXERCISE; FRUCTOSE; GLYCOGEN STORAGE DISEASE TYPE III; HUMANS; MUSCLE WEAKNESS; MUSCLE, SKELETAL; YOUNG ADULT;

EID: 84929118582     PISSN: 00283878     EISSN: 1526632X     Source Type: Journal    
DOI: 10.1212/WNL.0000000000001518     Document Type: Article

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