Proteasome-associated autoinflammatory syndromes: Advances in pathogeneses, clinical presentations, diagnosis, and management

International Journal of Dermatology

Volumn 54, Issue 2, 2015, Pages 121-129

  Mcdermott, Amelia ^a   Jacks, Jennifer ^b   Kessler, Marcus ^a   Emanuel, Peter D ^a   Gao, Ling ^a  

^a UNIVERSITY OF ARKANSAS FOR MEDICAL SCIENCES   (United States)

^b Jacks Dermatology PA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BARICITINIB; BORTEZOMIB; C REACTIVE PROTEIN; CD163 ANTIGEN; CD3 ANTIGEN; CD4 ANTIGEN; CD45RO ANTIGEN; CD8 ANTIGEN; CHLORDANE; DAPSONE; GLUCOCORTICOID; IMMUNOGLOBULIN A; IMMUNOGLOBULIN E; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; IMMUNOSUPPRESSIVE AGENT; INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; INTERLEUKIN 12; INTERLEUKIN 2 RECEPTOR; INTERLEUKIN 4; INTERLEUKIN 5; INTERLEUKIN 6; INTERLEUKIN 8; KALLIKREIN; MONOCYTE CHEMOTACTIC PROTEIN 1; MYELOPEROXIDASE; PROTEASOME; RANTES; TOFACITINIB; LMP7 PROTEIN;

ANEMIA; AUTOINFLAMMATORY DISEASE; CANDLE SYNDROME; CHRONIC ATYPICAL NEUTROPHILIC DERMATOSIS WITH LIPODYSTROPHY AND ELEVATED TEMPERATURE SYNDROME; CLINICAL FEATURE; EOSINOPHIL; ERYTHROCYTE SEDIMENTATION RATE; FAHR DISEASE; HEART FAILURE; HEPATOSPLENOMEGALY; HISTIOCYTE; HISTOPATHOLOGY; HUMAN; HYPERGAMMAGLOBULINEMIA; IMMUNOPATHOGENESIS; INFLAMMATION; JAPANESE AUTOINFLAMMATORY SYNDROME WITH LIPODYSTROPHY; JOINT CONTRACTURE; LEUKOCYTOSIS; LIPODYSTROPHY; LYMPHOCYTOPENIA; MICROCYTIC ANEMIA; MONONUCLEAR CELL; MUSCLE ATROPHY; MYOSITIS; NAKAJO NISHIMURA SYNDROME; NEUTROPHIL; NONHUMAN; PANNICULITIS; PROTEASOME ASSOCIATED AUTOINFLAMMATORY SYNDROME; RASH; RECURRENT FEVER; RESPIRATORY FAILURE; REVIEW; SYNDROME; WASTING SYNDROME; CONTRACTURE; FEVER; GENETICS; HEREDITARY AUTOINFLAMMATORY DISEASES; PATHOLOGY; SKIN DISEASE;

ANEMIA; CONTRACTURE; FEVER; HEREDITARY AUTOINFLAMMATORY DISEASES; HUMANS; LIPODYSTROPHY; MUSCULAR ATROPHY; PROTEASOME ENDOPEPTIDASE COMPLEX; SKIN DISEASES; SYNDROME;

EID: 84921548263     PISSN: 00119059     EISSN: 13654632     Source Type: Journal    
DOI: 10.1111/ijd.12695     Document Type: Review

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