Sickle cell disease in children: Chronic complications and search of predictive factors for adverse outcomes

European Journal of Haematology

Volumn 94, Issue 2, 2015, Pages 157-161

  Silva, Inês Vaz ^a   Reis, Ana Filipa ^b   Palaré, Maria João ^c   Ferrão, Anabela ^c   Rodrigues, Teresa ^d   Morais, Anabela ^c  

^a Vila Franca de Xira Hospital and Internal Medicine Department of the CUF Torres Vedras Hospital   (Portugal)

^b HOSPITAL GARCIA DE ORTA   (Portugal)

^c HOSPITAL DE SANTA MARIA   (Portugal)

^d INSTITUTO DE MEDICINA MOLECULAR   (Portugal)

Author keywords

Chronic complications; Dactylitis; Sickle cell disease

Indexed keywords

ADOLESCENT; ADVERSE OUTCOME; ALPHA THALASSEMIA; ARTICLE; BONE DISEASE; BRAIN BLOOD FLOW; CHILD; CHOLELITHIASIS; CLINICAL ARTICLE; DACTYLITIS; DELAYED PUBERTY; DISEASE SEVERITY; ENURESIS; FEMALE; HEART DILATATION; HUMAN; LEG ULCER; MALE; PORTUGAL; PRIAPISM; PRIORITY JOURNAL; RESPIRATORY TRACT DISEASE; RETINOPATHY; RISK FACTOR; SICKLE CELL ANEMIA; ANEMIA, SICKLE CELL; BLOOD; CHRONIC DISEASE; COMORBIDITY; INFANT; NEWBORN; PRESCHOOL CHILD; PREVALENCE; PROGNOSIS; RETROSPECTIVE STUDY;

ADOLESCENT; ALPHA-THALASSEMIA; ANEMIA, SICKLE CELL; CHILD; CHILD, PRESCHOOL; CHRONIC DISEASE; COMORBIDITY; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; MALE; PORTUGAL; PREVALENCE; PROGNOSIS; RETROSPECTIVE STUDIES;

EID: 84923035726     PISSN: 09024441     EISSN: 16000609     Source Type: Journal    
DOI: 10.1111/ejh.12411     Document Type: Article

References (16)

1. Prevalence of rare diseases: Bibliographic data, Orphanet Report Series, Rare Diseases collection, Nov 2013, Number 1: Listed in alphabetical order of disease or group of diseases, http://www.orpha.net/orphacom/cahiers/docs/GB/Prevalence:of_ rare diseases_ by_alphabetical_list.pdf
2. Sebastiani P, Nolan VG, Baldwin CT, et al. A network model to predict the risk of death in sickle cell disease. Blood 2007;100:2727-35.
3. Quinn CT, Shull EP, Ahmad N, Lee NJ, Rogers ZR, Buchanan GR. Prognostic significance of early vaso-occlusive complications in children with sickle cell anemia. Blood 2007;109:40-5.
4. Ogedegbe HO. Sickle cell disease: an overview. Lab Med 2002;33:515-43.
5. Platt OS, Brambilla DJ, Rosse WF, Milner PF, Castro O, Steinberg MH, Klug PP. Mortality in sickle cell disease. Life expectancy and risk factors for early death in sickle cell disease. N Engl J Med 1994;330:1639-44.
6. Miller ST, Sleeper LA, Pegelow CH, Enos LE, Wang WC, Weiner SJ, Wether DL, Smith J, Kinney TR. Prediction of adverse outcomes in children with sickle cell disease. N Engl J Med 2000;342:83-9.
7. Foucan L, Ekouevi D, Etienne-Julan M, Salmi LR, Diara JP. Early onset dactylitis associated with the occurrence of severe events in children with sickle cell anaemia. The Paediatric Cohort of Guadeloupe (1984-99). Paediatr Perinat Epidemiol 2006;20:59-66.
8. Vichinsky EP. Overview of the clinical manifestations of sickle cell disease [UpToDate Web site]. November 2012. Available at: www.uptodate.com. Accessed April 2013.
9. National Institute of Health Publication. The Management of Sickle Cell Disease, 4th edn. Bethesda, USA: National Institute of Health Publication, 2002.
10. Jones A, Granger S, Brambilla D, Gallagher D, Vichinsky E, Woods G, Berman B, Roach S, Nichols F, Adams RJ. Can peak systolic velocities be used for prediction of stroke in sickle cell anemia? Pediatr Radiol 2005;35:66-72.
11. Lagunju I, Sodeinde O, Brown B, Akinbami F, Adedokun B. Transcranial doppler ultrasonography in children with sickle cell anemia: clinical and laboratory correlates for elevated blood flow velocities. J Clin Ultrasound 2014;42:89-95.
12. Stallworth JR, Tripathi A, Jerrell JM. Prevalence, treatment, and outcomes of renal conditions in pediatric sickle cell disease. South Med J 2011;104:752-6.
13. a edn. Brasília: Agência Nacional de Vigilância Sanitária, 2002.
14. Platt OS, Thorington BD, Brambilla DJ, Milner PF, Rosse WF, Vichinsky E, Kinney TR. Pain in sickle cell disease, rates and risk factors. N Engl J Med 1991;325:11-6.
15. Quinn CT, Lee NJ, Shull EP, Ahmad N, Rogers ZR, Buchanan GR. Prediction of adverse outcomes in children with sickle cell anemia: a study of the Dallas Newborn Cohort. Blood 2008;111:544-8.
16. Wang WC, Ware RE, Miller ST, et al. A multicenter randomised controlled trial of hydroxyurea (hydroxycarbamide) in very young children with sickle cell anaemia. Lancet 2011;377:1663-72.