Recurrent Pyoderma gangrenosum and cystic acne associated with leucocyte adhesion deficiency due to novel mutations in ITGB2: Successful treatment with infliximab and adalimumab

Acta Dermato-Venereologica

Volumn 95, Issue 3, 2015, Pages 349-351

  Vahlquist, Anders ^a   Håkansson, Lena Douhan ^b   Rönnblom, Lars ^a   Karawajczyk, Malgorzata ^a   Fasth, Anders ^c   Van Gijn, Marielle E ^d   Roos, Dirk ^e   Venge, Per ^a  

^a UPPSALA UNIVERSITY   (Sweden)

^b UPPSALA UNIVERSITY HOSPITAL   (Sweden)

^c UNIVERSITY OF GOTHENBURG   (Sweden)

^d UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^e UNIVERSITY OF AMSTERDAM   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ADALIMUMAB; ANTIBIOTIC AGENT; AZATHIOPRINE; BETAMETHASONE; CD18 ANTIGEN; CYCLOSPORIN; ETANERCEPT; FLUCLOXACILLIN; FORMAZAN; IMMUNOGLOBULIN; INFLIXIMAB; ISOTRETINOIN; METHOTREXATE; OXACILLIN; PENICILLIN DERIVATIVE; PREDNISOLONE; SALAZOSULFAPYRIDINE; TACROLIMUS; TETRACYCLINE; ZINC SULFATE; IMMUNOSUPPRESSIVE AGENT;

ABSENCE OF SIDE EFFECTS; ACNE CYSTICA; ADULT; ANTIBIOTIC THERAPY; BALANITIS; BONE DISEASE; CASE REPORT; CLINICAL FEATURE; DRUG EFFICACY; DRUG MEGADOSE; DRUG RESPONSE; GENE MUTATION; GRANULOCYTE; HUMAN; HUMAN CELL; HUMAN TISSUE; IMMUNOTHERAPY; IMPETIGO; LEUKOCYTE ADHESION DEFICIENCY; MALE; MYOSITIS; NAUSEA; NITROBLUE TETRAZOLIUM TEST; NOTE; OTITIS MEDIA; POINT MUTATION; PRIORITY JOURNAL; PYODERMA GANGRENOSUM; RECURRENT DISEASE; SCAR FORMATION; SKIN ABSCESS; SKIN ULCER; WOUND HEALING; ACNE VULGARIS; CYSTS; DRUG COMBINATION; GENETIC PREDISPOSITION; GENETICS; LEUKOCYTE-ADHESION DEFICIENCY SYNDROME; MUTATION; PHENOTYPE; REMISSION; TREATMENT OUTCOME;

ACNE VULGARIS; ADALIMUMAB; ADULT; ANTIGENS, CD18; CYSTS; DRUG THERAPY, COMBINATION; GENETIC PREDISPOSITION TO DISEASE; HUMANS; IMMUNOSUPPRESSIVE AGENTS; INFLIXIMAB; LEUKOCYTE-ADHESION DEFICIENCY SYNDROME; MALE; MUTATION; PHENOTYPE; PYODERMA GANGRENOSUM; RECURRENCE; REMISSION INDUCTION; TREATMENT OUTCOME;

EID: 84922831239     PISSN: 00015555     EISSN: 16512057     Source Type: Journal    
DOI: 10.2340/00015555-1929     Document Type: Note

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